Chii chinonzi blue sclera, zvinogona kukonzera uye zvekuita

Zvemukati

• Zvinogona kukonzerwa
• 1. Iron kushaya anemia
• 2. Osteogenesis imperfecta
• 3. Marfan chirwere
• 4. Ehlers-Danlos chirwere
• 5. Kushandiswa kwemishonga

Bhuruu sclera ndiyo mamiriro anoitika kana chena chikamu cheziso chashanduka kuva bhuruu, chimwe chinhu chinogona kucherechedzwa mune vamwe vacheche kusvika pamwedzi mitanhatu yemakore, uye chinogonawo kuonekwa kune vanhu vakura vanopfuura makore makumi masere, semuenzaniso.

Nekudaro, mamiriro aya anogona kuve nehukama nekuonekwa kweimwe hosha senge kushomeka kwesimbi anemia, osteogenesis imperfecta, mamwe ma syndromes uye kunyangwe kushandiswa kwemimwe mishonga.

Kuongororwa kwezvirwere zvinotungamira pakuonekwa kweblue sclera kunofanirwa kuitwa nachiremba, chiremba wevana kana chiremba wemazino uye kunoitwa kuburikidza nekiriniki yemunhu uye nhoroondo yemhuri, kuongororwa kweropa nekufungidzira. Kurapa kunoratidzwa kunoenderana nerudzi uye kuomarara kwechirwere, izvo zvinogona kusanganisira shanduko mukudya, kushandiswa kwemishonga kana kurapwa kwemuviri.

Zvinogona kukonzerwa

Bhuruu sclera inogona kuoneka nekuda kwekudzikiswa kwesimbi muropa kana hurema mukugadzirwa kwecollagen, zvichitungamira mukubuda kwezvirwere zvakaita se:

1. Iron kushaya anemia

Iron kushomeka kupererwa neropa kunotsanangurwa nehemoglobin kukosha muropa, kunoonekwa muyedzo seHb, pazasi peyakajairika seisingasviki gumi nemaviri g / dL mune vakadzi kana 13.5 g / dL mune varume. Zviratidzo zverudzi urwu rweanemia zvinosanganisira kushaya simba, kutemwa nemusoro, kuchinja kuenda kumwedzi, kuneta zvakanyanya uye zvinogona kutungamira pakuonekwa kweblue sclera.

Kana zviratidzo zvikaonekwa, zvinokurudzirwa kutsvaga rubatsiro kubva kuna chiremba mukuru kana wehematologist, uyo anokumbira bvunzo senge yakazara huwandu hweropa uye ferritin dosage, kuti aone kana munhu ane chirwere chekushaya ropa uye huwandu hwechirwere. Dzidza zvakawanda nezve maitiro ekuziva kushomeka kwesimbi anemia.

Zvekuita: mushure mekunge chiremba aongorora, kurapwa kucharatidzirwa, uko kunowanzo kuve nekushandisa ferrous sulphate uye kuwedzera kudyiwa kwezvikafu zvine iron-izvo zvinogona kuve nyama tsvuku, chiropa, nyama yehuku, hove uye yakasvibira miriwo yakasvibirira, pakati pevamwe. Chikafu chakapfuma muvhitamini C, senge orenji, acerola uye ndimu, zvinogona zvakare kukurudzirwa, sezvo ivo vakavandudza kunwa kwesimbi.

2. Osteogenesis imperfecta

Osteogenesis imperfecta chirwere chinokonzeresa kutsemuka kwemapfupa nekuda kwehumwe hutachiona hwakabatana nemhando 1 kolajeni. Zviratidzo zvechirwere ichi zvinotanga kuoneka muhudiki, chimwe chezviratidzo chikuru kuve kuvapo kweblue sclera. Dzidza zvimwe zvimwe zviratidzo zveosteogenesis imperfecta.

Mamwe mapfupa akaremara mudehenya nemuzongoza, pamwe nekuregedzeka kwemitsipa yemapfupa kunoonekwa zvakanyanya mune ino mamiriro, nzira yakakodzera kwazvo iyo chiremba wevana kana chiremba wemazino anoita kuti aone isina kukwana osteogenesis iri nekuongorora izvi zviratidzo. Chiremba anogona kuraira panoramic X-ray kuti anzwisise kukura kwechirwere uye kuratidza kurapwa kwakakodzera.

