Munyori: Janice Evans
Zuva Rekusika: 1 Chikunguru 2021
Gadziridza Zuva: 13 Chivabvu 2024
Anonim
Cystic Fibrosis - Ivacaftor Part 1
Vhidhiyo: Cystic Fibrosis - Ivacaftor Part 1

Zvemukati

Ivacaftor inoshandiswa kurapa mamwe marudzi ecystic fibrosis (chirwere chinozvarwa chinokonzeresa matambudziko nekufema, kugaya, uye kubereka) muvanhu vakuru nevana vana vane makore mana zvichikwira. Ivacaftor inofanira kushandiswa chete muvanhu vane mamwe maitiro ekugadzira. Chiremba wako anogona kuraira kuongororwa kweropa kuti ubatsire kusarudza kana mushonga uyu wakanakira iwe. Ivacaftor iri mukirasi yemishonga inonzi cystic fibrosis transmembrane conductance regulator (CFTR) potentiators. Inoshanda nekuvandudza mashandiro eprotein mumuviri kudzikisira kuvaka kwemukati mamota mumapapu nekuvandudza zvimwe zviratidzo zvecystic fibrosis.

Ivacaftor inouya sehwendefa uye semaguneti kutora nemuromo. Inowanzo kutorwa nezvakakora zvine mafuta kaviri pazuva, maawa gumi nemaviri akaparadzana. Tora ivacaftor kwakatenderedza nguva dzakafanana mazuva ese. Tevedza zvinongedzo pane yako tsamba yekunyora zvakanyatsonaka, uye bvunza chiremba wako kana wemishonga kuti atsanangure chero chikamu chausinganzwisise. Tora ivacaftor chaizvo sezvakarairwa. Usatore zvimwe kana zvishoma nezvayo kana kuitora kakawanda pane zvakatemwa nachiremba wako.


Kugadzirira dhizaini yeivacaftor granules, sanganisa iyo packet yeganuanu mu 1 teaspoon (5 mL) yechando kana tembiricha yemukamuri chikafu chisina kunyorova kana mvura yakaita seyogati, applesauce, mvura, mukaka, fomura yemwana, mukaka wemuzamu, kana muto. Tora musanganiswa mukati me1 awa yekusanganisa granules nechikafu kana mvura.

Tora yega yega ivacaftor nechikafu chine mafuta senge mazai, bota, nzungu ruomba, chizi pizza, zvigadzirwa zvemukaka wakazara (semukaka wese, chizi, uye yogati), fomura yemwana, uye mukaka wemuzamu. Taura nachiremba wako nezve zvimwe zvekudya zvine mafuta zvekudya neivacaftor.

Ivacaftor inodzora cystic fibrosis asi hairape. Ramba uchitora ivacaftor kunyangwe iwe uchinzwa zvakanaka. Usarega kutora ivacaftor usina kutaura nachiremba wako.

Kumbira wemishonga wako kana chiremba kopi yemashoko emugadziri wemurwere.

Mushonga uyu unogona kupihwa zvimwe zvinoshandiswa; bvunza chiremba wako kana wemishonga kuti uwane rumwe ruzivo.

Usati watora ivacaftor,

  • udza chiremba wako uye wemishonga kana uri weergergic kune ivacaftor, chero mimwe mishonga, kana chero chinosanganisa mumapiritsi eivacaftor. Kumbira wako wemishonga kuti uwane runyorwa rwezvigadzirwa.
  • udza chiremba wako uye wemishonga kuti ndeipi imwe mishonga yekunyorera uye isina kunyoreswa, mavitamini, zvekuwedzera zvinovaka muviri, zvauri kutora kana kuronga kutora. Ive neshuwa yekutaura chero eanotevera: mamwe maantibhakitiriya akadai clarithromycin (Biaxin, muPrevPac), erythromycin (EES, E-Mycin, Ery-Tab, Erythrocin), uye telithromycin (Ketek); mamwe maantifungal akadai fluconazole (Diflucan), itraconazole (Onmel, Sporanox), ketoconazole (Nizoral), posaconazole (Noxafil), uye voriconazole (Vfend); cyclosporine (Gengraf, Neoral, Sandimmune); digoxin (Lanoxin); mimwe mishonga yekubatwa kwakadai se carbamazepine (Carbatrol, Epitol, Tegretol, vamwe), phenobarbital, uye phenytoin (Dilantin, Phenytek); midazolam; rifabutin (Mycobutin); rifampin (Rifadin, muRifamate, muRifater, Rimactane); tacrolimus (Astagraf, Prograf), kana warfarin (Coumadin, Jantoven). Chiremba wako angangoda kushandura madosi emishonga yako kana kukutarisisa nokungwarira mhedzisiro. Mimwe mishonga yakawanda inogona zvakare kudyidzana neivacaftor, saka ive shuwa kuudza chiremba wako nezve yese mishonga yauri kutora, kunyangwe iyo isinga oneke pane ino chinyorwa
  • udza chiremba wako kuti ndezvipi zvigadzirwa zvemakwenzi zvauri kutora, kunyanya St. John's wort.
  • udza chiremba wako kana iwe wakambove kana wakambove nechiropa kana itsvo chirwere.
  • udza chiremba wako kana iwe uri nepamuviri, ronga kuve nepamuviri, kana uri kuyamwisa. Kana iwe ukava nepamuviri uchitora ivacaftor, fonera chiremba wako.
  • iwe unofanirwa kuziva kuti ivacaftor inogona kukuita dzungu. Usatyaire mota kana kushandisa michina kusvikira iwe waziva kuti uyu mushonga unokubata sei.

