Munyori: John Stephens
Zuva Rekusika: 26 Ndira 2021
Gadziridza Zuva: 1 Chikunguru 2024
Anonim
Zvese Nezve Antiphospholipid Syndrome (Hughes Syndrome) - Utano
Zvese Nezve Antiphospholipid Syndrome (Hughes Syndrome) - Utano

Zvemukati

Mhedziso

Hughes syndrome, inozivikanwawo se "kunamira ropa syndrome" kana antiphospholipid syndrome (APS), ndeye autoimmune mamiriro ayo anokanganisa nzira iyo yako masero eropa anosunga pamwechete, kana kugwamba. Hughes syndrome inoonekwa isingawanzoitika.

Vakadzi vanowanzo kuve nepamuviri uye vanhu vane sitiroko vasati vava nemakore makumi mashanu dzimwe nguva vanoona kuti Hughes syndrome ndiyo yaive chikonzero. Inofungidzirwa kuti Hughes syndrome inokanganisa katatu kana kashanu kuwanda kwevakadzi sevarume.

Kunyangwe chikonzero cheHughes syndrome chisina kujeka, vaongorori vanodavira kuti kudya, mararamiro, uye genetics zvese zvinogona kubatsira mukuvandudza mamiriro acho.

Zviratidzo zveHughes syndrome

Zviratidzo zveHughes syndrome zvakaoma kuona, sezvo kugwamba kweropa hachisi chinhu chaunogona kuona zviri nyore pasina mamwe mamiriro ehutano kana matambudziko. Dzimwe nguva Hughes syndrome inokonzeresa kutsvuka kutsvuka kana kubuda ropa kubva mumhino nemumatadza.

Zvimwe zviratidzo zvekuti iwe unogona kunge uine Hughes syndrome zvinosanganisira:

  • kudzokazve kupfupfudzika kana kubereka mwana akafa
  • ropa rinogwamba mumakumbo ako
  • yekupedzisira ischemic kurwisa (TIA) (yakafanana nesitiroko, asi isina zvachose neurologic mhedzisiro)
  • sitiroko, kunyanya kana uri pasi pemakore makumi mashanu
  • yakaderera ropa platelet kuverenga
  • kumira kurova kwemoyo

Vanhu vane lupus vane Hughes syndrome.


Muzviitiko zvisingawanzoitika, Hughes syndrome isingarapwe inogona kuwedzera kana iwe uine zviitiko zvakafanana zvekuvhara muviri mumuviri wese. Izvi zvinonzi zvine njodzi antiphospholipid syndrome, uye zvinogona kukonzera kukuvara kwakanyanya kunhengo dzako pamwe nerufu.

Zvinokonzera Hughes syndrome

Vatsvakurudzi vachiri kushanda kuti vanzwisise zvinokonzera Hughes syndrome. Asi ivo vakatsunga kuti pane chibereko chekutamba pakutamba.

Hughes syndrome haina kupfuudzwa yakananga kubva kumubereki, nenzira iyo mamwe mamiriro eropa, senge hemophilia, anogona kuva. Asi kuva nenhengo yemhuri ine Hughes syndrome zvinoreva kuti iwe unokwanisa kuita mamiriro acho.

Zvinogoneka kuti geni rakabatana nezvimwe autoimmune mamiriro zvinokonzeresa Hughes syndrome. Izvi zvinogona kutsanangura kuti sei vanhu vane chirwere ichi vachiwanzo kuve nemimwe mamiriro ekuzvimiririra.

Kuva nezvimwe hutachiona kana hutachiona hutachiona, senge E. coli kana iyo parvovirus, inogona kukonzera Hughes syndrome kuti ikure mushure mekunge hutachiona hwabviswa. Mishonga yekudzivirira pfari, pamwe nemidziyo yekudzivirira pamuromo, inogona zvakare kutora chinzvimbo mukukonzera mamiriro acho.


Izvi zvezvakatipoteredza zvinogona zvakare kubatana nemararamiro ehupenyu - sekusawana zvakakwana kurovedza muviri uye kudya chikafu chakazara mu cholesterol - uye chinokonzeresa Hughes syndrome.

Asi vana nevakuru vasina chero eizvi hutachiona, mararamiro ehupenyu, kana kushandisa kwemushonga vanogona kuwana Hughes syndrome chero nguva.

