Akawanda system atrophy - parkinsonia mhando

Multiple system atrophy- parkinsonia mhando (MSA-P) chiitiko chisingawanzo chinokonzera zviratidzo zvakafanana nechirwere chePasinson. Nekudaro, vanhu vane MSA-P vane kukuvara kwakapararira kuchikamu chehurongwa hwemitsipa hunodzora mabasa akakosha senge kurova kwemoyo, BP, uye kudikitira.

Iyo imwe subtype yeMSA ndeye MSA-cerebellar. Inonyanya kukanganisa nzvimbo dzakadzika muuropi, pamusoro pespinal cord chete.

Chikonzero cheMSA-P hachizivikanwe. Nzvimbo dzakakanganiswa dzehuropi dzinopindirana nenzvimbo dzakakanganiswa nechirwere cheParkinson, chine zviratidzo zvakafanana. Neichi chikonzero, iyi subtype yeMSA inonzi parkinsonian.

MSA-P inowanzoonekwa muvarume vakura kupfuura makumi matanhatu.

MSA inokuvadza huta hurongwa. Chirwere chinowanzo fambira mberi nekukurumidza. Inenge hafu yevanhu vane MSA-P varasikirwa neakawanda emota yavo mota mukati memakore mashanu ekutanga kwechirwere.

Zviratidzo zvinogona kusanganisira:

• Kudengenyeka
• Mafambiro ekufamba, senge kunonoka, kurasikirwa pachiyero, shuffling kana uchifamba
• Kakawanda kuwira
• Tsandanyama aches uye marwadzo (myalgia), uye kuomarara
• Kuchinja kumeso, senge chitarisiko chakaita sekunge kumeso kumeso uye kutarisa
• Kuoma kutsenga kana kumedza (pano neapo), kusakwanisa kuvhara muromo
• Akavhiringidza maitiro ekurara (kazhinji panguva yekumhanyisa maziso kufamba [REM] kurara pakati pehusiku)
• Dzungu kana kupera simba paunenge wakamira kana mushure mekumira wakamira
• Matambudziko ekugadzirisa
• Kurasikirwa kwekutonga pamusoro pematumbo kana dundira
• Zvinetso nebasa rinoda kufamba kushoma (kurasikirwa kwehunyanzvi hwemotokari), sekunyora izvo zvidiki uye zvakaoma kuverenga
• Kurasikirwa nedikita mune chero chikamu chemuviri
• Kuderera mukushanda kwepfungwa
• Nausea uye matambudziko nekugaya
• Matambudziko ekumira, senge asina kugadzikana, akatsikitsira, kana kutsvedza
• Chiono chinoshanduka, chakadzikira kana chakakanganiswa kuona
• Inzwi uye kutaura kunochinja

Zvimwe zviratidzo zvinogona kuitika nechirwere ichi:

• Kuvhiringidzika
• Dementia
• Kushungurudzika
• Kurara-kwakanangana nekufema kunetseka, kusanganisira kurara kufema kana kuvharika munzira yemhepo inotungamira kune ruzha runodedera

Anokuchengetedza hutano anokuongorora, otarisa maziso ako, tsinga nemhasuru.

Kuwedzerwa kweropa rako kuchatorwa paunenge wakarara pasi uye wakamira.

Iko hakuna chaiwo miedzo yekusimbisa chirwere ichi. Chiremba anoongorora nezvehurongwa hwemitsipa (neurologist) anogona kuita kuti kuongororwa kubve pa:

• Nhoroondo yezviratidzo
• Ongororo yemuviri
• Kutonga zvimwe zvikonzero zvezviratidzo

Kwayedza kubatsira kusimbisa kuongororwa kunogona kusanganisira:

• MRI yemusoro
• Plasma norepinephrine mazinga
• Weti kuongorora kwe norepinephrine kuputsika zvigadzirwa (weti catecholamines)

Iko hakuna mushonga weMSA-P. Hapana nzira inozivikanwa yekudzivirira chirwere ichi kubva pakuwedzera. Chinangwa chekurapa ndechekudzora zviratidzo.

Mishonga yeDopaminergic, senge levodopa uye carbidopa, inogona kushandiswa kudzikisira kutanga kana kudedera kuderera.

Asi, kune vanhu vazhinji vane MSA-P, iyi mishonga haishande zvakanaka.

Mishonga inogona kushandiswa kurapa yakaderera BP.

Iyo pacemaker iyo yakagadzirirwa kumutsa moyo kurova nekukurumidza (inokurumidza kupfuura zana kurova paminiti) inogona kuwedzera kuwedzera kweropa kune vamwe vanhu.

Kuzvimbirwa kunogona kurapwa neakakwira-fiber chikafu uye laxatives. Mishonga inowanikwa yekurapa matambudziko erection.

Rumwe ruzivo uye rutsigiro rwevanhu vane MSA-P nemhuri dzavo zvinogona kuwanikwa pa:

• National Sangano reRare Dambudziko - rarediseases.org/rare-diseases/multiple-system-atrophy
• Iyo MSA Coalition - www.multiplesystematrophy.org/msa-resource/

Mhedzisiro yeMSA haina kusimba. Kurasikirwa kwemabasa epfungwa uye epanyama zvishoma nezvishoma zvinowedzera. Kufa kwekutanga kungangoitika. Vanhu vanowanzo rarama makore manomwe kusvika mapfumbamwe mushure mekuongororwa.

Fonera mupiki wako kana iwe ukava nezviratidzo zvechirwere ichi.

Fonera waunopa kana iwe waonekwa uine MSA uye zviratidzo zvako zvinodzoka kana kuwedzera kuipa. Zvakare fona kana zviratidzo zvitsva zvikaonekwa, kusanganisira zvinokonzeresa mhedzisiro yemishonga, senge:

• Shanduko mukusvinura / maitiro / manzwiro
• Mufambiro wekunyengera
• Dzungu
• Hallucinations
• Kufambisa kwekuzvipira
• Kurasikirwa kwekushanda kwepfungwa
• Kusvotwa kana kurutsa
• Kuvhiringidzika kwakanyanya kana kusagadzikana

Kana iwe uine nhengo yemhuri ine MSA uye mamiriro avo achiderera kusvika pakutadza kukwanisa kuchengeta munhu pamba, tsvaga rairo kubva kumupi wemhuri yako.

Shy-Drager chirwere; Neurologic orthostatic hypotension; Shy-McGee-Drager chirwere; Parkinson pamwe nechirwere; MSA-P; MSA-C

• Central nervous system uye yekumusoro tsinga system

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Romero-Ortuno R, Wilson KJ, Hampton JL. Kukanganiswa kweiyo autonomic nervous system. Mune: Zadza HM, Rockwood K, Mudiki J, eds. Brocklehurst's Textbook yeGeriatric Mishonga uye Gerontology. 8th ed. Philadelphia, PA: Elsevier; 2017: chits. 63.