Zvese Zvaunofanirwa Kuziva Nezve Porphyria Cutanea Tarda

Zvemukati

• Zviratidzo
• Mifananidzo ye porphyria cutanea tarda
• Zvinokonzera
• Njodzi zvinhu
• Zviitiko
• Kuongorora
• Kurapa
• Outlook

Mhedziso

Porphyria cutanea tarda (PCT) rudzi rwe porphyria kana kusagadzikana kweropa kunokanganisa ganda. PCT ndeimwe yemhando dzakajairika dze porphyria. Iyo dzimwe nguva inonzi kune colloquially sevampire chirwere. Izvi zvinodaro nekuti vanhu vane chirwere ichi vanowanzo kusangana nezviratidzo zvichitevera kupenya kwezuva.

Zviratidzo

Mazhinji ezviratidzo zve porphyria cutanea tarda anoonekwa paganda. Zviratidzo zvakajairika zvinosanganisira:

• mhoni paganda rakafumurwa kuzuva, kusanganisira maoko, kumeso, nemaoko
• photosensitivity, zvinoreva kuti ganda rako rinonzwisisa zuva
• ganda rakatetepa kana risina kusimba
• kuwedzera bvudzi kukura, kazhinji pachiso
• kubvaruka uye kupora kweganda
• kutsvuka, kuzvimba, kana kuchenesa kweganda
• maronda anokura mushure mekukuvara kudiki paganda
• hyperpigmentation, zvinoreva kuti zvigamba zveganda zvinozosviba
• weti yakasviba kupfuura zvakajairwa kana tsvuku shava
• kukuvara kwechiropa

Mushure mokunge mablisters aumba paganda rako, ganda rinogona kubuda. Zvakajairikawo kuti vanga riwone kana mablister apora.

Hyperpigmentation zvigamba zvinowanzoonekwa kumeso, maoko, uye mutsipa.

Mifananidzo ye porphyria cutanea tarda

Zvinokonzera

Porphyria cutanea tarda inogona kukonzerwa nezvinhu zvakasiyana. Izvo zvikonzero zvinowanzo kuverengerwa semajini kana kuwanikwa.

Izvo zvinowanzoitika zvikonzero zvinosanganisira:

• nhoroondo yemhuri ye porphyria cutanea tarda
• kushayiwa nhaka kwechiropa enzyme uroporphyrinogen decarboxylase
• nhoroondo yemhuri yechirwere chechiropa kana gomarara rechiropa
• yakawedzera chiropa simbi kupfuura zvakajairwa

Zvikonzero zvakajairika kuwanikwa zvinosanganisira:

• kunwa doro
• uchishandisa estrogen therapy
• kushandisa mishonga yekudzivirira mukanwa
• kuratidzwa kune zvimwe zvakatipoteredza zvinhu kana makemikari, akadai seAgent Orange
• kutora simbi yakawandisa
• kusvuta
• kuva nehepatitis C
• kuva neHIV

Mune zvimwe zviitiko, hazviite kuti uone chinokonzera porphyria cutanea tarda.

Njodzi zvinhu

Iwe uri panjodzi yakakwira ye porphyria cutanea tarda kana ukasvuta kana kushandisa doro. Iwe zvakare unokwanisa kuwana mamiriro aya kana uine hepatitis C kana HIV.

Kufumurwa kune mamwe makemikari, akadai seAgent Orange, kunogona zvakare kuwedzera njodzi yako. Iwe unogona kunge wakambosangana nekemikari iyi kana uri murwi wakamboshanda munzvimbo yaive neAgent Orange.

Zviitiko

Porphyria cutanea tarda inogona kukanganisa vese varume nevakadzi. Inowanzoonekwa mushure memakore makumi matatu, saka hazvisi zvakajairika pakati pevana kana vechidiki.

Porphyria cutanea tarda inokanganisa vanhu kutenderera pasirese uye haina kuganhurirwa kune imwe nharaunda kana nyika. Zvinofungidzirwa kuti munhu mumwe pavanhu zviuru gumi kusvika makumi maviri nezvishanu ane chirwere ichi.

Kuongorora

Chiremba wako anogona kuongorora muviri, kutarisa zviratidzo, uye kunyora nhoroondo yako yekurapa. Uye zvakare, ivo vanogona kushandisa anotevera bvunzo kuti vaone porphyria cutanea tarda:

• kuongororwa ropa
• weti bvunzo
• zvituru bvunzo
• ganda biopsy

Chiremba anozotarisa ako mazinga e porphyrin uye chiropa enzymes. Kuongorora genetic kunogona kukurudzirwa kune vanhu vane nhoroondo yemhuri yeichi chiitiko.

Kurapa

Iyo kurapwa kwe porphyria cutanea tarda inotarisa mukugadzirisa uye kumisa zviratidzo. Mararamire shanduko, senge kudzora kunwa doro uye kwete kusvuta, zvinogona kubatsira.

Kazhinji kurapa sarudzo dzinosanganisira:

• phlebotomy, kunova kubviswa kweropa kudzikisa iron
• chloroquine (Aralen)
• hydroxychloroquine (Plaquenil)
• mishonga inorwadza
• iron chelators
• kurapa zvirwere zvinokonzeresa porphyria cutanea tarda, senge HCV kana HIV

Phlebotomy ndeimwe yemishonga inowanzozivikanwa ye porphyria cutanea tarda. Mahwendefa eantimalarial anowanzo shandiswa.

Zvakajairika mararamiro ehupenyu kurapa porphyria cutanea tarda anosanganisira:

• kudzivisa doro
• kusasvuta
• kudzivisa chiedza chezuva
• kushandisa sunscreen
• kudzivisa kukuvara paganda
• kwete kutora estrogens

Iwe ungatofanira kupfeka sunscreen, maoko marefu, uye ngowani kunzvenga zuva.

Porphyria cutanea tarda inogona kuwedzera njodzi yekenza yechiropa kana cirrhosis, inova scarring yechiropa. Ichi ndicho chikonzero zvakakosha kuti usanwe doro kana uine mamiriro aya.

Outlook

Porphyria cutanea tarda kazhinji inobata vanhu vakuru vane makore anodarika makumi matatu. Chirwere cheropa chinonyanya kubata ganda. Ganda rako rinogona kutarisisa kuzuva, saka ungangoda kutora matanho ekuwedzera kudzivirira zuva. Blisters yakajairika kubva pane ino mamiriro.

Chiremba wako anogona kukurudzira akasiyana marapirwo eporphyria cutanea tarda. Phlebotomy uye mapiritsi ekurwisa marariya ndiwo maitiro akasarudzika ekurapa.

Kana iwe uchitsvaga rutsigiro, tarisa ino yakamisikidzwa runyorwa rweakanakisa ganda kusagadzikana mablog egore.