Zviratidzo zvehemophilia, sei kuongororwa uye kusahadzika kunowanzoitika

Zvemukati

• Mhando dzehemophilia
• Hemophilia zviratidzo
• Maitiro ekusimbisa kuongororwa
• Mibvunzo yakajairika nezve hemophilia
• 1. Hemophilia yakajairika muvarume here?
• 2. Ko hemophilia inogara nhaka here?
• 3. Hemophilia inopararira here?
• 4. Munhu ane hemophilia anogona here kuva neupenyu hwakajairika?
• 5. Ndiani ane hemophilia anogona kutora ibuprofen?
• 6. Munhu ane hemophilia anokwanisa here kutora maTatoo kana kuvhiyiwa?

Hemophilia chirwere chemagene uye chekugara nhaka, ndiko kuti, chinopfuudzwa kubva kuvabereki kuenda kuvana, chinozivikanwa nekubuda ropa kwenguva refu nekuda kwekushomeka kana kuderera kwezviitiko zveVIII neIX muropa, izvo zvakakosha pakuvhara.

Nekudaro, kana paine shanduko dzine chekuita nema enzymes aya, zvinokwanisika kuti pane ropa rinobuda, rinogona kunge riri remukati, nekubuda ropa mazino, mhuno, weti kana mutsvina, kana kupwanya pamuviri, semuenzaniso.

Kunyangwe pasina mushonga, hemophilia ine kurapwa, kunoitwa nemajekiseni epanguva nenguva nechinhu chinogwamba chiri kushomeka mumuviri, kudzivirira kubuda kweropa kana pese panobuda ropa, zvinoda kugadziriswa nekukurumidza. Nzwisisa kuti kurapwa kwehemophilia kunofanirwa kunge kuri sei.

Mhando dzehemophilia

Hemophilia inogona kuitika munzira mbiri, iyo, kunyangwe iine zviratidzo zvakafanana, zvinokonzerwa nekushaikwa kwezvikamu zvakasiyana zveropa:

• Hemophilia A:ndiyo mhando yakajairika yehemophilia, inozivikanwa nekushomeka mucoagulation factor VIII;
• Hemophilia B:inokonzeresa shanduko mukugadzirwa kwecoagulation factor IX, uye inozivikanwa seChristmas chirwere.

Coagulation zvinhu mapuroteni aripo muropa, ayo anogadzirwa pese panotsemuka muropa, kuitira kuti kubuda ropa kuvemo. Naizvozvo, vanhu vane hemophilia vanotambura nekubuda ropa izvo zvinotora nguva yakareba kuti zvidzorwe.

Iko kushomeka mune zvimwe zvinokonzeresa, izvo zvinokonzeresa kubuda ropa uye zvinogona kuvhiringidzika nehemophilia, senge kushomeka kwechikonzero XI, inozivikanwa senge rudzi C hemophilia, asi iyo inosiyana nemhando yekushandurwa kwemajini uye fomu yekutapurirana.

Hemophilia zviratidzo

Zviratidzo zvehemophilia zvinogona kuzivikanwa marogo mumakore ekutanga emwana ekuzvarwa, zvisinei anokwanisa kuzivikanwa panguva yekuyaruka, kuyaruka kana kuva munhu mukuru, kunyanya pazviitiko apo hemophilia inoenderana nekuderera kwezviitiko zvekugwamba. Nekudaro, izvo zvakakosha zviratidzo nezviratidzo zvinogona kunge zvichiratidza hemophilia ndeizvi:

• Kuonekwa kwemavara epepuru paganda;
• Kuzvimba uye kurwadziwa mumajoini;
• Kuzvimba kubuda ropa, pasina chikonzero chiri pachena, senge mune chingamu kana mhino, semuenzaniso;
• Kubuda ropa panguva yekuzvarwa kwemazino ekutanga;
• Kubuda ropa kwakaoma kumira mushure mekucheka kuri nyore kana kuvhiyiwa;
• Maronda anotora nguva yakareba kuti apore;
• Kuwedzeredza uye kwenguva refu kuenda kumwedzi.

Rwakanyanya kukura rudzi rwehemophilia, hunowanda huwandu hwezviratidzo uye nekukurumidza kwadzinobva, nekudaro, hemophilia yakaoma inowanzo kuwanikwa mumwana, mumwedzi yekutanga yehupenyu, nepo zvine mwero hemophilia inowanzo fungidzirwa mukati memwedzi mishoma yekutanga hupenyu makore mashanu, kana mwana paanotanga kufamba nekutamba.

Hunyoro hemophilia, kune rimwe divi, inogona kuwanikwa chete mukukura, kana munhu achinge atambura nekurohwa kwakasimba kana mushure mekurapwa senge kubviswa kwezino, uko kubuda ropa kunoonekwa pamusoro pechinyakare.

