Munyori: Lewis Jackson
Zuva Rekusika: 7 Chivabvu 2021
Gadziridza Zuva: 1 Chikunguru 2024
Anonim
Idiopathic Pulmonary Fibrosis - pathophysiology, signs and symptoms, investigation and treatment
Vhidhiyo: Idiopathic Pulmonary Fibrosis - pathophysiology, signs and symptoms, investigation and treatment

Zvemukati

Pulmonary fibrosis chiitiko chinokonzeresa kupora kwemapapu uye kuomarara. Izvi zvinoita kuti zvinetse kufema. Inogona kudzivirira muviri wako kubva pakuwana yakakwana oxygen uye inogona kupedzisira yakonzera kufema kutadza, moyo kutadza, kana zvimwe zvinonetsa.

Vatsvaguri parizvino vanotenda kuti musanganiswa wekuratidzwa nemapapu anogumbura semamwe makemikari, kusvuta, uye hutachiona, pamwe nemageneti uye maitiro ezvirwere zvemuviri, zvinoita basa rakakosha mupulmonary fibrosis.

Yakambofungidzirwa kuti mamiriro acho aikonzerwa nekuzvimba. Zvino masayendisiti anotenda kuti pane kurapa kusingaenzanisike mumapapu ayo anotungamira kukuvara. Iko kuumbwa kwekukosha kwemapapu kwekupedzisira kunopedzisira kwaita pulmonary fibrosis.

Ndezvipi zviratidzo zve pulmonary fibrosis?

Iwe unogona kunge uine pulmonary fibrosis kwenguva yakati pasina zviratidzo. Kufema kwekufema kazhinji ndicho chiratidzo chekutanga chinotanga.

Zvimwe zviratidzo zvinogona kusanganisira:

  • yakaoma, yekukosora chikosoro icho chisingaperi (kwenguva refu)
  • kushaya simba
  • kuneta
  • kumonera nzara, iyo inonzi klubbing
  • kuonda
  • chipfuva kusagadzikana

Sezvo mamiriro acho achiwanzo kubata vanhu vakuru, zviratidzo zvekutanga zvinowanzo kupihwa zvisirizvo nezera kana kushomeka kwekurovedza muviri.


Zviratidzo zvako zvinogona kuita sezvidiki pakutanga uye kufambira mberi nekufamba kwenguva. Zviratidzo zvinogona kusiyana kubva kune mumwe munhu kuenda kune mumwe. Vamwe vanhu vane pulmonary fibrosis vanorwara nekukurumidza.

Chii chinokonzeresa pulmonary fibrosis?

Zvinokonzera pulmonary fibrosis inogona kukamurwa muzvikamu zvakati:

  • autoimmune hosha
  • zvirwere
  • kusvibiswa kwezvakatipoteredza
  • mishonga
  • idiopathic (isingazivikanwe)
  • genetics

Zvirwere zvekuzvidzivirira

Zvirwere zvinodzivirira muviri zvinokonzeresa immune system yako kuzvirwisa. Mamiriro ekuzvidzivirira ega anogona kutungamira pulmonary fibrosis anosanganisira:

  • rheumatoid arthritis
  • lupus erythematosus, iyo inowanzozivikanwa se lupus
  • scleroderma
  • polymyositis
  • dermatomyositis
  • vasculitis

Zvirwere

Aya anotevera marudzi ehutachiona anogona kukonzera pulmonary fibrosis:

  • hutachiona hutachiona
  • hutachiona hutachiona, hunokonzerwa nehepatitis C, adenovirus, herpes virus, uye mamwe mavhairasi

Kuratidzwa kwezvakatipoteredza

Kujekesa kune zvinhu zviri munharaunda kana nzvimbo yebasa kunogona zvakare kubatsira kune pulmonary fibrosis. Semuenzaniso, utsi hwefodya hune makemikari mazhinji anogona kukuvadza mapapu ako uye oendesa kune ino mamiriro.


