Nhaka fructose kusawirirana

Hereditary fructose kusashivirira chirwere umo munhu achishaya protein inodikanwa kuputsa fructose. Fructose ishuga yemichero inowanzoitika mumuviri. Yakagadzirwa nevanhu fructose inoshandiswa seinotapira muzvikafu zvakawanda, zvinosanganisira chikafu chevana uye zvinwiwa.

Ichi chiitiko chinoitika kana muviri uchishaya enzyme inonzi aldolase B. Chinhu ichi chinodiwa kuputsa fructose.

Kana munhu asina chinhu ichi achidya fructose kana sucrose (nzimbe kana beet shuga, tafura yeshuga), yakaoma makemikari shanduko inoitika mumuviri. Muviri haugone kuchinja mafomu akachengetwa eshuga (glycogen) kuita glucose. Nekuda kweizvozvo, shuga yeropa inodonha uye zvinhu zvine njodzi zvinowanda muchiropa.

Hereditary fructose kusagadzikana inogara nhaka, zvinoreva kuti inogona kupfuudzwa kuburikidza nemhuri. Kana ivo vaviri vabereki vakatakura kopi isingashande yealdolase B geni, mumwe nemumwe wevana vavo ane 25% (1 mu4) mukana wekubatwa.

Zviratidzo zvinogona kuonekwa mushure mekunge mwana atanga kudya chikafu kana fomula.

Zviratidzo zvekutanga zve fructose kusashivirira zvakafanana neya galactosemia (kutadza kushandisa shuga galactose). Gare gare zviratidzo zvine chekuita nechiropa chirwere.

Zviratidzo zvinogona kusanganisira:

• Kugwinha
• Kurara zvakanyanya
• Kushatirwa
• Ganda jena kana vachena vemeso (jaundice)
• Kusadya zvakanaka uye kukura semucheche, kutadza kukura
• Matambudziko mushure mekudya michero uye zvimwe zvekudya zvine fructose kana sucrose
• Kusvipa

Kuongorora kwepanyama kunogona kuratidza:

• Yakawedzera chiropa uye spleen
• Jaundice

Miedzo inosimbisa kuongororwa inosanganisira:

• Ropa rekuvhara miedzo
• Ropa shuga bvunzo
• Enzyme inodzidza
• Kuongorora genetic
• Itsvo basa rekuyedza
• Chiropa basa bvunzo
• Chiropa biopsy
• Uric acid yeropa bvunzo
• Kuongorora urinal

Ropa shuga ichave yakaderera, kunyanya mushure mekugamuchira fructose kana sucrose. Uric acid mazinga achave akakwirira.

Kubvisa fructose uye sucrose kubva kuchikafu mushonga unoshanda kune vanhu vazhinji. Matambudziko anogona kurapwa. Semuenzaniso, vamwe vanhu vanogona kutora mushonga kudzikisa uric acid muropa ravo uye kudzikisa njodzi yavo yegout.

Hereditary fructose kusagadzikana inogona kunge iri nyoro kana yakaoma.

Kudzivisa fructose uye sucrose kunobatsira vana vazhinji vane mamiriro aya. Kufungidzira kwakanaka mune dzakawanda kesi.

Vana vashoma vane fomu yakakomba yechirwere vanozoita chirwere chakakomba chechiropa. Kunyangwe kubvisa fructose uye sucrose kubva kuchikafu kunogona kutadzisa chirwere chakakomba chechiropa muvana ava.

Kuita zvakanaka kwemunhu kunoenderana ne:

• Inokurumidza sei kuongororwa kunoitwa
• Inguvai pfupi fructose uye sucrose inogona kubviswa kubva kuchikafu
• Iyo enzyme inoshanda sei mumuviri

Aya matambudziko anogona kuitika:

• Kudzivisa chikafu chine fructose nekuda kwemhedzisiro yavo
• Kubuda ropa
• Gout
• Kurwara kubva pakudya chikafu chine fructose kana sucrose
• Chiropa kutadza
• Shuga shoma yeropa (hypoglycemia)
• Kufenda
• Rufu

Fonera wako mupi wezvehutano kana mwana wako akatanga zviratidzo zveichi chiitiko mushure mekutanga kudya. Kana mwana wako aine chirwere ichi, nyanzvi dzinokurudzira kuona chiremba uyo anonyanya kugadzirisa biochemical genetics kana metabolism.

Vakaroorana vane nhoroondo yemhuri yekusagadzikana kwefructose vanoshuvira kuve nemwana vanogona kufunga nezve kuraira kwemajini.

Mazhinji mhedzisiro inokuvadza yechirwere inogona kudzivirirwa nekudzikira fructose uye sucrose kudya.

Fructosemia; Kusagadzikana kweFructose; Fructose aldolase B-kushomeka; Fructose-1, 6-bisphosphate aldolase kushomeka

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