Acid mucopolysaccharides

Acid mucopolysaccharides bvunzo inoyera chiyero chemucopolysaccharides chakaburitswa mumugini kungave panguva imwe yechiitiko kana pamusoro pemaawa makumi maviri nemana.

Mucopolysaccharides maketani marefu eshuga mamorekuru mumuviri. Ivo vanowanzo kuwanikwa mumamousu uye mune fluid yakatenderedza majoini.

Kweyedzo yemaawa makumi maviri nemana, iwe unofanirwa kuita weti muhombodo chaiyo kana mudziyo nguva dzese paunoshandisa imba yekugezera Kazhinji kazhinji, iwe unozopihwa midziyo miviri. Uchaita weti wakananga mugaba diki rakakosha wobva waendesa iwo weti mune imwe hombe hombe.

• Pazuva 1, weta muchimbuzi paunomuka mangwanani.
• Mushure mekutanga kuita weti, wedzera mumudziyo wakasarudzika nguva dzese dzaunoshandisa yekugezera kwemaawa makumi maviri nemana anotevera. Chinjana weti yacho mumudziyo muhombe uye chengeta hombe yacho munzvimbo inotonhorera kana mufiriji. Chengetedza mudziyo uyu wakasungwa zvakaputirwa.
• Pazuva rechipiri, wedzera mumudziyo mangwanani zvakare paunomuka woendesa weti iyi mumudziyo muhombe.
• Tara hombodo hombe iine zita rako, zuva, nguva yekupedzisa, wobva wadzosera sekurairwa.

Zvemucheche:

Nyatsogeza nzvimbo yakatenderedza urethra (gomba panobuda weti). Vhura homwe yekuunganidza weti (bhegi repurasitiki riine pepa rekunamira kune rimwe divi).

• Kune vanhurume, isa nhengo yese muhombodo wosungirira bepa rinonamira paganda.
• Kune vanhukadzi, isa bhegi pamusoro pemapendero maviri eganda kudivi rese remukadzi (labia). Isa jira pamwana (pamusoro pebhegi).

Tarisa mucheche kazhinji, uye chinja bhegi mushure mekunge mucheche aita weti. Bvisa weti kubva muhomwe kuenda mumudziyo unopihwa nemupi wako wezvehutano.

Vacheche vanoshanda vanogona kufambisa bhegi, zvichikonzera kuti weti ipinde mumachira. Ungangoda mamwe mabhegi ekuunganidza.

Kana wapedza, nyora mudziyo uye woidzorera sezvawakaudzwa.

Iko hakuna gadziriro yakakosha inodiwa.

Iyo bvunzo inosanganisira chete zvakajairwa kuita weti, uye hapana kusagadzikana.

Muedzo uyu unoitwa kuti uongorore boka risingawanzo rezvirwere zvemagene zvinodaidzwa kuti mucopolysaccharidoses (MPS). Izvi zvinosanganisira, Hurler, Scheie, uye Hurler / Scheie syndromes (MPS I), Hunter syndrome (MPS II), Sanfilippo syndrome (MPS III), Morquio syndrome (MPS IV), Maroteaux-Lamy syndrome (MPS VI), uye Sly syndrome (MPS VII).

Kazhinji yenguva, bvunzo iyi inoitwa mune vacheche vanogona kuve nechiratidzo kana nhoroondo yemhuri yeimwe yeaya matambudziko.

Maitiro akajairika anosiyana nezera uye kubva kubazi kuenda kubazi. Taura nemupi wako nezve zvinorehwa nemimwe miedzo yako.

Zvakawanda zvisina kujairika mazinga anogona kuenderana nerudzi rwe mucopolysaccharidosis. Mimwe miedzo inodikanwa kuti uone iyo chaiyo mhando ye mucopolysaccharidosis.

AMP; Dermatan sulphate - weti; Weti heparan sulphate; Weti dermatan sulphate; Heparan sulfate - weti

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Mushambadzi JW. Mucopolysaccharidoses. Mune: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Chinyorwa chePediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chitsiko 107.

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