Zvekuita: kana uchitarisa kuvepo kwebhuruu sclera uye mapfupa akaremara chakanakira kutsvaga chiremba wevana kana chiremba wemazino kuti asimbise iyo isina kukwana osteogenesis uye kurapwa kwakakodzera kunoratidzwa, uko kungave kuri kushandiswa kwe bisphosphonates mutsinga, iri mishonga ku simbisa mapfupa. Kazhinji, zvakafanira zvakare kushandisa ekurapa zvigadzirwa kudzikamisa musana uye kuita epanyama kurapwa zvikamu.

3. Marfan chirwere

Marfan syndrome chirwere chekuzvarwa nacho chinokonzerwa neakanyanya geni, iyo inokanganisa kushanda kwemoyo, maziso, mhasuru nemapfupa. Iyi syndrome inokonzeresa kuratidzwa kwemaziso, senge bhuruu sclera uye inokonzeresa arachnodactyly, inova iyo iyo minwe yakanyanyisa kureba, inoshanduka mubhokisi repfupa uye inosiya musana wakakombama kudivi rimwe.

Kune mhuri dzine zviitiko zvechirwere ichi zvinokurudzirwa kuti zviitise zvemajini, kupi uko mageneti anozoongororwa uye timu yenyanzvi ichapa nhungamiro maererano nekurapwa. Tsvaga zvimwe pamusoro pekuti kupi kurairiswa kwemajini uye kuti kunoitwa sei.

Zvekuita: kuongororwa kwechirwere ichi kunogona kuitwa panguva yekuzvitakura, zvisinei, kana paine fungidziro mushure mekuzvarwa, chiremba wevana anogona kukurudzira kuongororwa kwegeneti uye kuongororwa kweropa kana kwekufungidzira kuti atarise kuti ndeapi mativi emuviri ayo chirwere chasvika. Sezvo Marfan's syndrome isina mushonga, kurapwa kunoenderana nekudzora shanduko munhengo.

4. Ehlers-Danlos chirwere

Ehlers-Danlos syndrome ndiyo seti yezvirwere zvakagarwa nhaka zvinoratidzwa nehurema mukugadzirwa kwe collagen, zvichitungamira mukusimba kweganda nemajoini, pamwe nematambudziko nerutsigiro rwemadziro etsinga nemitsipa yeropa. Dzidza zvakawanda nezve Ehlers-Danlos syndrome.

Zviratidzo zvinosiyana kubva pamunhu kuenda kumunhu, asi shanduko dzakasiyana dzinogona kuitika sekudambuka mumuviri, kupwanya mhasuru uye vanhu vane chirwere ichi vanogona kunge vaine hutete-kupfuura-hwakajairwa ganda pamhino nemiromo, zvichikonzera kukuvara kuitika kazhinji. Iko kuongororwa kunofanirwa kuitwa nachiremba wevana kana chiremba mukuru kuburikidza nekiriniki yemunhu uye nhoroondo yemhuri.

Zvekuita: mushure mekusimbiswa kwehutachiona, tevera navanachiremba vehunyanzvi hwakasarudzika, senge cardiologist, ophthalmologist, dermatologist, rheumatologist, inogona kukurudzirwa, kuitira kuti matanho ekutsigira atorwe kudzora mhedzisiro yechirwere munzvimbo dzakasiyana, sechirwere haina mushonga uye inowedzera kuwedzera nekufamba kwenguva.

5. Kushandiswa kwemishonga

Iko kushandiswa kwemamwe marudzi emishonga kunogona zvakare kutungamira pakuonekwa kweblue sclera, senge minocycline mune yakakwira madhizaini uye mune vanhu vanga vachishandisa kweanopfuura makore maviri. Mimwe mishonga yekurapa mamwe marudzi ekenza, senge mitoxantrone, inogona zvakare kukonzera iyo sclera kuti ishandure bhuruu, mukuwedzera pakukonzeresa kwembambo, ichivasiya iine grey grey.

Zvekuita: aya mamiriro haana kujairika, zvisinei, kana munhu achitora chero imwe yemishonga iyi uye akaona kuti chena chikamu cheziso chine bhuruu muvara, zvakakosha kuzivisa chiremba uyo akapa mushonga, kuitira kuti kumiswa, dosi shanduko kana kuchinjana nemumwe mushonga.