Maitiro ekurapa phenylketonuria uye maitiro ekudzivirira matambudziko

Zvemukati

• 1. Kurapa zvinovaka muviri
• Nzira yekupa mukaka wemukaka zvakachengeteka
• 2. Kushandiswa kwezvokuwedzera zvinovaka muviri
• Zvinogona kuitika phenylketonuria
• Nzira yekudzivisa

Kuchengetwa uye kurapwa kwe phenylketonuria mumucheche kunofanirwa kutungamirwa nachiremba wevana, asi chikuru kuchengetedza ndeyekudzivirira chikafu chakapfuma mu phenylalanine, izvo zviri zvakanyanya chikafu chakazara mumapuroteni, senyama, hove, mukaka, chizi nemazai. Nekudaro, vabereki vevacheche vane phenylketonuria vanofanirwa kutarisisa kune chikafu chemwana wavo, vese kumba uye kuchikoro.

Uye zvakare, kuyamwisa kwega kwega kunofanirwa kuve kwakatemerwa nachiremba wevana, nekuti mukaka wemuzamu une phenylalanine, kunyange iri shoma kwazvo kupfuura iyo inowanikwa mumafomasi mazhinji emishonga. Sezvineiwo, huwandu hwe phenylalanine hwemucheche unosvika pamwedzi mitanhatu yemakore inofanirwa kuchengetwa pakati pe20 kusvika 70 mg ye phenylalanine pa kg yehuremu hwemuviri.

Izvo zvakakosha kuti kurapwa kwe phenylketonuria kuteverwe maererano nemirairidzo yechiremba wevana uye nyanzvi yezvokudya kudzivirira matambudziko kubva, izvo zvinonyanya kuve zvine chekuita nekusimudzira kwehurongwa hwemitsipa.

1. Kurapa zvinovaka muviri

Kurapa zvinovaka muviri ndiyo nzira huru yekudzivirira kusagadzikana kwechirwere ichi, sezvo zviri kuburikidza nechikafu izvo zvinokwanisika kudzora mwero we phenylalanine muropa, nokudaro uchidzivirira kusangana kwechirwere. Izvo zvakakosha kuti kudya kwacho kutungamirirwe nenyanzvi maererano nezvakabuda mukuyedzwa kwemwana izvo zvinofanirwa kuitwa nguva nenguva kuyera huwandu hwe phenylalanine muropa.

Phenylalanine inogona kuwanikwa muzvikafu zvinoverengeka, zvese mhuka nemiriwo. Nekudaro, kudzora chirwere uye kudzivirira kunetsekana zvakakosha kudzivirira zvimwe zvekudya, senge:

• Zvikafu zvemhuka: nyama, mukaka uye nyama zvigadzirwa, mazai, hove, hove, uye nyama zvigadzirwa soseji, soseji, bhekoni, ham.
• Chikafu chemavambo chakatangira: gorosi, soya uye zvigadzirwa, nzizi, bhinzi, pizi, nyemba, nzungu, nzungu, walnuts, maarumondi, hazelnuts, pistachios, mapine nzungu;
• Zvinotapira zvine aspartame;
• Zvigadzirwa zvine chikafu chinorambidzwa sechinhu chinogadzirwazvakaita semakeke, makuki, ice cream nechingwa.

Zvibereko nemiriwo zvinogona kudyiwa ne phenylketonurics, pamwe neshuga nemafuta. Izvo zvakare zvinokwanisika kuwana pamusika zvigadzirwa zvinoverengeka zvakasarudzika zvakaitirwa vateereri ava, senge mupunga, pasita uye machipisi, uye kune akati wandei mabikirwo ayo anogona kushandiswa kugadzira chikafu chakaderera mu phenylalanine.

Tarisa uone runyorwa rwezvikafu zvakapfuma mu phenylalanine.