Usadye grapefruit kana orenji eSeville kana kunwa muto wemazambiringa uchinwa mushonga uyu.


Kana iwe uchirangarira iro rakarasika dhizaini mukati maawa matanhatu yenguva iwe yawakarongerwa kuitora, tora iyo yakarasika dosi ipapo ipapo nechikafu chine mafuta. Nekudaro, kana anopfuura maawa matanhatu apfuura apfuura kubva panguva yakatarwa, ruka iro rakarasika dhizaini uye enderera yako yenguva dzose dosing purogiramu. Usatore dosi yakapetwa kaviri kuti uwane imwe yakarasika.

Ivacaftor inogona kukonzera mhedzisiro. Udza chiremba wako kana chimwe chezviratidzo izvi chakanyanya kana kuti chisingaendi:

  • musoro
  • mapundu
  • kurwadza kwemajoini
  • muromo uye huro kurwadziwa
  • fivha, huro, kurwadziwa, kana zvimwe zviratidzo zvehutachiona
  • manyoka
  • dzungu

Mimwe mhedzisiro inogona kuve yakakomba. Kana iwe ukasangana nechimwe cheizvi zviratidzo, danaidza chiremba wako nekukasira:

  • kusvotwa
  • kurutsa
  • kurasikirwa nenzara
  • kurwadziwa kumusoro kwepamusoro chikamu chedumbu
  • weti yakasviba
  • kuneta zvakanyanya
  • kubuda ropa zvisina kujairika kana kupwanya
  • yero yeganda kana maziso
  • maonero anochinja

Ivacaftor inogona kuwedzera njodzi yekuti iwe kana mwana wako muve necartar. Taura nachiremba wako kana chiremba wemwana wako nezve njodzi dzekutora mushonga uyu.


Ivacaftor inogona kukonzera mamwe mhedzisiro. Fonera chiremba wako kana uine chero matambudziko asina kujairika uchitora mushonga uyu.

Kana iwe ukawana chakakomba mhedzisiro, iwe kana chiremba wako ungatumira chirevo kuchirongwa cheKudya neDrug Administration's (FDA) MedWatch Yakashata Chiitiko Chirongwa online (http://www.fda.gov/Safety/MedWatch) kana nefoni ( 1-800-332-1088).

Chengetedza iyi mishonga mumudziyo iyo yakauya mukati, yakasungwa yakavharwa, uye isingasvike kune vana. Zvichengetedze pane tembiricha yemukati uye kure nekupisa kwakanyanya uye hunyoro (kwete muchimbuzi).

Izvo zvakakosha kuti chengetedza mishonga yese isingaonekwe uye kusvika kwevana semidziyo yakawanda (senge vhiki nevhiki mapiritsi epfungwa uye ayo emadonhwe eziso, makirimu, zvigamba, uye inhalers) hazvirambe vana uye vana vadiki vanogona kuvhura zviri nyore. Kuchengetedza vana vadiki kubva kune chepfu, gara wakavharira makapu ekuchengetedza uye nekukurumidza isa mishonga munzvimbo yakachengeteka - imwe iri kumusoro uye kure uye kubva kwavari uye kusvika. http://www.upandaway.org

Mishonga isingadiwe inofanirwa kuraswa nenzira dzakakosha kuona kuti zvipfuyo, vana, nevamwe vanhu havagone kuzvidya. Nekudaro, iwe haufanire kuburitsa uyu mushonga pasi pechimbuzi. Panzvimbo iyoyo, nzira yakanakisa yekurasa mishonga yako ndeyekurapa-kudzosa chirongwa. Taura nachiremba wako kana kuti taura nedhipatimendi rako remarara / rekudzokorora kuti udzidze nezve zvirongwa zvekudzosa munharaunda yako. Ona iyo FDA's Safe Disposal yeMedicine webhusaiti (http://goo.gl/c4Rm4p) kuti uwane rumwe ruzivo kana iwe usina mukana wekutora-kudzoka chirongwa.

Kana zvikaitika zvekudarika, fonera iyo chepfu yekudzora rubatsiro pa1-800-222-1222. Ruzivo rwunowanikwawo online pa https://www.poisonhelp.org/help. Kana munhu akabatwa akadonha, akabatwa nepfari, achinetseka kufema, kana kutadza kumutswa, pakarepo danaidza mabasa ekukurumidzira pa911.

Zviratidzo zvekuwedzeredza zvinogona kusanganisira zvinotevera:

  • dzungu
  • manyoka

Chengetedza zvese zvakagadzwa nachiremba wako uye murabhoritari. Chiremba wako acharaira kuongororwa kwemaziso uye kumwe kuongororwa kwelebhu usati uye panguva yekurapwa kwako kuti utarise mhinduro yemuviri wako kune ivacaftor.

Usarega mumwe munhu achitora mushonga wako. Kumbira wemishonga wako chero mibvunzo yauinayo nezvekuzadza tsamba yako.

Izvo zvakakosha kuti iwe uchengete yakanyorwa rondedzero yeese emushonga uye asiri ekunyora (pamusoro-e-pikisheni) mishonga yauri kutora, pamwe nezvimwe zvigadzirwa zvakaita sevhitamini, zvicherwa, kana zvimwe zvekuwedzera zvekudya. Iwe unofanirwa kuuya nerondedzero iyi iwe nguva imwe neimwe paunoshanyira chiremba kana kana iwe uchigamuchirwa kuchipatara. Izvo zvakare zvakakosha ruzivo kutakura newe kana zvikaitika zvechimbi-chimbi.

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Yekupedzisira Yakagadziridzwa - 11/15/2020

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