Munyori: Morris Wright
Zuva Rekusika: 25 Kubvumbi 2021
Gadziridza Zuva: 25 Chikumi 2024
Anonim
Chii chinonzi mastocytosis, mhando, zviratidzo uye kurapwa - Utano
Chii chinonzi mastocytosis, mhando, zviratidzo uye kurapwa - Utano

Zvemukati

Mastocytosis chirwere chisingawanzozivikanwa chinoonekwa nekuwedzera uye kuwanda kwemasero maseru muganda uye mamwe materu emuviri, zvichitungamira pakuonekwa kwemavara uye madiki madiki akatsvukuruka-ganda paganda rinoruma zvakanyanya, kunyanya kana paine shanduko yetembiricha uye apo ganda rinopinda mukubatana nembatya, semuenzaniso.

Mast maseru maseru anogadzirwa mumongo wemapfupa, ayo anowanikwa mune akasiyana matissue emuviri uye ayo anogona zvakare kuve nehukama nekuzvidzivirira kwekuzvidzivirira, kunyanya mumhinduro yegoriki. Zvisinei, kusiyana nehutachiona, zviratidzo uye zviratidzo zve mastocytosis hazvigumi uye hazvina hukama nezvinokonzera zvinhu.

Izvo zvakakosha kuti mastocytosis ionekwe uye inorapwa zvinoenderana nemirairo yechiremba, nekuti mune dzimwe nguva inogona zvakare kuve yakabatana nemamwe matambudziko akakomba eropa, akadai seacute leukemia, lymphoma, chisingaperi neutropenia uye myeloproliferative shanduko.

Mhando dzemastocytosis

Mastocytosis inoitika kana mast mast achiwedzera uye achiungana mumuviri uye, zvichienderana nekuti masero aya akaunganidzwa kupi, mastocytosis inogona kuiswa mune:


  • Yakatemwa mastocytosis, umo mast masero anounganidzwa muganda, zvichitungamira pakuonekwa kwezvakachekwa zviratidzo nezviratidzo, kuva zvinowanzoitika muvana;
  • Systemic mastocytosis, umo mast mast anoungana mune mamwe matishu emuviri, kunyanya mumongo wepfupa, zvichikanganisa kugadzirwa kwemasero eropa. Uye zvakare, mune iyi mhando yemastocytosis, mast masero anogona kuunganidzwa muchiropa, spleen, lymph node uye mudumbu, uye anogona kupindira, mune dzimwe nguva, mukushanda kwenhengo.

Kubva panguva iyo paine huwandu hwakawanda hwemaseru munzvimbo iyi, zviratidzo nezviratidzo zvinoratidza chirwere zvinoonekwa, uye zvakakosha kuti ubvunze chiremba kuitira kuti bvunzo dziitwe kupedzisa kuongororwa uye kutanga kurapwa kwakakodzera.

Zviratidzo nezviratidzo zve mastocytosis

Zviratidzo nezviratidzo zve mastocytosis zvinogona kusiyana maererano nerudzi uye zvine chekuita nekutenderera kwekutenderera histamine. Imhaka yekuti mast masero akagadzirwa nemagirosa anoburitsa histamine. Nekudaro, iyo inowedzera kukosheswa kwemast mast, iko kwakanyanya kuwanda kwe histamine, zvinotungamira kune zviratidzo nezviratidzo zve mastocytosis, makuru acho ari:


  • Nguruve urticaria, idzo diki dzakatsvukuruka-shava makanda paganda dzinogona kuvava;
  • Peptic ulcer;
  • Kurwadziwa nemusoro;
  • Palpitations;
  • Kusvipa;
  • Manyoka asingagumi;
  • Marwadzo emudumbu;
  • Kunzwa dzungu pakusimuka;
  • Minyatso nezvigunwe zvine chiveve.

Mune zvimwe zviitiko, mastocytosis zviratidzo zvinogona kuwedzera kana paine shanduko mukushisa, mushure mekudya zvakanyanya kana zvinwiwa zvekudya kana zvinwiwa, mushure mekurovedza muviri, mushure mekubatana nembatya kana semhedzisiro yekushandisa imwe mishonga.

Kuongororwa kwemastocytosis kunoitwa kuburikidza nekuongororwa kweropa kunovavarira kuona mwero we histamine uye prostaglandin D2 muropa, iyo inofanirwa kuunganidzwa nekukurumidza mushure medambudziko, kana mumurini wemaawa makumi maviri nemana.

Uye zvakare, mune kesi yekucheka mastocytosis, histological bvunzo inogona kuitwawo, mune iyo sampuro diki yechironda inounganidzwa uye inotumirwa ku laboratori kuti iongororwe uye kutarisa kana paine huwandu hwakawanda hwemast cell mumashutu. .


Kwakadii kurapwa

Kurapa kwemastocytosis kunofanirwa kutungamirwa neye immunoallergologist kana general general maererano neyakafambiswa histamine mazinga, nhoroondo yehutano hwemunhu uye zviratidzo nezviratidzo.

Muzviitiko zvakawanda, chiremba anogona kukurudzira kushandiswa kwemishonga kubvisa zviratidzo, kunyanya antihistamines uye corticosteroid makirimu uye mafuta. Zvisinei, apo zviratidzo zvinonyanya kuoma, kunyanya kana zvasvika kune systemic mastocytosis, kurapwa kunogona kuve kwakaomarara, uye mune dzimwe nguva kuvhiya kunogona kudikanwa.

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