Idiopathic pulmonary fibrosis

Idiopathic pulmonary fibrosis (IPF) inotsvaira kana kuomesa kwemapapu pasina chikonzero chinozivikanwa.

Vanopa hutano havazive chinokonzeresa IPF kana kuti nei vamwe vanhu vachiigadzira. Idiopathic zvinoreva kuti chikonzero hachizivikanwe. Mamiriro acho anogona kunge ari nekuda kwemapapu achipindura kune chinhu chisingazivikanwe kana kukuvara. Majini anogona kutora chinzvimbo mukuvandudza IPF. Chirwere ichi chinowanzoitika muvanhu vari pakati pemakore makumi matanhatu nemakumi manomwe ekuberekwa. IPF yakajairika muvarume kupfuura vakadzi.

Paunenge uine IPF, mapapu ako anova neronda uye kuomarara. Izvi zvinoita kuti zvikuomere kufema. Muvanhu vazhinji, IPF inowedzera kukurumidza kupfuura mwedzi kana makore mashoma. Mune vamwe, IPF inowedzera kupfuura kwenguva yakareba.

Zviratidzo zvinogona kusanganisira chero zvinotevera:

• Kurwadziwa pachifuva (dzimwe nguva)
• Kukosora (kazhinji kuoma)
• Haikwanise kuve wakashanda sepakutanga
• Kufema kwekufema panguva yechiitiko (ichi chiratidzo chinogara kwemwedzi kana makore, uye nekufamba kwenguva kunogona kuitika kana uchizorora)
• Kunzwa kupera simba
• Zvishoma nezvishoma uremu

Iye mupi achaita bvunzo dzepanyama uye obvunza nezve yako nhoroondo yekurapa. Iwe uchabvunzwa kana iwe wakambosangana neasbestos kana imwe chepfu uye kana wanga uchisvuta.

Iko kuongorora kwepanyama kunogona kuona kuti une:

• Kufema kusingaite kunonzwika kunonzi kutsemuka
• Bluish ganda (cyanosis) kutenderedza muromo kana nzara nekuda kweakaderera oxygen (ine advanced chirwere)
• Kuwedzera uye kumisikidza kwezvigunwe zvigunwe, zvinonzi clubbing (ine advanced chirwere)

Kuyedza kunobatsira kuongorora IPF kunosanganisira zvinotevera:

• Bronchoscopy
• Yakakwirira resolution chest CT scan (HRCT)
• Chest x-ray
• Echocardiogram
• Kuyera kweropa reokisijeni (arterial ropa magasi)
• Pulmonary basa bvunzo
• 6-miniti kufamba bvunzo
• Kuyedzwa kwezvirwere zvemuviri zvakaita se rheumatoid arthritis, lupus, kana scleroderma
• Vhura mapapu (kuvhiya) mapapu biopsy

Iko hakuna kurapwa kunozivikanwa kweIPF.

Kurapa kunoitirwa kudzikisira zviratidzo uye kunonoka kufambira mberi kwechirwere:

• Pirfenidone (Esbriet) uye nintedanib (Ofev) mishonga miviri inorapa IPF. Vanogona kubatsira kunonoka kukuvara kwemapapu.
• Vanhu vane yakaderera ropa okisijeni nhanho vachada oksijeni rutsigiro kumba.
• Kugadziriswa kwemapapu hakurape chirwere ichi, asi kunogona kubatsira vanhu kurovedza muviri nekunetseka kushoma kwekufema.

Kuita kumba uye mararamiro shanduko kunogona kubatsira kubata zviratidzo zvekufema. Kana iwe kana chero nhengo yemhuri uchisvuta, ino ndiyo nguva yekumira.

Kuiswa kwemapapu kunogona kutaridzirwa kune vamwe vanhu vane advanced IPF.

Unogona kudzikisira kushushikana kwehurwere nekujoinha boka rekutsigira. Kugovana nevamwe vane zvakajairika zviitiko uye matambudziko zvinogona kukubatsira kuti usazonzwa kusurukirwa.

Rumwe ruzivo uye rutsigiro rwevanhu vane IPF uye mhuri dzavo zvinogona kuwanikwa pa:

• Pulmonary Fibrosis Foundation - www.pulmonaryfibrosis.org/life-with-pf/support-groups
• American Lung Association - www.lung.org/support-and-community/

IPF inogona kusimudzira kana kuramba yakagadzikana kwenguva yakareba uine kana pasina kurapwa. Vanhu vazhinji vanowedzera, kunyangwe nekurapwa.

Kana zviratidzo zvekufema zvikave zvakanyanya, iwe nemupi wako munofanira kukurukura marapirwo anowedzera hupenyu, sekumisikidza mapapu. Zvekare kurukurai pamusoro pekuronga kuchengetedza.

Zvinetso zveIPF zvinogona kusanganisira:

• Asina kujairika akakwirira maseru matsvuku eropa nekuda kweakaderera eropa oxygen mazinga
• Mapapu akadonha
• Kuwedzera kweropa mumitsipa yemapapu
• Kukundikana kwekufema
• Cor pulmonale (kurudyi-sided moyo kutadza)
• Rufu

Fonera mupiki wako ipapo kana uine chero chinotevera:

• Kufema kwakaoma, kukurumidza, kana kudzika (haugone kutora mweya wakadzika)
• Kusendamira kumberi kana wakagara kuti ufeme zvakanaka
• Kazhinji musoro
• Kurara kana kuvhiringidzika
• Kupindwa nechando
• Mucheka wakasviba paunokosora
• Bhuruu zvigunwe kana ganda rakatenderedza nzara dzako

Idiopathic inoparadzira interstitial pulmonary fibrosis; IPF; Pulmonary fibrosis; Cryptogenic fibrosing alveolitis; CFA; Fibrosing alveolitis; Unowanzoitika pneumonitis; UIP

• Kushandisa oxygen kumba

• Spirometry
• Kutamba
• Kufuridzira system

National Moyo, Lung, uye Ropa Institute webhusaiti. Idiopathic pulmonary fibrosis. www.nhlbi.nih.gov/health-topics/idiopathic-pulmonary-fibrosis. Yakasvika muna Ndira 13, 2020.

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Raghu G, Rochwerg B, Zhang Y, et al. Mukuru weATTS / ERS / JRS / ALAT kiriniki yekudzidzira nhungamiro: kurapwa kweidiopathic pulmonary fibrosis. Iyo yekuvandudza ye2011 kiriniki yekudzidzira nhungamiro. Am J Respir Crit Kuchengeta Med. 2015; 192 (2): e3-e19. PMID: 26177183 pubmed.ncbi.nlm.nih.gov/26177183/.

Ryu JH, Selman M, Colby TV, King TE. Idiopathic interstitial pneumonias. Mune: Broaddus VC, Mason RJ, Ernst JD, et al, eds. Murray naNadel Chinyorwa cheKufema Kwemishonga. 6th ed. Philadelphia, PA: Elsevier Saunders; 2016: chits. 63.

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