Ndeipi Ndeipi Tarisiro Yeupenyu Kune Vane Cystic Fibrosis?

Zvemukati

• Chii chinonzi cystic fibrosis?
• Ndeipi tarisiro yehupenyu?
• Inorapwa sei?
• Yakajairika sei cystic fibrosis?
• Ndezvipi zviratidzo uye matambudziko?
• Kurarama necystic fibrosis

Chii chinonzi cystic fibrosis?

Cystic fibrosis chirwere chisingaperi chinokonzeresa hutachiona hwemapapu uye chichiita kuti zvive zvakaoma kufema. Izvo zvinokonzerwa nehurema muiyo CFTR geni. Iko kusagadzikana kunokanganisa gland dzinoburitsa masi uye ziya. Zvizhinji zvezviratidzo zvinokanganisa maitiro ekufema uye ekugaya.

Vamwe vanhu vanotakura geni rakakanganisika, asi haumbofi wakaita cystic fibrosis. Unogona chete kuwana chirwere kana iwe ukagara nhaka yakaremara gene kubva kuvabereki vese.

Kana vatakuri vaviri vaine mwana, panongova nemakumi maviri neshanu muzana mukana wekuti mwana ave necystic fibrosis. Pane mukana we50 muzana mwana anozove mutakuri, uye makumi maviri neshanu muzana mukana mwana wacho haazogare nhaka iyo shanduko zvachose.

Kune zvakawanda zvakasiyana shanduko yeCFTR geni, saka zviratidzo uye kuomarara kwechirwere zvinosiyana kubva pamunhu kusvika kumunhu.

Ramba uchiverenga kuti udzidze zvakawanda nezvekuti ndiani ari panjodzi, sarudzo dzakagadziriswa dzekurapa, uye nei vanhu vane cystic fibrosis vari kurarama kwenguva yakareba kupfuura nakare kose.

Ndeipi tarisiro yehupenyu?

Mumakore apfuura, pakave nekufambira mberi mune zvekurapa zviripo kune vanhu vane cystic fibrosis. Kunyanya nekuda kweiyi nzira yekuvandudza marapirwo, hupenyu hwevanhu vane cystic fibrosis yanga ichiramba ichivandudza kwemakore makumi maviri neshanu apfuura. Makumi emakore mashoma apfuura, vana vazhinji vane cystic fibrosis havana kurarama kusvika vakura.

MuUnited States neUnited Kingdom nhasi, avhareji yekutarisirwa kweupenyu makore makumi matatu kusvika makumi mana. Vamwe vanhu vanogara zvakanaka kupfuura ipapo.

Hupenyu hunotarisirwa hwakadzikira zvakanyanya mune dzimwe nyika, kusanganisira El Salvador, India, neBulgaria, uko kuri pasi pemakore gumi nemashanu.

Inorapwa sei?

Kune akatiwandei ehunyanzvi uye marapirwo anoshandiswa kurapa cystic fibrosis. Chimwe chinangwa chakakosha kusunungura mamasi uye kuchengetedza nzira dzepamhepo dzakajeka. Chimwe chinangwa ndechekuvandudza kunwa kwemuviri.

Sezvo paine zviratidzo zvakasiyana pamwe nekuoma kwezviratidzo, kurapwa kwakasiyana kune munhu wega wega. Masarudzo ako ekurapa anoenderana nezera rako, chero matambudziko, uye nemabatiro aunoita kune mamwe marapirwo. Zvingangodaro kusangana kwemishonga kuchadikanwa, uko kunogona kusanganisira:

• kurovedza muviri uye kurapwa kwemuviri
• muromo kana IV hutano hwekuwedzera
• mishonga yekubvisa mamasi kubva mumapapu
• bronchodilators
• corticosteroids
• mishonga yekuderedza acids mudumbu
• muromo kana inhaled maantibhakitiriya
• pancreatic enzymes
• jekiseni

CFTR-modulators ndeimwe yemarapirwo matsva ayo anotarisana nehurema hwenzara.

Mazuva ano, vanhu vazhinji vane cystic fibrosis vari kugashira mapapu. MuUnited States, vanhu makumi maviri nevaviri vane chirwere ichi vakaiswa mapapu muna2014. Kunyangwe kuiswa kwemapapu kusiri mushonga, kunogona kuvandudza hutano nekurebesa hupenyu. Mumwe muvatanhatu vanhu vane cystic fibrosis vane makore anodarika makumi mana vakaiswa mapapu.

Yakajairika sei cystic fibrosis?

Pasi rese, vanhu zviuru makumi manomwe kusvika zviuru zana vane cystic fibrosis.

MuUnited States, vangangoita vanhu zviuru makumi matatu vari kugara nayo. Gore rega rega vanachiremba vanoongorora chiuru chimwe chezviitiko.

