Munyori: Robert Simon
Zuva Rekusika: 21 Chikumi 2021
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Shepherd Center Patient Stories of Hope: Chuck Bruney
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Zvemukati

Chii chinonzi Guillain-Barré syndrome?

Guillain-Barré syndrome chirwere chisingawanzoitika asi chakakomba autoimmune umo immune system inorwisa maseru etsinga ane hutano muhunhu hwako hwekunze (PNS).

Izvi zvinotungamira mukushaya simba, kuveveve, uye kurira, uye zvinogona kupedzisira zvakuomesa mitezo.

Chikonzero cheichi chiitiko hachizivikanwe, asi chinowanzo kukonzerwa nechirwere chinotapukira, senge gastroenteritis (kutsamwa kwemudumbu kana ura) kana hutachiona hwemapapu.

Guillain-Barré isingawanzoitika, ichingobata anenge mumwe chete muvanhu zviuru zana vekuAmerica, sekureva kweNational Institute of Neurological Disorders uye Stroke.

Iko hakuna kurapwa kwechirwere, asi kurapwa kunogona kudzikisira kuomarara kwezviratidzo zvako uye kupfupisa nguva yekurwara.

Kune akatiwandei marudzi eGuillain-Barre, asi fomu yakajairika ndeyekurwisa kwakanyanya kunodzora polyradiculoneuropathy (CIDP). Izvo zvinoguma nekukuvara kune myelin.

Mamwe marudzi anosanganisira Miller Fisher syndrome, iyo inokanganisa tsinga dzenyonganyonga.


Chii chinokonzera Guillain-Barré syndrome?

Chikonzero chaicho chaGuillain-Barre hachizivikanwe. Sekureva kweiyo, vangangoita zvikamu zviviri kubva muzvitatu zvevanhu vane Guillain-Barré vanokudziridza ichangoburwa mushure mekurwara nemanyoka kana chirwere chekufema.

Izvi zvinoratidza kuti mhinduro isiriyo yechirwere kuzvirwere zvakapfuura inokonzeresa kusagadzikana.

Campylobacter jejuni hutachiona hwave hwakabatana naGuillain-Barré. Campylobacter ndeimwe yezvakanyanya kukonzera hutachiona muUnited States. Ichowo chinowanzoitika njodzi kuna Guillain-Barré.

Campylobacter inowanzo kuwanikwa mune chikafu chisina kubikwa, kunyanya huku.

Zvirwere zvinotevera zvakabatanawo naGuillain-Barré:

  • furuwenza
  • cytomegalovirus (CMV), iri dambudziko rehutachiona hwehepe
  • Epstein-Barr hutachiona (EBV) hutachiona, kana mononucleosis
  • mycoplasma pneumonia, inova atypical pneumonia inokonzerwa nehutachiona-senge zvipenyu
  • HIV kana AIDS

Chero ani zvake anogona kuwana Guillain-Barre, asi zvinowanzoitika pakati pevakuru vakuru.


Mune zviitiko zvisingawanzoitika, vanhu vanogona kukudziridza kusagadzikana mazuva kana vhiki mushure mekugamuchira a.

ICDC neKudya neDrug Administration (FDA) zvine masystem aripo ekuongorora kuchengetedzwa kwemishonga, kuona zviratidzo zvekutanga zvemhedzisiro, uye kunyora chero zviitiko zveGuillain-Barre zvinokura zvichitevera mushonga.

CDC iyo tsvagiridzo inoratidza kuti uri mukana wekuwana Guillain-Barre kubva kufuru, pane mushonga.

Ndeapi zviratidzo zveGuillain-Barre syndrome?

MuGuillain-Barre syndrome, immune system yako inorwisa yako peripheral nervous system.

Mitsipa iri munharaunda yako yekutenderera sisitimu inobatanidza uropi hwako kune hwese muviri wako uye ichitumira zviratidzo kumasuru ako.

Tsandanyama hadzizogone kupindura kumasaini avanogamuchira kubva kuuropi hwako kana tsinga idzi dzakakuvara.

Chiratidzo chekutanga chinowanzo kuve kutinhira kwekunzwa muzvigunwe zvako, tsoka, uye makumbo. Iko kurira kunopararira kumusoro kumusoro kumaoko ako neminwe.

Zviratidzo zvinogona kufambira mberi nekukurumidza zvakanyanya. Mune vamwe vanhu, chirwere ichi chinogona kuve chakakomba mumaawa mashoma chete.