Zvimwe zvidzidzo zvinodiwa kugadzirisa zvikonzero zveHughes syndrome.

Kuongororwa kweHughes syndrome

Hughes syndrome inoonekwa kuburikidza nekuteedzana kweropa kuongororwa. Aya maedzo eropa anoongorora masoja ekudzivirira anoita masero ako ekudzivirira muviri kuti aone kana achizvibata zvakajairika kana achitarisa mamwe maseru ane hutano.

Kuongororwa kweropa kwakajairika kunozivisa Hughes syndrome kunonzi antibody immunoassay. Ungangoda kuve nezvakawanda zveizvi zvinoitwa kutonga kunze mamwe mamiriro.

Hughes syndrome inogona kusanzwisiswa seyakawandisa sclerosis nekuti iwo maviri mamiriro ane zvakafanana zviratidzo. Kunyatso kuyedzwa kunofanirwa kuona kunyatso kuongororwa kwako, asi zvinogona kutora nguva.


Kurapa kweHughes syndrome

Hughes syndrome inogona kurapwa neropa rakapfava (mushonga unoderedza njodzi yako yekuvhara ropa).

Vamwe vanhu vane Hughes syndrome havaratidzi zviratidzo zvekugwamba kweropa uye havangade chero kurapwa kupfuura aspirin kudzivirira njodzi yemapundu anokura.

Mishonga yeanticoagulant, senge warfarin (Coumadin) inogona kupihwa, kunyanya kana iwe uine nhoroondo yeakadzika vein thrombosis.

Kana iwe uri kuyedza kutakura nhumbu kusvika kune imwe nguva uye uine Hughes syndrome, unogona kupihwa yakaderera-dose aspirin kana muyero wezuva nezuva weropa rakatetepa heparin.

Vakadzi vane Hughes syndrome vane makumi masere muzana mukana wekuti vatakure mwana kutemu kana vaonekwa uye vatanga kurapwa kuri nyore.

Kudya uye kurovedza muviri kweHughes syndrome

Kana iwe ukabatwa uine Hughes syndrome, chikafu chine hutano chinogona kudzora njodzi yako yezvinogona kusangana, senge sitiroko.

Kudya chikafu chakapfuma mumichero nemiriwo uye chakaderera mumafuta ekufambisa neshuga kuchakupa hutano hutano hwemwoyo, zvichiita kuti ropa riwedzere kushomeka.

Kana iwe uchirapa Hughes syndrome newarfarin (Coumadin), iyo Mayo Clinic inokukurudzira kuti iwe uwirirane nehuwandu hwevhitamini K yaunodya.

Kunyange madiki vhitamini K asingakwanise kukanganisa kurapwa kwako, kugara uchisiyanisa kudya kwako vhitamini K kunogona kuita kuti mushonga wako ushanduke zvine njodzi. Broccoli, nhungirwa yeBrussels, garbanzo nyemba, uye avocado zvimwe zvezvikafu zvine vhitamini K.

Kugara uchirovedza muviri kunogona zvakare kuve chikamu chekugadzirisa mamiriro ako. Dzivisa kusvuta uye chengeta huremu hune hutano hwerudzi rwemuviri wako kuti uchengete moyo wako uye tsinga dzakasimba uye dzikurire kuramba kukuvara.

Maonero

Kune vanhu vazhinji vane Hughes syndrome, zviratidzo uye zviratidzo zvinogona kutarisirwa pamwe neropa rakapfava uye anticoagulant mishonga.

Pane zvimwe zviitiko apo kurapwa uku kusingashande, uye dzimwe nzira dzinofanirwa kushandiswa kuchengetedza ropa rako kuti rirege kugwamba.

Kana ikasiiwa isingarapwe, Hughes syndrome inogona kukuvadza yako yemwoyo system uye nekuwedzera njodzi yako kune mamwe mamiriro ehutano, sekuparara uye kurohwa. Kurapa kweHughes syndrome ndekweupenyu hwese, sezvo pasina mushonga weichi chiitiko.

Kana iwe uine chero cheanotevera, taura nachiremba wako nezve kuyedzwa Hughes syndrome:

  • kanopfuura kamwechete akagwamba ropa akagwamba akakonzera kusagadzikana
  • imwe kana kupfuura akanganisa mushure mevhiki yegumi yekuzvitakura
  • matatu kana anopfuura ekutanga miscarriage mune yekutanga trimester yepamuviri

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