Hemochromatosis: chii, zviratidzo uye kurapwa

Zvemukati

• Hemochromatosis zviratidzo
• Maitiro ekuongororwa kunoitwa
• Zvinokonzera hemochromatosis
• Kurapwa kunoitwa sei
• Chikafu chinofanira kunge chiri sei

Hemochromatosis chirwere umo mune iron yakawandisa mumuviri, zvichifarira kuunganidzwa kwechicherwa ichi munhengo dzakasiyana dzemuviri uye kutaridzika kwezvinetso zvakadai secirrhosis yechiropa, chirwere cheshuga, kusviba kweganda, kusasimba kwemoyo, kurwadziwa pamwe. kana gland kusagadzikana pabonde, semuenzaniso.

Kurapa kwe hemochromatosis kunoratidzwa nehematologist, ine maphlebotomies, ayo anobviswa nguva nenguva kubva muropa kuitira kuti simbi yakaiswa iendeswe kumasero matsvuku eropa anoburitswa nemuviri, uye mune dzimwe nguva kushandiswa kwevatengesi kubva mumuviri kunogona simbi zvakarehwa, sezvo vachibatsira mukuibvisa.

Hemochromatosis zviratidzo

Hemochromatosis zviratidzo zvinomuka apo huwandu hwesimbi inotenderera muropa hwakanyanya, izvo zvinoita kuti iiswe mune dzimwe nhengo dzakadai sechiropa, moyo, rwatata, ganda, majoini, machende, ovari, utachiona uye pituitary gland. Nekudaro, iyo mikuru zviratidzo nezviratidzo zvinogona kumuka ndeizvi:

• Kuneta;
• Kushaya simba;
• Cirrhosis yechiropa;
• Chirwere cheshuga;
• Kukundikana kwemoyo uye arrhythmias;
• Joint kurwadziwa;
• Kushaya kwekuenda kumwedzi.

Uye zvakare, mune dzimwe nguva, iron yakawandisa inogona kukonzera kushaya bonde, kushaya mbereko uye hypothyroidism. Ziva zvimwe zviratidzo zvinoratidza zvakawandisa iron.

Maitiro ekuongororwa kunoitwa

Kuongororwa kwehemacromatosis kunoitwa pekutanga kuburikidza nekuongororwa kwezviratidzo uye kuongororwa kweropa kunoratidzwa nachiremba wezvematambudziko kana wezvekurapa kuitira kuti aongorore huwandu hwesimbi huripo mumuviri, kuwedzera kune iko kusunganidzwa kweferritin uye kuendesa kweTransferin, zvinoenderana kuchengetedza nekutakura simbi mumuviri.

Uye zvakare, mimwe miedzo inogona kurairwa kuti ibatsire kuongorora izvo zvinokonzeresa hemochromatosis, uye zvinotevera zvinogona kukurudzirwa:

• Kuongorora genetic, iyo inogona kuratidza shanduko mumagene anokonzera chirwere;
• Chiropa biopsy, kunyanya kana zvanga zvisati zvave kukwanisa kusimbisa chirwere kana kuratidza simbi inoiswa muchiropa;
• Phlebotomy mhinduro bvunzo, inoitwa nekubviswa kweropa uye kuongororwa kwematanho esimbi, ichiratidzwa zvakanyanya kune vanhu vasingakwanise kuenda pachiropa biopsy kana uko kuchine kusahadzika nezve kuongororwa.

Iyo hematologist ichakwanisawo kukumbira kuyerwa kwemakemikari echiropa, kuongorora mashandiro kana kuisa simbi munhengo dzinogona kukanganisika, pamwe nekubvisa zvimwe zvirwere zvinogona kukonzera zviratidzo zvakafanana.

Hemochromatosis inofanirwa kuongororwa kune vanhu vane zviratidzo zvekuratidzira, kana paine chisina kutsanangurwa chirwere chechiropa, chirwere cheshuga, chirwere chemwoyo, kusagadzikana pabonde kana chirwere chejoinhi, uye zvakare mune vanhu vane hama dzekutanga-denda vane chirwere kana vane shanduko pamitengo ye ropa rinoongorora iron.