Zvimwe zvinhu zvinogona kukuvadza mapapu ako zvinosanganisira:

  • asbestosi tambo
  • guruva rezviyo
  • silica guruva
  • mamwe magasi
  • radiation

Mishonga

Mimwe mishonga inogona zvakare kusimudzira njodzi yako yekukudziridza pulmonary fibrosis. Kana iwe ukatora mumwe wemishonga iyi nguva dzose, ungangoda kunyatso tariswa nachiremba wako.

  • chemotherapy zvinodhaka, zvakadai se cyclophosphamide
  • mishonga inorwisa mabhakitiriya, yakadai senitrofurantoin (Macrobid) uye sulfasalazine (Azulfidine)
  • mishonga yemwoyo, senge amiodarone (Nexterone)
  • biologic mishonga yakadai saadalimumab (Humira) kana etanercept (Enbrel)

Idiopathic

Muzviitiko zvakawanda, iyo chaiyo inokonzeresa yemapulmonary fibrosis mukusazivikanwa. Kana zvirizvo, mamiriro acho anonzi idiopathic pulmonary fibrosis (IPF).

Sekureva kweAmerican Lung Association, vanhu vazhinji vane pulmonary fibrosis vane IPF.

Genetics

Sekureva kwePulmonary Fibrosis Foundation, inenge 3 kusvika ku20 muzana yevanhu vane IPF vane imwe nhengo yemhuri ine pulmonary fibrosis. Muzviitiko izvi, inozivikanwa seyemhuri pulmonary fibrosis kana yemhuri yemukati pneumonia.


Vatsvakurudzi vakabatanidza mamwe majeni nemamiriro acho, uye kutsvagurudza nezve iro basa genetics rinotamba kuri kuenderera.

Ndiani ari panjodzi ye pulmonary fibrosis?

Iwe unowanzo kuve unowanikwa uine pulmonary fibrosis kana iwe:

  • varume
  • vari pakati pemakore makumi mana kusvika makumi manomwe
  • vane nhoroondo yekusvuta
  • uve nenhoroondo yemhuri yemamiriro acho
  • vane autoimmune kusagadzikana kwakabatana nemamiriro acho
  • vatora mimwe mishonga inosanganisirwa nechirwere ichi
  • vakarapwa cancer, kunyanya chest radiation
  • shanda mune basa rine hukama nenjodzi yakawedzera, senge kuchera, kurima, kana kuvaka

Pulmonary fibrosis inoonekwa sei?

Pulmonary fibrosis ndeimwe yemhando dzinopfuura mazana maviri dzezvirwere zvemapapu zviripo. Nekuti kune akawanda akasiyana marudzi ezvirwere zvemapapu, chiremba wako anogona kunetseka kuziva kuti pulmonary fibrosis ndiyo inokonzera zviratidzo zvako.

Mune ongororo yakaitwa nePulmonary Fibrosis Foundation, 55 muzana yevakabvunzwa vakataura kuti vakaonekwa zvisirizvo pane imwe nguva. Mhedzisiro yakajairwa zvakanyanya yaive asthma, pneumonia, uye bronchitis.

Kushandisa nhungamiro dzazvino uno, zvinofungidzirwa kuti vaviri muvatatu varwere vane pulmonary fibrosis vanogona kunyatso kuongororwa pasina bhiopsy.

Nokubatanidza ruzivo rwako rwechiremba uye mhedzisiro yeimwe mhando yeCT scan yechipfuva, chiremba wako anozonyanya kukuongorora.

Mumamiriro ezvinhu apo kuongororwa kwacho kusiri kujeka, sampuro yeshutu, kana biopsy, inogona kudikanwa.

Kune nzira dzinoverengeka dzekuita yekuvhiya yemapapu biopsy, saka chiremba wako anokurudzira kuti ndeipi nzira yakakunakira iwe.

