Myasthenia gravis: chii zvazviri, zviratidzo, kuongororwa uye kurapwa

Zvemukati
- Zviratidzo zvinogona kuitika
- Maitiro ekuongororwa kunoitwa
- Chii chinokonzera myasthenia gravis
- Kurapwa kunoitwa sei
- 1. Mishonga
- 2. Plasmapheresis
- 3. Kuvhiya
- 4. Physiotherapy
Myasthenia gravis, kana myasthenia gravis, chirwere chemuviri chinokonzeresa kushomeka kwemhasuru, chichiwanzoitika kune vakadzi uye kazhinji chinotanga pakati pemakore makumi maviri kusvika makumi mana ekuberekwa. Zviratidzo zvemyasthenia gravis zvinogona kutanga kamwe kamwe, asi kazhinji zvinotanga kuoneka uye zvishoma nezvishoma zvichitowedzera.
Izvo zvinokonzeresa myasthenia gravis zvine chekuita neshanduko mune immune system iyo inokonzeresa kuti ma antibodies arwise zvimwe zvivakwa izvo zvakakosha kune mhasuru kudzora.
THE myasthenia gravis haina mushonga chaiwo, asi kurapwa kwakashandisirwa nyaya imwe neimwe, nemishonga chaiyo uye kurovedza muviri, kunogona kusimudzira hupenyu.

Zviratidzo zvinogona kuitika
Zviratidzo zvekutanga zve myasthenia gravis ndezvi:
- Eyelid kushaya simba uye kunetseka kuvhura maziso kana kubwaira;
- Kushaya simba kwetsandanyama dzemaziso, izvo zvinotungamira kune strabismus uye kuona kaviri;
- Kunyanya kuneta kwemhasuru mushure mekurovedza muviri kana kuita nesimba.
Sezvo chirwere ichi chichienderera mberi, zviratidzo zvinowedzera uye zvinosanganisira:
- Kushaya simba kwemhasuru dzemutsipa dzinosiya musoro wakarembera kumberi kana kudivi;
- Zvakaoma kukwira masitepisi, kusimudza maoko, kunyora;
- Zvakaoma kutaura uye kumedza chikafu;
- Kushaya simba kwemaoko nemakumbo, izvo zvinosiyana mukusimba kwemaawa kana mazuva.
Muzvikamu zvakakomba zvakanyanya, panogona zvakare kuve nekuremara kwemhasuru dzekufema, chirwere chinonzi myasthenic dambudziko, chakakomba uye chinogona kutungamira kurufu kana chikasarapwa nekukurumidza muchipatara.
Zviratidzo zvinowanzo kuwedzera nekudzokorora kushandiswa kwemhasuru yakakanganiswa, asi zvinogona zvakare kuitika kana iwe uchinge uchinge uchinge uchinge uchinge uchipisa, kana uri pasi pekunetseka kana kushushikana, kana kana uchishandisa anxiolytic zvinodhaka kana maantibayoti.
Maitiro ekuongororwa kunoitwa
Kazhinji yenguva iyo chiremba anofungira kuongororwa kwechirwere myasthenia graviskuburikidza nekuongororwa kwezviratidzo, kuongororwa kwemuviri uye kudzidza nhoroondo yehutano hwemunhu.
Nekudaro, bvunzo dzinoverengeka dzinogona kushandiswa kuongorora mamwe matambudziko uye kusimbisa myasthenia gravis. Mimwe yemiedzo iyi inosanganisira electroneuromyography, imagin resonance imaging, computed tomography uye kuongororwa kweropa.
Chii chinokonzera myasthenia gravis
THE myasthenia gravis zvinokonzerwa neshanduko mune immune system iyo inokonzeresa kuti mamwe ma antibodies arwise anogamuchira aripo mumhasuru. Kana izvi zvikaitika, meseji yemagetsi haigone kupfuura nemazvo kubva kune maNeuron kuenda kumhasuru fibers uye, nekudaro, mhasuru hadzibvumirane, zvichiratidza kushaya simba kweiyo myasthenia.
Kurapwa kunoitwa sei
Kune akatiwandei marudzi ekurapa anogona kusimudzira hupenyu hwemunhu, zvinoenderana nezviratidzo zvinoratidzwa. Mamwe mafomu anonyanya kushandiswa anosanganisira:
1. Mishonga
Mishonga ndiyo inonyanya kushandiswa nzira yekurapa, nekuti, pamusoro pekuita inoshanda, ine mhedzisiro yakanaka. Mhando dzinonyanya kushandiswa dzemishonga ndeidzi:
- Cholinesterase inhibitors, senge Pyridostigmine: kunatsiridza kufamba kwesimba remagetsi pakati peiyo neuron uye mhasuru, kugadzirisa kunetseka kwemhasuru uye simba;
- Corticosteroids, senge Prednisone: deredza kushanda kwe immune immune uye, nekudaro, inogona kudzikisira mhando dzakasiyana dzezviratidzo. Nekudaro, izvo hazvigone kushandiswa kwenguva yakareba, sezvo vachigona kuve nemhedzisiro mhedzisiro;
- Immunosuppressants, seAzathioprine kana Ciclosporin: mishonga iyi inoderedza mashandiro ezvirwere zvemuviri, asi anoshandiswa mumatambudziko akawandisa, apo zviratidzo zvisingaite nemimwe mishonga.
Pamusoro pemishonga yekumuromo, chiremba anogona zvakare kukurudzira kushandiswa kwemushonga, senge monoclonal antibodies, ayo anoderedza huwandu hwemamwe maseru ekudzivirira mumuviri, achivandudza zviratidzo zve myasthenia gravis.
2. Plasmapheresis
Plasmapheresis kurapwa, kwakafanana nedialysis, umo ropa rinobviswa mumuviri uye richipfuura nemuchina unobvisa masoja ekudzivirira anorwisa maseru receptors, zvichifambisa kufambisa kwechiratidzo chemagetsi pakati peeuron uye mhasuru fibers.
Kunyangwe iri kurapwa ine mibairo yakanaka, zvakare ine dzimwe njodzi dzehutano dzakadai sekubuda ropa, mhasuru yemhasuru uye kunyangwe hwakasimba hwemaitiro ekurwisa.
3. Kuvhiya
Kuvhiya kurapwa kusingawanzoitika, asi zvinogona kudikanwa kana bundu rikazivikanwa munhengo yemasoja ekudzivirira muviri izvo zviri kukonzera kugadzirwa kwemasoja ekudzivirira anounza myasthenia gravis.
4. Physiotherapy
Mota uye yekufema physiotherapy zvinoratidzwawo pakurapa myasthenia gravis kuitira kusimbisa mhasuru, kugadzirisa mwero wekufamba, kufema uye kudzivirira hutachiona hwekufema.