Goodpasture syndrome: chii icho, zviratidzo, zvinokonzera uye kurapwa
Zvemukati
Goodpasture Syndrome chirwere chisingawanzoitika mumuviri, umo masero ekudzivirira emuviri anorwisa itsvo nemapapu, zvichinyanya kukonzeresa zviratidzo sekukosora kweropa, kunetseka kufema uye kurasikirwa neropa mumurini.
Ichi chirwere chinoitika nekuda kwekuvapo kwema antibodies anorwisa maseru eitsvo nemapapu. Zvimwe zvinhu zvinoita sekunge zvinowedzera mukana wekukura kwechirwere ichi ndezvinoti: kuva nenhoroondo yechirwere uye kuputa fodya, kuva nehutachiona hwekufema zvakare uye kusangana nekufemerwa kwezvinhu zvakaita semethane kana propane, semuenzaniso.
Kurapa kunoenderana nekushandiswa kwemishonga yakadai seyemunosuppressants uye corticosteroids, asi muzviitiko zvakanyanya, plasmapheresis kana hemodialysis inogona kudikanwa.
Zviratidzo zvikuru
Zviratidzo zvikuru zveGoodpasture Syndrome ndezvi:
- Kuneta zvakanyanya;
- Kukosora ropa;
- Kunetseka kufema;
- Kurwadziwa kana kufema;
- Kuwedzera kweiyo urea muropa;
- Kuvapo kweropa uye / kana furo mune weti;
- Kusvira paunenge uchiita weti.
Kana zviratidzo zvikaonekwa, zvinokurudzirwa kutsvaga kurapwa nekukurumidza kuitira bvunzo uye chiratidzo chekurapwa kwakanyanya, sezvo zviratidzo zvingatonyanya kana chirwere chikasarapwa nekukurumidza.
Uye zvakare, zvimwewo zvirwere zvinogona kunge zvine zviratidzo zvakafanana nezvechirwere ichi, senge Wegener's granulomatosis, iyo inoita kuti kuongororwa kuome. Ziva zviratidzo uye maitiro ekurapa Wegener's granulomatosis.
Maitiro ekusimbisa kuongororwa
Kuti uone chirwere cheGoodpasture's, chiremba achaongorora nhoroondo yako yehutano uye hurefu hwezviratidzo zvako. Ipapo, chiremba anogona kuraira kumwe kuyedzwa, kwakadai sekuongororwa kweropa uye neweti, kuti aone masoja ekudzivirira muviri anogadzirwa nemuviri anokonzera Goodpasture's syndrome.
senge itsvo biopsy, kunova kubviswa kwechikamu chidiki cheitsvo yenyama, kuti uone kana paine masero anokonzera Goodpasture's syndrome.
Uye zvakare, chiremba anogona zvakare kuraira kumwe kuyedzwa, senge itsvo biopsy, iyo inosanganisira kubvisa chidimbu chidiki cheitsvo yenyuchi inozoongororwa murabhoritari, kuti uone kana paine masero anokonzera Goodpasture's syndrome.
X-ray uye CT scans inogona zvakare kurairwa nachiremba wako kuti aone kukuvara kwemapapu. Ona zvimwe zvakawanda nezvekuti computed tomography inoitwa sei.
Zvinogona kukonzerwa
Chikonzero cheGoodpasture's syndrome chakakonzerwa nema anti-GBM antibodies anorwisa NC-1 chikamu cherudzi IV collagen muitsvo nemapapu maseru.
Ichi chirwere chinoratidzika kunge chakajairika kuvarume kupfuura vakadzi, vari pakati pemakore makumi maviri nemakumi matatu ekuberekwa, uye nevanhu vane ganda rakareruka. Pamusoro pezvo, kuiswa kumakemikari akaita semushonga wezvipembenene, utsi hwefodya, uye hutachiona hunokonzerwa nemavhairasi zvimwe zvinhu zvinoita sekunge zvinowedzera mukana wekukura kwechirwere, sezvo zvichikonzera maseru ekudzivirira emuviri kurwisa mapapu nemapapu.
Kurapwa kunoitwa sei
Kurapa kweGoodpasture's Syndrome kunowanzoitwa kuchipatara uye kunoenderana nekushandiswa kwemishonga yekudzivirira muviri uye corticosteroids, izvo zvinodzivirira maseru ekudzivirira emuviri kubva mukuparadza itsvo nemapapu.
Mune zvimwe zviitiko, kurapwa neplasmapheresis kunoratidzwa, inova nzira inozadza ropa uye kupatsanura masoja ekudzivirira anokuvadza kuitsvo nemapapu. Kana itsvo dzakakanganiswa zvakanyanya, hemodialysis kana kuisirwa itsvo kunogona kudikanwa. Zvirinani unzwisise kuti plasmapheresis chii uye kuti zvinoitwa sei.