Nzira yekupa mukaka wemukaka zvakachengeteka

Kunyangwe kurudziro iri yekusiya mukaka wemuzamu kubva mukudya kwemwana, uchishandisa mukaka wemishonga chete pasina phenylalanine, zvichiri kugona kuyamwisa mwana phenylketonuric, zvisinei pane izvi zvakakosha:

• Ita ongororo yeropa pamwana vhiki rega rega kuti uone huwandu hwe phenylalanine muropa;
• Verenga huwandu hwemukaka wemukaka kuti upe mwana, zvinoenderana nemitengo ye phenylalanine muropa remwana uye nekutungamira kwachiremba wevana;
• Verenga huwandu hwemukaka wefamasi pasina phenylalanine, kupedzisa kuyamwa kwemwana;
• Nepombi, bvisa huwandu hwakafanira hwemukaka wemukaka uyo amai vanogona kupa kumwana;
• Shandisa bhodhoro kana nzira yekubatanidza kudyidzana nemwana.

Izvo zvakakosha kuti ubvise amino acid phenylalanine kubva muchikafu, kuitira kuti mwana asave nezvinetso mukukura kwepanyama uye kwepfungwa, senge kudzora kwepfungwa. Ona kuti chikafu chinofanira kunge chakaita sei mu phenylketonuria.

2. Kushandiswa kwezvokuwedzera zvinovaka muviri

Sezvo kudya kwemunhu ane phenylketonuria kuchinyanya kuvharirwa, zvinokwanisika kuti haana huwandu hwevhitamini nemaminerari anodiwa pakushanda kwakanaka kweiyo muviri uye nekukudziridza kwakakodzera kwemwana. Nekudaro, wezvehutano anokwanisa kukurudzira kushandiswa kwezvokuwedzera uye mafomura ekuvaka muviri kuti ave nechokwadi chekukura kwakanaka kwemwana nekusimudzira hutano hwake.

Iyo yekuwedzera iyo inoshandiswa inoratidzirwa neano nutritionist maererano nezera, huremu hwemunhu uye kugona kwemwana kugaya, uye inofanirwa kuchengetwa muhupenyu hwese.

Zvinogona kuitika phenylketonuria

Zvinetso zve phenylketonuria zvinomuka apo kuongororwa kwacho kusingaitwe kare kana kurapwa kusingateedzwe zvinoenderana nemirayiridzo yechiremba, pamwe nekuunganidzwa kwe phenylalanine muropa, iyo inogona kusvika munzvimbo dzakananga dzehuropi uye inotungamira mukuvandudzika kweshanduko dzechigarire, zvakadai se:

• Kunonoka mukusimudzira psychomotor;
• Kukura kwehuropi hudiki;
• Microcephaly;
• Kusagadzikana;
• Matambudziko ekuzvibata;
• Yakadzikira IQ;
• Kukanganisa kwakakomba kwepfungwa;
• Kubvunda;
• Kudengenyeka.

Nekufamba kwenguva, kana mwana akasarapwa zvakanaka, pangave nekuomerwa mukugara uye kufamba, hunhu kusagadzikana uye kunonoka kutaura uye kusimudzira kwehungwaru, pamusoro pekushungurudzika, pfari uye ataxia, kunova kurasikirwa kwekudzora kwekufamba kwekuzvidira.

Nzira yekudzivisa

Kuti udzivise matambudziko, zvakakosha kuti kuongororwa kwechirwere kuitwe mumazuva ekutanga mushure mekuzvarwa kwemwana kuburikidza nesheel prick test. Kana mhedzisiro yacho yakanaka, zvakakosha kuti kurapwa kwacho kuitwe maererano nehutungamiriri hwechiremba.

Uye zvakare, mune izvi zviitiko zvakakosha kuti bvunzo dzese dzinoitwa kuti utarise hutano hwese hwemwana uye, nekudaro, kuratidza shanduko mukudya uye zvekuwedzera zvekudya.

Miedzo yekutevera inowanzoitwa vhiki nevhiki kusvikira mwana asvitsa gore rimwe chete. Vana vari pakati pemakore maviri kusvika matanhatu ekuberekwa vanodzokorora bvunzo mazuva gumi nemashanu ese uye, kubva pamakore manomwe, bvunzo inoitwa kamwe chete pamwedzi.