Retroperitoneal fibrosis

Retroperitoneal fibrosis chirwere chisingawanzovharike chinotadzisa machubhu (ureters) anotakura weti kubva kuitsvo kuenda kudundira.

Retroperitoneal fibrosis inoitika kana mamwe mafuru ane mafomu ari munzvimbo iri kumashure kwedumbu uye ura. Iyo turu inoumba huremu (kana masasi) kana yakaoma fibrotic tishu. Inogona kuvhara machubhu anotakura weti kubva kuitsvo kuenda kudundira.

Zvinokonzera dambudziko iri hazvizivikanwe. Inowanzoitika kune vanhu vane makore makumi mana kusvika makumi matanhatu. Varume vanokwanisa zvakapetwa kaviri kuita mamiriro sevakadzi.

Zviratidzo zvekutanga:

• Kusanzwisisika kurwadziwa mudumbu kunowedzera nenguva
• Marwadzo uye shanduko yerudzi mumakumbo (nekuda kwekuderera kweropa kuyerera)
• Kuzvimba kwegumbo rimwe

Gare gare zviratidzo:

• Yakaderera weti kubuda
• Hapana weti kuburitsa (anuria)
• Nausea, kurutsa, shanduko muhunhu hwepfungwa inokonzerwa neitsvo kutadza uye kuvaka-kwemakemikari ane chepfu muropa
• Kutambudzika kwakanyanya kwepamuviri neropa muchitsiko (nekuda kwekufa kwematumbo matumbu)

Abdominal CT scan ndiyo nzira yakanakisa yekuwana retroperitoneal mass.

Mimwe bvunzo inogona kubatsira kuongorora iyi mamiriro inosanganisira:

• BUN uye creatinine kuongororwa kweropa
• Intravenous pyelogram (IVP), kwete seinowanzo shandiswa
• Itsvo Ultrasound
• MRI yemudumbu
• CAT scan yemudumbu uye retroperitoneum

Biopsy yehuremu inogona zvakare kuitwa kutonga kunze kwegomarara.

Corticosteroids inoedzwa kutanga. Vamwe vanopa hutano vanopirawo mushonga unonzi tamoxifen.

Kana corticosteroid kurapwa isingashande, biopsy inofanira kuitwa kusimbisa kuongororwa. Mimwe mishonga yekudzvinyirira immune system inogona kupihwa.

Kana mushonga usinga shande, kuvhiya uye stents (kudhonza machubhu) zvinodiwa.

Maonero anoenderana nekukura kwedambudziko uye huwandu hwekukuvara kwetsvo.

Kukuvara kweitsvo kunogona kuve kwechinguva kana kwechigarire.

Dambudziko racho rinogona kutungamira ku:

• Inoenderera ichivharika yemachubhu anotungamira kubva kuitsvo kune rimwe kana mativi ese
• Kusingaperi itsvo kutadza

Fonera mupi wako kana iwe uine dumbu repazasi kana kurwadziwa kweparutivi uye kushoma kubuda kweweti.

Edza kudzivirira kushandiswa kwenguva refu kwemishonga ine methysergide. Ichi chinodhaka chakaratidzirwa kukonzera retroperitoneal fibrosis. Methysergide dzimwe nguva inoshandiswa kurapa migraine kutemwa nemusoro.

Idiopathic retroperitoneal fibrosis; Chirwere chaOrmond

• Urume urinary system

Comperat E, Bonsib SM, Cheng L.Renal pelvis uye ureter. Mune: Cheng L, MacLennan GT, Bostwick DG, eds. Urologic Nzira Yokuvhiya Pathology. 4th ed. Philadelphia, PA: Elsevier; 2020: chits. 3.

Nakada SY, Yakanakisa SL. Manejimendi yepamusoro yekuvharira nzira. Mune: Wein AJ, Kavoussi LR, Partin AW, Peters, CA, eds. Campbell-Walsh Urology. 11th ed. Philadelphia, PA: Elsevier; 2016: chits. 49.

O'Connor OJ, Maher MM. Iyo weti turakiti: kuongorora kweatomi, maitiro uye radiation radiation. Muna: Adam A, Dixon AK, Gillard JH, Schaefer-Prokop CM, eds. Grainger & Allison's Kuongorora Radiology: Bhuku Rezvinyorwa Zvekurapa Kufananidza. 6th ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2015: chits. 35.

Shanmugam VK. Vasculitis uye zvimwe zvisingawanzo arteriopathies. Mune: Sidawy AN, Perler BA, eds. Rutherford Kuvhiya kweVascular uye Endovascular Therapy. 9th ed. Philadelphia, PA: Elsevier; 2019: chitsiko 137.

Turnage RH, Mizell J, Badgwell B. Mudumbu mudhuri, umbilicus, peritoneum, mesenteries, omentum, uye retroperitoneum. Mu: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Sabiston Chinyorwa Chekuvhiya. 20th ed. Philadelphia, PA: Elsevier Saunders; 2017: chitsiko 43.