Munyori: Judy Howell
Zuva Rekusika: 5 Chikunguru 2021
Gadziridza Zuva: 19 Chikumi 2024
Anonim
Pyruvate Kinase Muedzo - Utano
Pyruvate Kinase Muedzo - Utano

Zvemukati

Pyruvate Kinase Muedzo

Masero matsvuku eropa (RBCs) anotakura okisijeni mumuviri wako wese. Enzyme inozivikanwa se pyruvate kinase inodikanwa kuti muviri wako ugadzire maRBCs uye ushande nemazvo. Iyo pyruvate kinase testis kuongororwa kweropa kunoshandiswa kuyera iwo mazinga e pyruvate kinase mumuviri wako.

Paunenge uine zvishoma zvishoma pyruvate kinase, ako maRBC anoputsa nekukurumidza kupfuura zvakajairwa. Izvi zvinoderedza huwandu hweRBCs dzinowanikwa kutakura okisijeni kunhengo dzakakosha, nyama, uye maseru. Iyo inoguma mamiriro inozivikanwa sehemolytic anemia uye inogona kuve neakakosha hutano mhedzisiro.

Zviratidzo zvehemolytic anemia zvinosanganisira:

  • jaundice (yero yeganda)
  • kuwedzera kwepleen (iro rekutanga spleen kusefa ropa uye kuparadza maRBC ekare uye akakuvara)
  • kupererwa neropa (kushomeka kweRBCs zvine hutano)
  • ganda rakachenuruka
  • kuneta

Chiremba wako anogona kuona kana iwe uine pyruvate kinase kushomeka zvichienderana nemhedzisiro yeiyi uye imwe bvunzo dzekuongorora.

Nei Iyo Pyruvate Kinase Bvunzo Yakarairwa?

Pyruvate kinase kushomeka ihwo hutachiona kusagadzikana kuri autosomal yakawandisa. Izvi zvinoreva kuti mubereki wega wega anotakura rakaremara jeni rechirwere ichi. Kunyangwe iro jeni risingaratidzwe mune chero evabereki (zvichireva kuti kana kushomeka kwepyruvate kinase), hunhu hwakawandisa hune mukana we1-mu-4 wekuonekwa mune chero vana vane vabereki pamwechete.


Vana vanozvarwa kuvabereki vane pyruvate kinase kushomeka gene vanozoongororwa chirwere ichi vachishandisa iyo pyruvate kinase bvunzo. Chiremba wako anogona zvakare kuraira bvunzo pakuziva zviratidzo zve pyruvate kinase kushomeka. Dhata rakaunganidzwa kubva kuongororo yemuviri, iyo pyruvate kinase bvunzo, uye kumwe kuongorora kweropa kunobatsira kusimbisa kuongororwa.

Bvunzo Inoitiswa Sei?

Iwe haufanire kuita chero chakanangana kugadzirira iyo pyruvate kinase bvunzo. Nekudaro, iyo bvunzo inowanzo kupihwa kuvana vadiki, saka vabereki vangangoda kutaura nevana vavo nezvekuti muyedzo unonzwa sei. Iwe unogona kuratidza bvunzo pane chidhori kuti ubatsire kudzikisa kushushikana kwemwana wako.

Iyo pyruvate kinase bvunzo inoitwa paropa rakatorwa panguva yakajairwa ropa dhizaini. Anopa hutano anotora muyenzaniso weropa kubva paruoko rwako kana ruoko achishandisa tsono kana banga rinodaidzwa kuti lancet.

Ropa racho rinounganidza mutubhu robva raenda kurabhoritari kunoongororwa. Chiremba wako anozokwanisa kukupa iwe ruzivo nezve mhedzisiro uye zvavanoreva.


Ndezvipi Njodzi dzeMuyedzo?

Varwere vanoitwa pyruvate kinase bvunzo vanogona kusangana nekusagadzikana mukati meropa reropa. Panogona kuve nekumwe kurwadziwa kunzvimbo yejekiseni kubva kune tsono tsono. Mushure mezvo, varwere vanogona kurwadziwa, kupwanya, kana kurohwa panzvimbo yejekiseni.

Njodzi dzomuedzo idiki. Njodzi dzinogona kuitika chero ipi zvayo yeropa inosanganisira:

  • kunetsekana kuwana sampuro, zvichikonzera tsvimbo dzakawanda dzetsono
  • kubuda ropa zvakanyanya panzvimbo yesero
  • kufenda nekuda kwekurasikirwa neropa
  • kuunganidzwa kweropa pasi peganda, rinozivikanwa sehematoma
  • kukura kwehutachiona uko ganda rakatyorwa netsono

Kunzwisisa Mhedzisiro Yako

Mhedzisiro yeiyo pyruvate kinase bvunzo inozosiyana zvichienderana nerabhoritari inoongorora muyero weropa. Iyo yakasarudzika kukosha yeiyo pyruvate kinase bvunzo inowanzo kuita 179 kuwedzera kana kubvisa 16 zviyero zve pyruvate kinase pamamirioni zana emaRBC. Akadzika mazinga e pyruvate kinase anoratidza kuvepo kwekushomeka kwepyruvate kinase.


Iko hakuna mushonga we pyruvate kinase kushomeka. Kana iwe ukaonekwa uine iyi mamiriro, chiremba wako anogona kukurudzira marapirwo akasiyana siyana. Muzviitiko zvakawanda, varwere vane pyruvate kinase kushomeka vachazoda kuwedzerwa ropa kutsiva maRBC akakuvara. Kuwedzerwa ropa jekiseni reropa kubva kune anenge apa.

Kana zviratidzo zvechirwere zvakanyanya, chiremba wako anogona kukurudzira splenectomy (kubviswa kwepleen). Kubvisa spleen kunogona kubatsira kudzikisa huwandu hweRBCs dziri kuparadzwa. Kunyangwe nepleen yabviswa, zviratidzo zvechirwere zvinogona kuramba zviripo. Nhau dzakanaka ndedzekuti kurapwa kunenge kuchaderedza zviratidzo zvako uye nekuvandudza hupenyu hwako.

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