Chirwere cheMachado Joseph chinorapika here?

Zvemukati
- Kurapwa kunoitwa sei
- Masangano epanyamaotherapy anoitwa sei
- Ndiani angave nechirwere
- Maitiro ekuongororwa kunoitwa
Chirwere cheMachado-Joseph chirwere chisingawanzoitika chinokonzeresa kudzikira kwehurongwa hwemitsipa, zvichikonzera kurasikirwa kwemhasuru kudzora pamwe nekubatana, kunyanya mumaoko nemakumbo.
Kazhinji, chirwere ichi chinoonekwa mushure memakore makumi matatu ekuberekwa, ichigadzika zvishoma nezvishoma, kutanga ichikanganisa mhasuru dzemakumbo nemaoko uye ichifambira mberi nekufamba kwenguva kune mhasuru dzinotarisira kutaura, kumedza uye kunyange kufamba kwemaziso.
Chirwere cheMachado-Joseph hachigone kurapwa, asi chinogona kudzorwa nekushandiswa kwemishonga uye zvikamu zvephysiotherapy, izvo zvinobatsira kubvisa zviratidzo uye kubvumira kushanda kwakazvimirira kwezviitwa zvezuva nezuva.

Kurapwa kunoitwa sei
Kurapa kwechirwere cheMachado-Joseph kunofanirwa kutungamirirwa nachiremba wezveuropi uye kazhinji kunovavarira kudzikisira izvo zvikanganiso zvinomuka nekuenderera kwechirwere.
Nekudaro, kurapwa kunogona kuitwa ne:
- Kudya kwemishonga yaPasinson, saLevodopa: batsira kudzikisa kuomarara kwekufamba uye kudedera;
- Kushandiswa kwemishonga yeantispasmodic, seBaclofeno: dzinodzivirira kutaridzika kwemhasuru, kuvandudza kufamba;
- Kushandisa magirazi kana malenzi ekururamisa: kudzikisira kuoma kwekuona uye kuoneka kwemaonero maviri;
- Shanduko mukupa: kurapa matambudziko ane chekuita nekumedza kunetseka, kuburikidza neshanduko mukugadzirwa kwechikafu, semuenzaniso.
Uye zvakare, chiremba anogona zvakare kukurudzira kuita zvemuviri zvikamu zvekubatsira murwere kukurira zvaasingakwanise kuita uye kurarama hupenyu hwakazvimirira mukuita zviitiko zvezuva nezuva.
Masangano epanyamaotherapy anoitwa sei
Kurapa kwepanyama kwechirwere cheMachado-Joseph kunoitwa nekugara uchirovedza muviri kubatsira murwere kukurira zvinokanganiswa nechirwere ichi. Naizvozvo, panguva yezvirongwa zvemuviri, zviitwa zvakasiyana zvinogona kushandiswa, kubva pakuita maekisesaizi kuti uchengetedze kuwanda kwemajoini, kudzidza kushandisa madondoro kana mawiricheya, semuenzaniso.
Uye zvakare, physiotherapy inogona zvakare kusanganisira kumedza kurapa kwekurapa iyo inokurudzirwa uye yakakosha kune vese varwere vane chinetso chekumedza chikafu, icho chinoenderana nekukuvara kwemitsipa kunokonzerwa nechirwere.

Ndiani angave nechirwere
Chirwere cheMachado-Joseph chinokonzerwa nekuchinja kwemajini kunogadzira kugadzirwa kweprotein, inozivikanwa seAtaxin-3, iyo inoungana mumasero ehuropi ichikonzera kukura kwezvironda zvinofambira mberi uye kuoneka kwezviratidzo.
Sechinetso chemajini, chirwere cheMachado-Joseph chinowanzoitika muvanhu vanoverengeka mumhuri imwechete, iine mukana we50% wekubva kuvabereki kuenda kuvana. Kana izvi zvikaitika, vana vanogona kukudziridza zviratidzo zvekutanga zvechirwere pakutanga kupfuura vabereki vavo.
Maitiro ekuongororwa kunoitwa
Muzviitiko zvakawanda, chirwere cheMachado-Joseph chinoonekwa nekucherechedza zviratidzo naeurologist uye kuongorora nhoroondo yemhuri yechirwere.
Uye zvakare, kune kuongororwa kweropa, kunozivikanwa seSCA3, iyo inokutendera kuti uone kushanduka kwemajini kunokonzera chirwere. Nenzira iyoyo, kana iwe uine mumwe munhu mumhuri ane chirwere ichi, uye iwe ukaedzwa, zvinokwanisika kuti uone kuti ndeipi njodzi yekuvandudza chirwere ichi zvakare.