Munyori: William Ramirez
Zuva Rekusika: 20 Gunyana 2021
Gadziridza Zuva: 1 Chikunguru 2024
Anonim
An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Vhidhiyo: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias idiki, yakawedzera tsinga dzeropa paganda. Kazhinji hazvikuvadzi, asi zvinogona kusanganiswa nezvirwere zvinoverengeka.

Telangiectasias inogona kukura chero mukati memuviri. Asi ivo vanoonekwa zviri nyore kwazvo paganda, mucous membranes, uye vachena vemeso. Kazhinji, hazvikonzere zviratidzo. Mamwe telangiectasias akabuda ropa uye anokonzera matambudziko akakura. Telangiectasias inogona zvakare kuitika muuropi kana ura uye inokonzeresa matambudziko makuru kubva mukubuda ropa.

Zvinokonzera zvinogona kusanganisira:

  • Rosacea (dambudziko reganda rinokonzeresa kumeso kutsvuka)
  • Kukwegura
  • Dambudziko nemajini
  • Kubata pamuviri
  • Kubuda kwezuva
  • Varicose tsinga
  • Kunyanyisa kushandisa steroid makirimu
  • Kushungurudzika kunharaunda

Zvirwere zvinosanganiswa nemamiriro aya zvinosanganisira:

  • Ataxia-telangiectasia (chirwere chinokanganisa ganda, chiyero nekubatana, uye dzimwe nzvimbo dzomuviri)
  • Bloom syndrome (chirwere chakagarwa nhaka chinokonzera chimiro chipfupi, kunzwisisika kweganda kumwaranzi yezuva, uye kutsvuka kwechiso)
  • Cutis marmorata telangiectatica congenita (hosha yeganda inokonzeresa zvigamba zvetsvuku)
  • Hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu chirwere)
  • Klippel-Trenaunay-Weber syndrome (chirwere chinokonzera port-waini tsvina, varicose veins, uye zvinyoro zvinyama zvinetso)
  • Nevus flammeus senge chiteshi chewaini-waini
  • Rosacea (mamiriro eganda anokonzera kutsvuka kwechiso)
  • Sturge-Weber chirwere (chirwere chinosanganisira chiteshi chewaini-waini uye matambudziko ehurongwa)
  • Xeroderma pigmentosa (chirwere umo ganda pamwe chete nemucheka unovhara ziso zvinonyanya kutaridzika kune ultraviolet mwenje)
  • Lupus (immune system chirwere)
  • CREST syndrome (rudzi rwe scleroderma iyo inosanganisira kuwanda kwemavara-akafanana neturu mukati meganda uye kumwe kunhu mumuviri uye inokuvadza maseru anoteedzera madziro etsinga diki)

Fonera wako mupi wezvehutano kana iwe ukaona yakawedzera midziyo muganda, mucous membranes, kana maziso.


Iye mupi achaita bvunzo dzepanyama uye obvunza nezve zviratidzo zvako, zvinosanganisira:

  • Midziyo yeropa iripi?
  • Vanobuda ropa zviri nyore uye pasina chikonzero here?
  • Ndezvipi zvimwe zviratidzo zviripo?

Miedzo inogona kudikanwa kuti uongorore kana kutonga kunze kwehutano mamiriro. Miedzo inogona kusanganisira:

  • Kuongororwa kweropa
  • CT inoongorora
  • Chiropa chinoshanda zvidzidzo
  • MRI inoongorora
  • X-ray

Sclerotherapy kurapwa kwetelangiectasias pamakumbo. Mune maitiro aya, sarine (munyu) mhinduro kana imwe kemikari inojowa yakanangana mutsinga dzebanga pamakumbo. Laser kurapwa inowanzo shandiswa kurapa telangiectasias yechiso.

Vascular ectasias; Spider angioma

  • Angioma serpiginosum
  • Telangiectasia - makumbo
  • Telangiectasias - ruoko rwekumusoro

Kelly R, Baker C. Zvimwe zvinetso zvevascular. Mune: Bolognia JL, Schaffer JV, Cerroni L, eds. Dermatology. 4th ed. Philadelphia, PA: Elsevier; 2018: chits. 106.


Patterson JW. Vascular mamota. Mune: Patterson JW, ed. Weedon's Ganda Pathology. 4th ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: chitsiko 38.

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