Biliary atresia

Biliary atresia kuvhara mukati memachubhu (ducts) anotakura mvura inonzi bile kubva kuchiropa kusvika kune nduru.

Biliary atresia inoitika kana iyo ducts mukati kana kunze kwechiropa isina kujairika, yakavharika, kana kusavapo. Iyo bile ducts inotakura chirwere chekugaya kubva kuchiropa kuenda mudiki ura kuputsa mafuta uye kusefa tsvina kubva mumuviri.

Chikonzero chechirwere hachisi pachena. Inogona kunge iri nekuda kwe:

• Utachiona hutachiona mushure mekuzvarwa
• Kuratidzirwa kune zvinhu zvine chepfu
• Multiple genetic zvinhu
• Kukuvara kwepainatal
• Mimwe mishonga yakadai secarbamazepine

Iyo inowanzo bata vanhu vekuEast Asia neAfrican-American dzinza.

Iyo bile ducts inobatsira kubvisa marara kubva muchiropa uye kutakura munyu unobatsira dumbu ura kuputsa (kugaya) mafuta.

Mune vacheche vane biliary atresia, bile inoyerera kubva pachiropa ichienda kune nduru yakavharwa. Izvi zvinogona kutungamira kukuvara kwechiropa uye cirrhosis yechiropa, izvo zvinogona kuuraya.

Zviratidzo zvinowanzotanga kuitika pakati pemasvondo maviri kusvika masere. Jaundice (yero yeruvara kune ganda uye mamukisi membranes) inokura zvishoma zvishoma mavhiki maviri kusvika matatu mushure mekuzvarwa. Mucheche anogona kuwedzera uremu kazhinji kwemwedzi wekutanga. Mushure meizvozvo, mwana anodzikira huremu uye oshatirwa, uye achange ave nekuwedzera jaundice.

Zvimwe zviratidzo zvinogona kusanganisira:

• Weti yakasviba
• Dumbu rakazvimba
• Zvinonhuwirira uye zvituru zvinoyangarara
• Pale kana chevhu-chitsvuku zvituru
• Kunonoka kukura

Anokuchengetedza hutano anotora nhoroondo yezvechiremba yemwana wako uye ozoongorora muviri kuti aone chiropa chakawedzerwa.

Miedzo yekuongorora biliary atresia inosanganisira:

• Abdominal x-ray kutarisa kuwedzerwa chiropa uye spleen
• Abdominal ultrasound kutarisa nhengo dzemukati
• Ropa bvunzo kuti uone yakazara uye yakananga bilirubin mazinga
• Hepatobiliary scintigraphy kana HIDA scan kuti uone kana iyo bile ducts uye nduru iri kushanda nemazvo
• Chiropa biopsy kutarisa kuomarara kwecirrhosis kana kutonga zvimwe zvikonzero zvejaundice
• X-ray yema bile ducts (cholangiogram) kutarisa kana maburi eb bile akavhurwa kana akavharwa

Kuvhiya kunodaidzwa kuti maitiro eKasai kunoitwa kubatanidza chiropa neura hutumbu. Nzira dzisina kujairika dzakapfuura. Kuvhiya kunonyanya kubudirira kana kukaitwa mwana asati ave nemavhiki masere ekuberekwa.

Chiropa chekuisa chinogona kuchiri kudikanwa pamberi pemakore makumi maviri ekuberekwa mune mazhinji emakesi.

Kuvhiyiwa kwekutanga kunovandudza kupona kweanopfuura chetatu chevacheche vane chirwere ichi. Iyo yakareba-nguva kubatsirwa kwechiropa kuisirwa haisati yazivikanwa, asi inotarisirwa kuvandudza kupona.

Zvinetso zvinogona kusanganisira:

• Utachiona
• Isingachinjiki cirrhosis
• Chiropa kutadza
• Matambudziko ekuvhiya, kusanganisira kutadza kweKasai maitiro

Fonera wako mupi kana mwana wako achioneka jaundiced, kana kana zvimwe zviratidzo zve biliary atresia zvichikura

Jaundice vacheche - biliary atresia; Achangoberekwa jaundice - biliary atresia; Extrahepatic ductopenia; Kufambira mberi kwekuparadzanisa cholangiopathy

• Achangoberekwa jaundice - buditsa
• Achangoberekwa jaundice - chii kubvunza chiremba wako

• Biri rakagadzirwa muchiropa

Berlin SC. Kufungidzira kufungidzira kweanaonate. Mune: Martin RJ, Fanaroff AA, Walsh MC, eds. Fanaroff naMartin's Neonatal-Perinatal Mushonga. 11th ed. Philadelphia, PA: Elsevier; 2020: chitsiko 38.

Cazares J, Ure B, Yamataka A. Biliary atresia. Mune: Holcomb GW, Murphy JP, St. Peter SD, eds. Holcomb uye Ashcraft's Pediatric Kuvhiya. 7th ed. Philadelphia, PA: Elsevier; 2020: chitsiko 43.

Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC. Cholestasis. Mune: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Chinyorwa chePediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chitsiko 383.

O'Hara SM. Chirwere chevana uye spleen. Mu: Rumack CM, Levine D, eds. Kuongorora Ultrasound. 5 ed. Philadelphia, PA: Elsevier; 2018: chits. 51.