Izvo zvinowanzoitika kune vanhu vanobva kuchamhembe kweEurope vanobva kune mamwe madzinza. Inoitika kamwe muvacheche vachangoberekwa makumi maviri nemashanu kusvika mazana matatu nemazana mashanu. Pakati pevanhu Vatema, chiyero chiri chimwe chete mu17,000 uye kune vekuAsia vekuAmerican, ndeimwe mu31,000.

Inofungidzirwa kuti anenge mumwe muvanhu makumi matatu nevatatu muUnited States anotakura jini risina kukwana. Vazhinji havazive uye vacharamba vakadaro kutoti nhengo yemhuri ikabatwa necystic fibrosis

MuCanada anenge mumwe wevacheche 3 600 voga voga ane chirwere ichi. Cystic fibrosis inokanganisa vacheche muEuropean Union uye mumwe chete muvana 2 500 vanozvarwa muAustralia.

Chirwere hachiwanzoitika muAsia. Chirwere ichi chinogona kunge chisingawanikwe-kuongororwa uye kusambotaurwa-mune mamwe matunhu epasi.

Varume nevakadzi vanobatwa pamwero wakaenzana.

Ndezvipi zviratidzo uye matambudziko?

Kana iwe uine cystic fibrosis, unorasikirwa nemunyu wakawandisa kuburikidza nemamousu ako uye ziya, ndosaka ganda rako rinogona kuravira munyu. Kurasikirwa kwemunyu kunogona kugadzira kusaenzana kwemamineral muropa rako, izvo zvinogona kutungamira ku:

• zvisina kujairika moyo mutinhimira
• yakaderera BP
• kuvhunduka

Dambudziko hombe nderekuti zvakaoma kuti mapapu arambe akajeka mamasi. Inovaka uye inovhara mapapu uye nzira dzekufema. Pamusoro pekuita kuti zvive zvakaoma kufema, inokurudzira hutachiona hunotora mukana kutora.

Cystic fibrosis inobatawo pancreas. Kuwanda kwemamoushu ikoko kunovhiringidza ma enzymes ekugaya, zvichiita kuti zviomere muviri kugadzirisa chikafu uye kutora mavitamini uye zvimwe zvinovaka muviri.

Zviratidzo zvecystic fibrosis zvinogona kusanganisira:

• zvigunwe zvakabvarurwa nezvigunwe
• kufema kana kufema kwekufema
• sinus zvirwere kana nasal polyps
• kukosora izvo dzimwe nguva zvinoburitsa phlegm kana ine ropa
• mapapu akadonha nekuda kwekukosora kusingaperi
• anowanzoitika hutachiona hwemapapu senge bronchitis uye pneumonia
• kushaya zvinovaka muviri uye kushomeka kwevhitamini
• kukura kwakashata
• mafuta, zvituru zvakakura
• kushaya mbereko muvarume
• chirwere cheshuga chine chekuita necystic fibrosis
• chirwatata
• nduru
• chirwere chechiropa

Nekufamba kwenguva, sezvo mapapu achiramba achidzikira, zvinogona kutungamira mukufema kutadza.

Kurarama necystic fibrosis

Iko hakuna kuzivikanwa kurapa kwecystic fibrosis. Icho chirwere chinoda kunyatsoongorora uye kurapwa kwehupenyu hwese. Kurapa kwechirwere kunoda kubatana kwepedyo nachiremba wako uye nevamwe vari kuchikwata chako chekuchengetedza hutano.

Vanhu vanotanga kurapwa vachiri vadiki vanowanzove nehupamhi hwehupenyu, pamwe nehupenyu hwakareba. MuUnited States, vanhu vazhinji vane cystic fibrosis vanoonekwa vasati vasvitsa makore maviri. Vazhinji vacheche vava kuongororwa pavanoedzwa vachangoberekwa.

Kuchengeta yako yemhepo nemapapu yakajeka yemamousu kunogona kutora maawa kubva pazuva rako. Kune nguva dzose njodzi yezvinetso zvakakomba, saka zvakakosha kuyedza kudzivirira utachiona. Izvi zvinorevawo kuti usasangane nevamwe vane cystic fibrosis. Mabhakitiriya akasiyana kubva mumapapu ako anogona kukonzera hutano hwakakomba imi mese.

Nezvose izvi zvekuvandudza mune zvehutano, vanhu vane cystic fibrosis vari kurarama hupenyu hune hutano uye hwakareba hupenyu.

Dzimwe nzira dzinoenderera mberi dzekutsvagisa dzinosanganisira kurapa kwemajini uye madhimoni emushonga anogona kudzora kana kumisa kufambira mberi kwechirwere.

Muna 2014, vanopfuura hafu yevanhu vakaiswa mucystic fibrosis murwere registry vaive vanopfuura makore gumi nemasere. Yaive yekutanga. Masayendisiti uye vanachiremba vari kushanda nesimba kuti vachengetedze iyo yakanaka maitiro kuenda.