Munyori: Virginia Floyd
Zuva Rekusika: 13 Nyamavhuvhu 2021
Gadziridza Zuva: 22 Chikumi 2024
Anonim
Optic Nerve Glioma
Vhidhiyo: Optic Nerve Glioma

Gliomas mamota anokura munzvimbo dzakasiyana dzeuropi. Optic gliomas inogona kukanganisa:

  • Imwe kana ese maviri emitsipa yemaziso inotakura ruzivo rwekuona kuuropi kubva paziso rega rega
  • Iyo optic chiasm, iyo nzvimbo iyo maziso emaziso anodungamidzana pamberi peiyo hypothalamus yeuropi

Optic glioma inogona zvakare kukura pamwe neiyo hypothalamic glioma.

Optic gliomas hazviwanzo. Chikonzero che optic gliomas hachizivikanwe. Mazhinji optic gliomas ari kunonoka-kukura uye asiri ecancerous (benign) uye anoitika muvana, kazhinji nguva dzose asati asvika makore makumi maviri. Kazhinji kesi dzinoonekwa nemakore mashanu ezera.

Kune hukama hwakasimba pakati pe optic glioma uye neurofibromatosis mhando 1 (NF1).

Zviratidzo zvinokonzerwa nebundu rinokura uye kumanikidza pa-optic nerve uye zvivakwa zviri padyo. Zviratidzo zvinogona kusanganisira:

  • Kusazvibata yeziso reziso
  • Kunze kuputika kweumwe kana ese maziso
  • Kuchema
  • Kuona kurasikirwa mune rimwe kana maviri maziso anotanga nekurasikirwa neoneya uye pakupedzisira kunotungamira kuhupofu

Mwana anogona kuratidza zviratidzo zve diencephalic syndrome, iyo inosanganisira:


  • Kurara masikati
  • Kupera kwendangariro uye kushanda kwehuropi
  • Kutemwa nemusoro
  • Kunonoka kukura
  • Kurasikirwa kwemafuta emuviri
  • Kusvipa

Uropi uye huta hurongwa (neurologic) bvunzo inoratidza kurasikirwa kwemaonero mune rimwe kana ese maziso. Panogona kunge paine shanduko mumutsipa wemaziso, unosanganisira kuzvimba kana kupora kwetsinga, kana kuchena uye kukuvara kwe disc disc.

Bundu rinogona kuwedzera kusvika munzvimbo dzakadzika dzehuropi. Panogona kuve nezviratidzo zvekuwedzera kumanikidzwa muuropi (intracranial pressure). Panogona kuve nezviratidzo zveeurofibromatosis mhando 1 (NF1).

Iyi bvunzo inotevera inogona kuitwa:

  • Cerebral angiography
  • Kuongororwa kwetishu kubviswa kubva bundu panguva yekuvhiya kana CT scan-inotungamirwa biopsy kuratidza iyo bundu mhando
  • Musoro CT scan kana MRI yemusoro
  • Kuona munda bvunzo

Kurapa kunosiyana nehukuru hwebundu uye hutano hwese hwemunhu. Chinangwa chingave chekurapa kusagadzikana, kubvisa zviratidzo, kana kugadzirisa maonero uye kunyaradza.


Kuvhiya kubvisa bundu kunorapa mamwe ma optic gliomas. Kusarura kwakasarudzika kudzikisa saizi yebundu kunogona kuitwa mune dzakawanda zviitiko. Izvi zvinochengetedza bundu kubva mukukuvadza zvakajairika maturusi maturusi akarikomberedza. Chemotherapy inogona kushandiswa mune vamwe vana. Chemotherapy inogona kunyanya kubatsira kana bundu racho richiwedzera kupinda mu hypothalamus kana kana chiratidzo chave chakashatiswa nekukura kwebundu.

Radiation therapy inogona kukurudzirwa mune zvimwe zviitiko apo bundu riri kukura kunyangwe chemotherapy, uye kuvhiyiwa hakugoneke. Mune zvimwe zviitiko, kurapwa nemwaranzi kunogona kunonoka nekuti bundu iri rinononoka kukura. Vana vane NF1 kazhinji havagamuchire radiation nekuda kwemhedzisiro.

Corticosteroids inogona kunyoreswa kudzikisira kuzvimba uye kuzvimba panguva ye radiation radiation, kana kana zviratidzo zvichidzoka.

Masangano anopa rutsigiro uye rumwe ruzivo anosanganisira:

  • Yevana Oncology Boka - www.childrensoncologygroup.org
  • Neurofibromatosis Network - www.nfnetwork.org

Maonero acho akasiyana zvakanyanya kumunhu wega wega. Kurapa kwekutanga kunovandudza mukana wemhedzisiro yakanaka. Kuchenjerera kuteedzesa neboka rekutarisira rakasangana nemhando iyi yebundu kwakakosha.


Kana chiono chikarasika kubva mukukura kwetumaziso, zvinogona kusadzoka.

Kazhinji, kukura kwebundu kunononoka, uye mamiriro acho anoramba akadzikama kwenguva refu. Zvisinei, bundu rinogona kuramba richikura, saka rinofanira kutariswa zvakanyanya.

Fonera wako mupi wezvehutano nezve chero kurasikirwa kwekuona, kurwadziwa kusinga ziso, kana zvimwe zviratidzo zveichi chiitiko.

Genetic counselling inogona kurairwa kune vanhu vane NF1. Kugara uchiongorora maziso kunogona kubvumidza kuongororwa kwekutanga kwemamota aya asati aunza zviratidzo.

Glioma - optic; Optic tsinga glioma; Vechidiki pilocytic astrocytoma; Gomarara repfungwa - optic glioma

  • Neurofibromatosis I - yakawedzera optic foramen

Eberhart CG. Ziso uye ocular adnexa. Mune: Goldblum JR, Mwenje LW, McKenney JK, Myers JL, eds. Rosai naAckerman's Surgical Pathology. 11th ed. Philadelphia, PA: Elsevier; 2018: chits.

Goodden J, Mallucci C. Optic nzira hypothalamic gliomas. Mune: Winn HR, ed. Youmans uye Winn Neurological Kuvhiya. 7th ed. Philadelphia, PA: Elsevier; 2017: chitsiko 207.

Olitsky SE, Marsh JD. Kusagadzikana kweiyo optic nerve. Mune: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Chinyorwa chePediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chap 649.

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