Chiremba wako anogona zvakare kushandisa akasiyana siyana maturusi kuti aongorore pulmonary fibrosis kana kutonga kunze mamwe mamiriro. Izvi zvinogona kusanganisira:

  • kupomba oximetry, bvunzo isinga tsvete yeropa rako reokisijeni mazinga
  • kuongororwa kweropa kutsvaga autoimmune zvirwere, hutachiona, uye kupererwa neropa
  • arterial yeropa gasi bvunzo kuti unyatso kuongorora iwo oxygen mazinga muropa rako
  • samputum sampu yekutarisa zviratidzo zvehutachiona
  • pulmonary function bvunzo kuyera mapapu ako
  • iyo echocardiogram kana yemoyo kushushikana bvunzo kuti uone kana dambudziko remwoyo riri kukonzera zviratidzo zvako

Inorapwa sei pulmonary fibrosis?

Chiremba wako haakwanise kudzosera mabara emapapu, asi vanogona kukuraira mishonga yekubatsira kunatsiridza kufema kwako uye kunonoka kufambira mberi kwechirwere.

Mishonga iripazasi mimwe mienzaniso yesarudzo dzazvino dzinoshandiswa kugadzirisa pulmonary fibrosis:

  • kuwedzera okisijeni
  • prednisone kudzvinyirira immune system yako uye kudzikisira kuzvimba
  • azathioprine (Imuran) kana mycophenolate (CellCept) kudzvinyirira immune system yako
  • pirfenidone (Esbriet) kana nintedanib (Ofev), mishonga inorwisa mabhakitiriya inodzivirira maitiro ekupwanya mumapapu.

Chiremba wako anogona zvakare kukurudzira pulmonary kugadzirisa. Uku kurapwa kunosanganisira chirongwa chekurovedza muviri, dzidzo, uye rutsigiro kukubatsira iwe kudzidza kufema zviri nyore.

Chiremba wako anogona zvakare kukukurudzira iwe kuti uchinje mararamiro ako. Shanduko idzi dzinogona kusanganisira zvinotevera:

  • Iwe unofanirwa kudzivirira hutsi hwefodya uye kutora matanho ekusiya kana uchisvuta. Izvi zvinogona kubatsira kunonoka kufambira mberi kwechirwere uye kurerutsa kufema kwako.
  • Idya kudya kwakanyatsonaka.
  • Tevera chirongwa chekurovedza muviri chakagadzirwa nachiremba wako.
  • Zorora zvakakwana uye dzivisa kunetseka zvakanyanya.

Kuiswa kwemapapu kunogona kukurudzirwa kune avo vari pasi pemakore makumi matanhatu nemashanu vane chirwere chakakomba.

Ndeupi maonero evanhu vane pulmonary fibrosis?

Chiyero icho pulmonary fibrosis mavanga mapapu evanhu anosiyana. Iyo yekuvhunika haina kudzoserwa, asi chiremba wako anogona kukurudzira kurapwa kuti uderedze mwero uriko mamiriro ako ekuenderera.

Mamiriro acho anogona kukonzera kuwanda kwezvinetso, kusanganisira kutadza kufema. Izvi zvinoitika kana mapapu ako asisashande mushe uye vasingakwanise kuwana oxygen yakakwana muropa rako.

Pulmonary fibrosis inomutsawo njodzi yako yekenza yemapapu.

Matipi ekudzivirira

Zvimwe zviitiko zve pulmonary fibrosis zvinogona kunge zvisingadziviririke. Zvimwe zviitiko zvakabatanidzwa kune zvakatipoteredza uye zvehunhu zvinhu zvine njodzi zvinogona kudzorwa. Tevedza aya matipi ekudzora njodzi yako yekuwana chirwere:

  • Dzivisa kusvuta.
  • Dzivisa utsi hwefodya.
  • Pfeka chifukidzo kumeso kana chimwe chinhu chekufema kana ukashanda munzvimbo ine makemikari anokuvadza.

Kana iwe uchinetseka kufema, ita musangano nachiremba wako. Kuongororwa kwekutanga uye kurapwa kunogona kuvandudza kutaridzika kwenguva refu kwevanhu vane zvirwere zvakawanda zvemapapu, kusanganisira pulmonary fibrosis.

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