Zviratidzo zveGuillain-Barre zvinosanganisira:

  • kurira kana kubaya manzwiro muminwe yako nezvigunwe
  • mhasuru kushaya simba mumakumbo ako anofamba achienda kune yako yepamusoro muviri uye anowedzera kuwedzera nekufamba kwenguva
  • kunetseka kufamba zvakatsiga
  • kuoma kufambisa maziso ako kana kumeso, kutaura, kutsenga, kana kumedza
  • kurwadziwa kwakanyanya kwepashure
  • kurasikirwa kwedundira kudzora
  • kukurumidza kurova kwemoyo
  • kunetseka kufema
  • kuoma mutezo

Guillain-Barré syndrome inoonekwa sei?

Guillain-Barré akaoma kuongorora pakutanga. Izvi zvinodaro nekuti zviratidzo zvacho zvakafanana zvikuru nezvimwe zvinonetsa zvetsinga kana mamiriro anokanganisa hurongwa hwemitsipa, senge botulism, meningitis, kana heavy metal poisoning.

Heavy metal poisoning inogona kukonzerwa nezvinhu zvakaita semutobvu, mercury, uye arsenic.

Chiremba wako anozobvunza mibvunzo nezve chaiwo zviratidzo uye nhoroondo yako yekurapa. Ive neshuwa yekuudza chiremba wako nezve chero asina kujairika zviratidzo uye kana iwe wakambove neazvino kana apfuura maronda kana hutachiona.

Iyi bvunzo inotevera inoshandiswa kubatsira kusimbisa kuongororwa:

Musana pombi

Iyo pombi yemuzongoza (lumbar puncture) inosanganisira kutora hushoma hwemvura kubva musana wako muzasi kwako kumashure. Mvura iyi inonzi cerebrospinal fluid. Yako cerebrospinal fluid inozoedzwa kuti ione maprotein mazinga.

Vanhu vane Guillain-Barré vanowanzove akakwirisa-kupfuura-akajairwa mazinga eprotein mune yavo cerebrospinal fluid.

Electromyography

Iyo electromyography ndeye nerve basa bvunzo. Inoverenga zviitiko zvemagetsi kubva kumhasuru kubatsira chiremba wako kuti adzidze kana hurema hwako hwesimba hunokonzerwa nekukuvara kwetsinga kana kukuvara kwemhasuru.

Tsinga conduction bvunzo

Tsinga dzekuitisa zvidzidzo zvinogona kushandiswa kuyedza kuti tsinga dzako nemhasuru zvinopindura sei kune madiki emagetsi.

Anorapwa sei Guillain-Barré syndrome?

Guillain-Barré ndeye autoimmune kuzvimba maitiro anozvidzora wega, zvichireva kuti ichagadzirisa yega. Zvisinei, chero munhu ane chirwere ichi anofanira kuiswa muchipatara kuti anyatsocherechedzwa. Zviratidzo zvinogona kukurumidza kuwedzera uye zvinogona kuuraya kana zvisina kurapwa.

Muzviitiko zvakakomba, vanhu vane Guillain-Barré vanogona kukura muviri uzere nekufa mitezo. Guillain-Barré anogona kutyisidzira hupenyu kana kuremara kukabata diaphragm kana mhasuru dzechipfuva, kudzivirira kufema kwakakodzera.

Chinangwa chekurapa ndechekuderedza kukomba kwekurwisa immune uye kutsigira muviri wako mashandiro, senge mapapu mashandiro, nepo system yako yetsinga ichipora.

Mishonga inogona kusanganisira:

Plasmapheresis (plasma kuchinjana)

Ma immune immune anogadzira mapuroteni anonzi antibodies anowanzo kurwisa zvinhu zvinokuvadza zvekunze, zvakaita sehutachiona nemavhairasi Guillain-Barré inoitika kana immune system yako ikaita zvisirizvo zvidziviriro zvinorwisa tsinga dzakagadzikana dzetsinga dzako.

Plasmapheresis inoitirwa kubvisa masoja anorwisa tsinga kubva muropa rako.

Munguva iyi maitiro, ropa rinobviswa mumuviri wako nemuchina. Muchina uyu unobvisa masoja ekudzivirira muropa rako wobva wadzosera ropa kumuviri wako.

