Munyori: Christy White
Zuva Rekusika: 9 Chivabvu 2021
Gadziridza Zuva: 1 Chikunguru 2024
Anonim
Hemolytic kupererwa neropa: chii chiri, chikuru zviratidzo uye kurapwa - Utano
Hemolytic kupererwa neropa: chii chiri, chikuru zviratidzo uye kurapwa - Utano

Zvemukati

Autoimmune hemolytic anemia, inozivikanwawo nechidimbu AHAI, chirwere chinoratidzirwa nekugadzirwa kwemasoja anorwisa masero matsvuku eropa, achiaparadza uye achiburitsa kupererwa neropa, ane zviratidzo zvakaita sekuneta, kupora, dzungu, yero uye yakaipa ganda uye maziso ave

Rudzi urwu rweanemia runogona kubata chero munhu, asi rwunowanzoitika kune vechidiki vakuru. Kunyangwe hazvo chikonzero chayo chisingajekeswe nguva dzose, chinogona kumuka kubva mukudzikisirwa kwema immune system mushure mehutachiona, kuvepo kwechimwe chirwere chemuviri, kushandiswa kwemimwe mishonga, kana kunyangwe gomarara.

Autoimmune hemolytic anemia haigone kurapwa nguva dzose, zvisinei, ine kurapwa kunoitwa kunyanya nekushandiswa kwemishonga kudzora immune system, senge corticosteroids uye immunosuppressants. Mune zvimwe zviitiko, kubviswa kwepleen, kunonzi splenectomy, kunogona kuratidzwa, sezvo ino ndiyo nzvimbo panoparadzwa chikamu chemasero matsvuku eropa.

Zviratidzo zvikuru

Zviratidzo zve autoimmune hemolytic anemia zvinosanganisira:


  • Kushaya simba;
  • Kunzwa kupera simba;
  • Pallor;
  • Kushaiwa kudya;
  • Dzungu;
  • Kuneta;
  • Kurara;
  • Indisposition;
  • Kurwadziwa nemusoro;
  • Nzara dzisina kusimba;
  • Ganda rakaoma;
  • Kurasikirwa nevhudzi;
  • Kufema kwekufema;
  • Paleness mu mucous membranes yemeso nemuromo;
  • Jaundice.

Zviratidzo izvi zvakafanana chaizvo neizvo zvinokonzerwa nemamwe marudzi ekushaya ropa, saka zvakafanira kuti chiremba vagadzirire bvunzo dzinogona kubatsira kuziva chaicho chinokonzeresa, senge muyero wakadzikiswa wemasero matsvuku eropa, iyo yakakwira reticulocyte kuverenga, ayo ari masero matsvuku eropa, kuwedzera pakuongororwa kwemuviri.

Tarisa uone kusiyanisa pakati pezvinokonzera kushomeka.

Ndezvipi zvikonzero

Icho chinokonzera autoimmune hemolytic anemia hachiwanzo kuzivikanwa, zvisinei, mune dzakawanda zviitiko zvinogona kuve zvechipiri pakuvapo kwezvimwe autoimmune hosha, senge lupus uye rheumatoid arthritis, cancer, senge lymphomas kana leukemias kana nekuda kwekuita kumishonga, seLevodopa, Methyldopa, anti-inflammatories nemimwe mishonga inorwisa mabhakitiriya.


Inogona zvakare kumuka mushure mehutachiona, senge idzo dzinokonzerwa nehutachiona sengeEpstein-Barr kana Parvovirus B19, kana nemabhakitiriya akadai Mycobacterium pneumoniae kana Treponema pallidum kana ichikonzera njovhera yepamusoro, semuenzaniso.

Mune angangoita makumi maviri muzana ezviitiko, autoimmune hemolytic anemia inowedzerwa nechando, sezvazviri mune izvi zviitiko, masoja ekudzivirirwa anogoneswa netembiricha yakaderera, ichinzi AHAI nemahutachiona anotonhora. Mhosva dzasara dzinodaidzwa kuti AHAI yezvirwere zvinopisa, uye ndivo vakawanda.

Maitiro ekusimbisa kuongororwa

Zvekuongororwa kwe autoimmune hemolytic anemia, bvunzo idzo chiremba acharaira dzinosanganisira:

  • Kuverenga kweropa, kuziva kupererwa neropa uye kucherechedza kuomarara kwayo;
  • Immunological bvunzo, senge yakanangana neCoombs bvunzo, iyo inoratidza kuvepo kwemasoja ekudzivirira akasungirirwa pamusoro pemasero matsvuku eropa. Nzwisisa kuti bvunzo yeCoombs inorevei;
  • Miedzo inoratidza hemolysis, sekuwedzera kwe reticulocytes muropa, ayo ari masero matsvuku eropa asina kujeka anoonekwa muropa kuwanda kana hemolysis;
  • Chipimo chemushonga we bilirubin isina kunangana, iyo inowedzera mumamiriro eakanyanya hemolysis. Ziva kuti ndeyei uye kana iyo bilirubin bvunzo inoratidzwa.

Sezvo anemias akati wandei anogona kuve nezviratidzo zvakafanana uye bvunzo, zvakakosha kuti chiremba agone kusiyanisa pakati pezvakakonzera kushomeka kweropa. Tsvaga zvimwe nezve bvunzo pa: Miedzo inosimbisa kupererwa neropa.


Kurapwa kunoitwa sei

Hazvigone kutaurwa kuti kune mushonga we autoimmune hemolytic anemia, sezvo zvakajairika kuti varwere vane chirwere ichi vawane nguva dzekuputika uye kugadzirisa mamiriro avo.

Kuti urarame kwenguva yakareba sezvinobvira munguva yekuregererwa, zvakafanira kuita kurapwa kunoratidzwa nehematologist, yakagadzirwa nemishonga inodzora immune system, inosanganisira corticosteroids, senge Prednisone, immunosuppressants, senge Cyclophosphamide kana Cyclosporine, immunomodulators, senge munhu immunoglobulin kana plasmapheresis, iyo inobatsira kubvisa zvakawandisa masoja ekudzivirira kubva muropa, mune zvakakomba zviitiko.

Kuvhiya kubviswa kwepleen, kunonzi splenectomy, isarudzo mune zvimwe zviitiko, kunyanya kune varwere vasingateerere zvakanaka kurapwa. Sezvo njodzi yehutachiona inogona kuwedzera vanhu vanobvisa nhengo iyi, majekiseni akadai seantipneumococcal uye antimeningococcal anoratidzwa. Tarisa uone zvakawanda nezve kuchengetwa uye kupora mushure mekubviswa kwepleen.

Uye zvakare, kusarudzwa kwekurapa kunoenderana nerudzi rwe autoimmune hemolytic anemia, zviratidzo zvinoratidzwa uye kuomarara kwechirwere chemunhu wega. Nguva yekurapa inosiyana, uye mune dzimwe nguva unogona kuedza kutanga kutora mishonga mushure memwedzi mitanhatu kuti uongorore mhinduro, zvinoenderana nekutungamira kwehematologist.

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