Maitiro ekusimbisa kuongororwa

Kuongororwa kwehemophilia kunoitwa mushure mekuongororwa nachiremba wehematologist, uyo anokumbira bvunzo dzinoongorora kugona kweropa, senge nguva yekugwamba, inoongorora nguva inotora kuti ropa riite ganda, uye kuyerwa kwekuvapo kwezvinhu yekugwamba uye huwandu hwayo muropa.

Kuvhara zvinhu kwakakosha mapuroteni eropa, ayo anouya mukutamba kana paine kubuda ropa, kuabvumira kuti amire. Kushaikwa kwechimwe chezvinhu izvi kunokonzeresa chirwere, semhando A hemophilia, iyo inokonzerwa nekusavapo kana kuderera kwechinhu VIII, kana mhando B hemophilia, mune icho chinhu IX chakashomeka. Nzwisisa mashandiro anoita coagulation.

Mibvunzo yakajairika nezve hemophilia

Mimwe mibvunzo yakajairika nezve hemophilia ndeiyi:

1. Hemophilia yakajairika muvarume here?

Hemophilia inoshomeka coagulation zvinhu zviripo pane X chromosome, iyo yakasarudzika muvarume uye yakadzokororwa muvakadzi. Nekudaro, kuti ave nechirwere, murume anongoda kugamuchira 1 akabatwa X chromosome, kubva kuna amai, nepo kuti mukadzi ave nechirwere ichi, anofanirwa kugamuchira maviri akachinjika echromosomes, uye, nekudaro, chirwere ichi chinowanzoitika varume.

Kana mukadzi ane 1 chete akabata X chromosome, yakagara nhaka kubva kune chero mubereki, anozove mutakuri, asi haazove nechirwere, sezvo imwe X chromosome inobhadharira hurema, zvisinei, ine 25% mukana wekuva nemwana chirwere ichi.

2. Ko hemophilia inogara nhaka here?

Mune angangoita makumi matatu muzana ezviitiko zvehemophilia, hapana nhoroondo yemhuri yechirwere, icho chinogona kunge chiri mhedzisiro yekushanduka kwemajini muDNA yemunhu. Panyaya iyi, zvinofungidzirwa kuti munhu akawana hemophilia, asi kuti anogona kunge achikwanisa kutapurira chirwere kuvana vake, sekungofanana neumwe munhu ane hemophilia.

3. Hemophilia inopararira here?

Hemophilia haina kutapukira, kunyangwe paine kusangana chaiko neropa remunhu anotakura kana kunyangwe kuwedzerwa ropa, sezvo izvi zvisingakanganise kuumbwa kweropa remunhu wega wega kuburikidza nemongo wepfupa.

4. Munhu ane hemophilia anogona here kuva neupenyu hwakajairika?

Paunenge uchitora kurapwa kwekudzivirira, pamwe nekutsiva kwekugwamba, munhu ane hemophilia anogona kuve nehupenyu hwakajairika, kusanganisira kutamba mitambo.

Pamusoro pekurapwa kwekudzivirira tsaona, kurapwa kunogona kuitwa kana paine kubuda ropa, kuburikidza nejekiseni yezvinhu zvinogwambisa ropa, izvo zvinofambisa kugwamba kweropa uye zvinodzivirira kubuda kukuru kweropa, kuri kuitwa zvinoenderana nekutungamira kwehematologist.

Pamusoro pezvo, pese panenge munhu achizoita imwe nzira yekuvhiya, kusanganisira kutora mazino uye kuzadza, semuenzaniso, zvinodikanwa kuita madosi ekudzivirira.

5. Ndiani ane hemophilia anogona kutora ibuprofen?

Mishonga yakadai seIbuprofen kana iine acetylsalicylic acid mukuumbwa kwayo haifanire kunwiwa nevanhu vanoonekwa vaine hemophilia, sezvo iyi mishonga inogona kupindira pakuvhara kweropa uye kufarira kuitika kweropa, kunyangwe kana chinhu chinovhara chikaiswa.

6. Munhu ane hemophilia anokwanisa here kutora maTatoo kana kuvhiyiwa?

Iye munhu akawanikwa aine hemophilia, zvisinei nemhando uye kuomarara, anogona kuwana maTattoos kana maitiro ekuvhiya, zvisinei kurudziro ndeyekutaura mamiriro ako kune nyanzvi uye nekupa iyo coagulant chinhu pamberi pemaitiro, kudzivirira kubuda kukuru kweropa, semuenzaniso.

Uye zvakare, mune yekuwana matattoo, vamwe vanhu vane hemophilia vakashuma kuti kurapa uye marwadzo mushure mekuitwa kwacho aive mashoma pavakazora chinhu vasati vatora nyora. Izvo zvakare zvakakosha kuti utarise chinzvimbo chinogadziriswa neANVISA, chakachena uye chisina kuchena uye chakachena zvinhu, tichidzivirira chero njodzi yematambudziko.