Munyori: Frank Hunt
Zuva Rekusika: 19 Kurume 2021
Gadziridza Zuva: 13 Nyamavhuvhu 2025
Anonim
Chii chinonzi Leber congenital amaurosis uye maitiro ekurapa - Utano
Chii chinonzi Leber congenital amaurosis uye maitiro ekurapa - Utano

Zvemukati

Leber congenital amaurosis, inozivikanwawo se ACL, Leber's syndrome kana Leber nhaka nhaka optic neuropathy, chirwere chisingawanzoitika chinodzora chinokonzeresa shanduko zvishoma nezvishoma mumagetsi emagetsi, rinova iro ziso reziso rinoona mwenje neruvara, zvichikonzera kurasikirwa kwakanyanya kwekuona kubva pakuzvarwa uye mamwe matambudziko eziso, akadai senzwi kuchiedza kana keratoconus, semuenzaniso.

Kazhinji, mwana ane chirwere ichi haaratidze zviratidzo zvichiwedzera kana kudzikira kwekuona nekufamba kwenguva, asi anochengetedza huwandu hwakaganhurirwa hwekuona, uhwo, kazhinji, hunongobvumidza kufamba kwepedyo, maumbirwo uye shanduko mukuvhenekera.

Leber congenital amaurosis haina mushonga, asi magirazi akasarudzika uye dzimwe nzira dzekugadzirisa dzinogona kushandiswa kuyedza kuvandudza kuona uye hupenyu hwehupenyu. Kazhinji, vanhu vane zviitiko zvechirwere ichi mumhuri, vanofanirwa kuita zvemajini kuraira vasati vaedza kubata pamuviri.

Kurapa uye kurarama nechirwere

Leber akaberekwa Amaurosis haatonyanya kuwedzera pamusoro pemakore uye, nekudaro, mwana anokwanisa kuchinjira padanho rekuona pasina matambudziko mazhinji. Nekudaro, mune dzimwe nguva, zvingave zvinokurudzirwa kushandisa akakosha magirazi kuyedza kuwedzera zvishoma mwero wekuona.


Mune zviitiko apo kuona kwakaderera kwazvo, zvinogona kubatsira kudzidza braille, kukwanisa kuverenga mabhuku, kana kushandisa imbwa inotungamira kufamba famba mumugwagwa, semuenzaniso.

Uye zvakare, chiremba wevana anogona zvakare kukurudzira kushandiswa kwemacomputer akagadziridzwa kune vanhu vane zvakaderera kuona, kuitira kufambisa kukura kwemwana uye kubvumidza kudyidzana nevamwe vana. Rudzi urwu rwechigadzirwa runonyanya kubatsira kuchikoro, kuitira kuti mwana adzidze nhanho imwechete sevezera rake.

Zviratidzo zvikuru uye maitiro ekuziva

Zviratidzo zveLeber yekuzvarwa amaurosis yakajairika kutenderera gore rekutanga zera uye inosanganisira:

  • Zvakaoma kubata zvinhu zviri padyo;
  • Zvakaoma kuziva zvimiro zvinozivikanwa kana vasipo;
  • Kufamba kusingaoneki kwemaziso;
  • Hypersensitivity kune mwenje;
  • Pfari;
  • Kunonoka mukusimudzira mota.

Ichi chirwere hachigone kuzivikanwa panguva yekuzvitakura, uye hachikonzere shanduko mukuumbwa kweziso. Nenzira iyoyo, chiremba wevana kana ophthalmologist anogona kuita bvunzo dzinoverengeka kubvisa dzimwe fungidziro dzinogona kunge dzichikonzera zviratidzo.


Chero pese panenge paine fungidziro yematambudziko ekuona mumwana, zvinokurudzirwa kubvunza chiremba wevana kuti aite bvunzo dzekuona, senge electroretinography, kuti aone dambudziko uye kutanga kurapwa kwakakodzera.

Nzira yekuwana sei chirwere

Ichi chirwere chekugara nhaka uye, nekudaro, chinopfuudzwa kubva kuvabereki kuenda kuvana.Nekudaro, kuti izvi zviitike, vese vabereki vanofanirwa kuve nechirwere chirwere, uye hazvisi zvekumanikidzwa kuti chero mubereki ave nechirwere.

Nekudaro, zvakajairika kuti mhuri dzisaratidze zviitiko zvechirwere kumazera akati wandei, sezvo paine 25% chete yekupararira kwechirwere.

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