Intravenous immunoglobulin

Yakakwira madosi emunogoglobulin anogona zvakare kubatsira kuvharira maantibhakitiriya anokonzera Guillain-Barre. Immunoglobulin ine zvakajairika, zvine hutano immune kubva kune vanopa.

Plasmapheresis uye intravenous immunoglobulin inoshanda zvakaenzana. Zviri kwauri uye nachiremba wako kuti musarudze kuti ndeupi kurapwa kwakanyanya.

Mamwe marapirwo

Unogona kupihwa mishonga yekudzora marwadzo uye kudzivirira kuwonda kweropa iwe paunenge usinga fambe.

Iwe ungangodaro unogamuchira kurapa kwemuviri uye kwebasa. Munguva yechikamu chakakomba chehurwere, vanokuchengeta vanofambisa maoko ako nemakumbo kuitira kuti zvigadzikane.

Paunongotanga kupora, varapi vanoshanda newe pakusimbisa mhasuru uye huwandu hwezviitiko zvehupenyu hwezuva nezuva (ADLs). Izvi zvinogona kusanganisira zviitiko zvekuchengeta zvemunhu, sekupfeka.

Ndeapi matambudziko angangoitika eGuillain-Barre syndrome?

Guillain-Barre anokanganisa tsinga dzako. Kushaya simba uye kuoma mitezo kunoitika kunogona kukanganisa zvikamu zvakawanda zvemuviri wako.

Zvinetso zvinogona kusanganisira kunetseka kufema kana kuoma muviri kana kushaya simba kuchipararira kumhasuru dzinodzora kufema. Iwe ungangoda muchina unonzi wekufema kuti ubatsire iwe kufema kana izvi zvikaitika.

Matambudziko anogona zvakare kusanganisira:

  • inononoka kushaya simba, chiveve, kana kumwe kusanzwisisika kwekunzwa kunyangwe mushure mekupora
  • matambudziko emwoyo kana kweropa
  • kurwadziwa
  • kunonoka ura kana dundira basa
  • kuvhara ropa uye kurwara nekuda kwekuoma mitezo

Ndeupi mutarisiro wenguva refu?

Iyo yekudzoreredza nguva yaGuillain-Barre inogona kuva yakareba, asi vanhu vazhinji vanopora.

Kazhinji, zviratidzo zvichawedzera zvakanyanya kwemasvondo maviri kana mana vasati vagadzikana. Kudzorera kunogona kutora chero kupi kubva kumavhiki mashoma kusvika kumakore mashoma, asi mazhinji anopora mumwedzi mitanhatu kusvika gumi nemiviri.

Vanenge makumi masere muzana yevanhu vanobatwa naGuillain-Barré vanogona kufamba vakazvimiririra pamwedzi mitanhatu, uye makumi matanhatu muzana vanowana simba ravo remhasuru mugore rimwe.

Kune vamwe, kupora kunotora nguva yakareba. Vanenge makumi matatu muzana vachiri kuona kushaya simba mushure memakore matatu.

Vanenge 3 muzana yevanhu vanobatwa naGuillain-Barré vanozoona kudzokazve kwezviratidzo zvavo, sekushaya simba uye kurira, kunyangwe makore mushure mechiitiko chekutanga.

Muzviitiko zvisingawanzoitika, mamiriro acho anogona kutyisidzira hupenyu, kunyanya kana ukasawana kurapwa. Zvinhu zvinogona kutungamira kune yakaipa mhedzisiro zvinosanganisira:

  • kukwegura
  • chirwere chakakomba kana chiri kukurumidza kukura
  • kunonoka kwekurapa, izvo zvinogona kukonzera kukuvara kwetsinga kwakawanda
  • kushandiswa kwenguva refu kwemuchina wekufema, izvo zvinogona kukuisa pneumonia

Kuvhara kweropa uye mabhero emubhedha anokonzerwa nekushomeka anogona kuderedzwa. Ropa rakapfava uye kumanikidza masokisi anogona kudzikamisa kugwamba.

Kugara uchimisazve muviri wako kunoderedza kumanikidza kwemuviri kuwanda kunotungamira mukuparara kwemashuga, kana maronda.

Kuwedzera kune ako epanyama zviratidzo, iwe unogona kusangana nematambudziko emanzwiro. Zvinogona kuve zvinonetsa kugadzirisa kune mashoma kufamba uye kuwedzera kuvimba kune vamwe. Unogona kuona zvichibatsira kutaura nachiremba.

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