Munyori: William Ramirez
Zuva Rekusika: 18 Gunyana 2021
Gadziridza Zuva: 17 Chikumi 2024
Anonim
Esophageal Atresia : Etiology, Types, Pathophysiology , Clinical Features , Diagnosis and Treatment
Vhidhiyo: Esophageal Atresia : Etiology, Types, Pathophysiology , Clinical Features , Diagnosis and Treatment

Esophageal atresia chirwere chekugaya chikafu umo esophagus isingakure zvakanaka. Iyo esophagus ndiyo chubhu iyo inowanzo takura chikafu kubva pamuromo kuenda mudumbu.

Esophageal atresia (EA) kukanganisa kwakazvarwa. Izvi zvinoreva kuti kunoitika asati aberekwa. Kune mhando dzinoverengeka. Muzviitiko zvakawanda, iyo yekumusoro esophagus inopera uye haibatanidze neyezasi yegurokuro nedumbu.

Vazhinji vacheche vane EA vane chimwe chiremara chinonzi tracheoesophageal fistula (TEF). Uku ndiko kubatana kusingaenzanisike pakati peyesophagus uye windpipe (trachea).

Mukuwedzera, vacheche vane EA / TEF kazhinji vane tracheomalacia. Uku ndiko kushaya simba uye kusagadzikana kwemadziro epombi, iyo inogona kukonzeresa kufema kurira zvine mutsindo kana ruzha.

Vamwe vacheche vane EA / TEF vane zvimwe zvakakanganisika futi, kazhinji kacho hurema hwemwoyo.

Zviratidzo zveEE zvinogona kusanganisira:

  • Bluish coloration kune iro ganda (cyanosis) pamwe nekuyedza kudya
  • Kukosora, kubata muromo, uye kudzipwa nekuyedza kudya
  • Kudonhedza mvura
  • Kudya zvisina tsarukano

Asati aberekwa, iyo ultrasound yaamai inogona kuratidza yakawandisa amniotic fluid. Izvi zvinogona kuve chiratidzo cheEE kana kumwe kuvharika kwenzira yekugaya yemwana.


Dambudziko racho rinowanzoonekwa nguva pfupi mushure mekuzvarwa apo mucheche anoedza kuyamwisa uyezve kukosora, kudzipwa, uye kuita bhuruu. Kana EA ichifungidzirwa, mupi wezvehutano anoedza kupfuudza diki diki yekudyisa chubhu kuburikidza nemuromo wemwana kana mhino mudumbu. Kana iyo yekudyisa chubhu isingakwanise kupfuura nzira yese kuenda mudumbu, mucheche angangoonekwa aine EA.

X-ray inozoitwa uye inoratidza chero yeanotevera:

  • Homwe izere nemweya mudumbu.
  • Mhepo mudumbu uye ura.
  • Iyo yekudyisa chubhu inozoonekwa yakabikwa mune yekumusoro esophagus kana iyo yakaiswa pamberi peiyo x-ray.

EA inyanzvi yekuvhiya. Kuvhiya kwekugadzirisa isophagus kunoitwa nekukurumidza sezvinobvira mushure mekuzvarwa kuitira kuti mapapu arege kukuvara uye mwana akwanise kupihwa chikafu.

Asati avhiyiwa, mwana haapiwe chikafu nemuromo uye anozoda intravenous (IV) chikafu. Kuchengetwa kunoitwa kudzivirira kufamba kwekufema kwekubuda mumapapu.

Kuongororwa kwekutanga kunopa mukana uri nani wemhedzisiro yakanaka.


Mucheche anogona kufema mate uye zvimwe zvinwiwa mumapapu, zvichikonzera kushushikana nemabayo, kudzipwa, uye pamwe kufa.

Zvimwe zvinonetsa zvinogona kusanganisira:

  • Matambudziko ekudyisa
  • Reflux (kudzokororwa kuunzwa kwechikafu kubva mudumbu) mushure mekuvhiyiwa
  • Kuderedza (kuomesa) kwesophagus nekuda kwekukanganisa kubva pakuvhiya

Prematurity inogona kuomesa mamiriro acho. Sezvambotaurwa pamusoro, panogona zvakare kuve nekukanganisa mune dzimwe nzvimbo dzomuviri.

Ichi chirwere chinowanzoonekwa munguva pfupi mushure mekuberekwa.

Fonera mupi wemwana wako ipapo ipapo kana mwana akarutsa kasingaperi mushure mekudyiswa, kana kana mwana achiva nematambudziko ekufema

Madanick R, Orlando RC. Anatomy, histology, embryology, uye kusimudzira kusagadzikana kwesopu. Muna: Feldman M, Friedman LS, Brandt LJ, eds. Sleisenger uye Fordtran's Gastrointestinal uye Chirwere Chirwere: Pathophysiology / Diagnosis / Management. 10th ed. Philadelphia, PA: Elsevier Saunders; 2016: chitsuwa 42.

Rothenberg SS. Esophageal atresia uye tracheoesophageal fistula malformations. Mune: Holcomb GW, Murphy JP, St. Peter SD, eds. Holcomb uye Ashcraft's Pediatric Kuvhiya. 7th ed. Philadelphia, PA: Elsevier Saunders; 2020: chitsiko 27.


Mhumhi RB. Kufungidzira kwemukati. Mu: Resnik R, Lockwood CJ, Moore TR, Greene MF, Copel JA, Sirivha RM, eds. Creasy uye Resnik's Maternal-Fetal Mushonga: Misimboti uye Dzidzira. 8th ed. Philadelphia, PA: Elsevier Saunders; 2019: chitsiko 26.

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