Zvinokonzera hemochromatosis

Hemochromatosis inogona kuitika semhedzisiro yekuchinja kwemajini kana semhedzisiro yezvirwere zvine chekuita nekuparadzwa kwemasero matsvuku eropa, ayo anosimudzira kuburitswa kwesimbi muropa. Nekudaro, zvinoenderana nechikonzero, hemochromatosis inogona kuiswa muchikamu:

• Nhaka hemochromatosis, iyo ndiyo honzeri huru yechirwere uye kuti zvinoitika nekuda kwekuchinja kwemajini anokonzeresa kufema kwesimbi mugero rekugaya, iyo inotanga kunyudzwa muhuwandu hwakawanda, ichiwedzera huwandu hwesimbi inotenderera mumuviri;
• Sekondari kana kuwanikwa haemochromatosis, umo kuunganidzwa kwesimbi kunoitika nekuda kwemamwe mamiriro ezvinhu, kunyanya hemoglobinopathies, umo kuparadzwa kwemasero matsvuku eropa kunoburitsa simbi yakawanda muropa. Zvimwe zvikonzero zvinodzokerwa kuwedzerwa ropa, chisingaperi cirrhosis kana kushandiswa zvisirizvo kwemishonga yekushaya ropa, semuenzaniso.

Izvo zvakakosha kuti chikonzero che hemochromatosis chinozivikanwa nachiremba, sezvo zvichidaro kuti kurapwa kwakakodzera kwazvo kunoratidzwa, kubatsira kudzivirira matambudziko uye kudzikisira zviratidzo zvinokonzerwa neyakawandisa iron.

Kurapwa kunoitwa sei

Hereditary hemochromatosis haina mushonga, zvisinei, kurapwa kunogona kuitwa senzira yekudzora zvitoro zvesimbi muropa uye kudzivirira kuiswa munhengo. Nekudaro, mune idzi kesi, nzira huru yekurapa ndeye phlebotomy, inonziwo kubuda ropa, mune chikamu cheropa chinobviswa kuitira kuti iron yakawandisa ive chikamu chemasero matsvuku eropa ayo muviri unoburitsa.

Mushonga uyu une chikamu chinotyisa chekutanga, asi zvakafanira kuita madosi ekuchengetedza, umo ma350 kusvika ku450 ml yeropa inotorwa ka1 kana ka2 pasvondo. Ipapo, zvikamu zvacho zvinogona kupatsanurwa zvinoenderana nemhedzisiro yekubvunzurudza bvunzo, inoratidzwa nahematologist.

Imwe nzira yekurapa ndeyekushandisa mishonga inozivikanwa sesimbi chelators kana "vanotsvaira", senge Desferroxamine, sezvo vachisimudzira kudzikiswa kwemazinga esimbi anotenderera. Uku kurapwa kunoratidzwa kune vanhu vasingakwanise kutsungirira phlebotomy, kunyanya avo vane chirwere chakakomba chekushaya ropa, kutadza kwemoyo kana cirrhosis yepamusoro yechiropa.

Ona zvimwe zvakawanda zvehutano hwesimbi yakawandisa muropa.

Chikafu chinofanira kunge chiri sei

Pamusoro pekurapa kunoratidzwa nachiremba, zvakakoshawo kuti utarise kune chikafu, uye zvinokurudzirwa kudzivirira kunwa zvakanyanya zvekudya zvine iron. Mimwe mirayiridzo ine chekuita nechikafu ndeiyi:

• Dzivisa kudya nyama muhuwandu hwakawanda, uchipa kuda kune chena nyama;
• Idya hove kanokwana kaviri pasvondo;
• Dzivisa kudya miriwo ine iron, senge sipinashi, beet kana bhinzi yegirini, kanopfuura kamwe pasvondo;
• Idya chingwa chegorosi chakazara pachinzvimbo chechingwa chena kana simbi-yakasimbiswa;
• Idya chizi, mukaka kana yogati zuva nezuva nekuti calcium inoderedza kutora kwesimbi;
• Dzivisa kudya michero yakaoma, yakaita semazambiringa akaomeswa, muhuwandu hwakawanda nekuti iine iron.

Mukuwedzera, munhu wacho anofanira kudzivisa zvinwiwa zvinodhaka kuitira kuti arege kukuvara kwechiropa uye kuti asashandise mavitamini anowedzera nesimbi uye vitamini C, sezvo izvi zvinowedzera kuiswa kwesimbi.