Mucopolysaccharides

Mucopolysaccharides maketeni marefu eshuga mamorekuru anowanikwa mukati memuviri wese, kazhinji mumusuru uye mune mvura inotenderedza majoini. Ivo anowanzozivikanwa anonzi glycosaminoglycans.

Kana muviri ukatadza kuputsa mucopolysaccharides, mamiriro anonzi mucopolysaccharidoses (MPS) anoitika. MPS inoreva kune boka rezvinetso zvakagara nhaka zvemetabolism. Vanhu vane MPS havana chero, kana kukwana, yechinhu (enzyme) inodiwa kupaza mashuga mamorekuru eshuga.

Mafomu ePMP anosanganisira:

• MPS I (Hurler chirwere; Hurler-Scheie syndrome; Scheie syndrome)
• MPS II (Hunter chirwere)
• MPS III (Sanfilippo chirwere)
• MPS IV (Morquio syndrome)

Glycosaminoglycans; GAG

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Pyeritz RE. Nhaka yezvirwere zvezvibatanidza. Mune: Goldman L, Schafer AI, eds. Goldman-Cecil Mushonga. 26th ed. Philadelphia, PA: Elsevier; 2020: chitsama 244.

Mushambadzi JW. Mucopolysaccharidoses. Mune: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Chinyorwa chePediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chitsiko 107.