Munyori: Roger Morrison
Zuva Rekusika: 27 Gunyana 2021
Gadziridza Zuva: 1 Chikumi 2025
Anonim
Fanconi chirwere - Utano
Fanconi chirwere - Utano

Zvemukati

Fanconi syndrome chirwere chisingawanzoitika cheitsvo dzinotungamira mukuunganidzwa kweshuga, bicarbonate, potasium, phosphates uye mamwe akawandisa amino acids mumurini. Muchirwere ichi mune zvakare kurasikirwa kweprotein mumuti uye weti inova yakasimba uye iwedzere kuva acidic.

Hereditary Fanconi Syndrome inokonzeresa shanduko dzinoitika kubva kuna baba kuenda kumwanakomana. Kana iri Akawana Fanconi syndrome, kunwa simbi dzinorema, dzakadai semutobvu, kumedza mishonga inorwisa mabhakitiriya yakapera, vhitamini D kushomeka, kuisirwa itsvo, myeloma yakawanda kana amyloidosis zvinogona kutungamira mukukura kwechirwere.

Fanconi Syndrome haina mushonga uye kurapwa kwayo kunosanganisira kutsiva izvo zvinhu zvakarasika mumuti, zvinoratidzwa nephrologist.

Zviratidzo zveFanconi Syndrome

Zviratidzo zveFanconi Syndrome zvinogona kuva:

  • Kuita weti yakawanda weti;
  • Weti yakasimba uye ine acidic;
  • Nyota kwazvo;
  • Kupera mvura mumuviri;
  • Pfupi;
  • Yakakwira acidity muropa;
  • Kushaya simba;
  • Kurwadziwa kwepfupa;
  • Kofi-mukaka mavara ane zvigamba paganda;
  • Kusavapo kana kuremara mune zvigumwe;

Kazhinji, hunhu hweFanconi Syndrome nhaka inoonekwa muhudiki pamakore mashanu ezera.


O kuongororwa kweFanconi Syndrome inoitwa zvichibva nezviratidzo, kuongororwa kweropa kunoratidza acidity yakakwira uye bvunzo yeweti inoratidza yakawandisa glucose, phosphate, bicarbonate, uric acid, potasium uye sodium.

Kurapa kweFanconi Syndrome

Kurapa kweFanconi Syndrome kunovavarira kuwedzera izvo zvinhu zvakaraswa nevanhu mune weti. Kune izvi, zvinogona kuve zvakafanira kuti varwere vatore potasium, phosphate uye vhitamini D yekuwedzera, pamwe nesodium bicarbonate yekushayisa ropa acidosis.

Mune varwere vane kukomba kwakakomba kwetsvo, kuiswa kweitsvo kunoratidzwa.

Zvinobatsira zvinongedzo:

  • Zvokudya zvine potassium
  • Zvikafu zvakapfuma muvhitamini D
  • Itsvo Kuisazve

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