Munyori: Laura McKinney
Zuva Rekusika: 7 Kubvumbi 2021
Gadziridza Zuva: 22 Chikumi 2024
Anonim
Bhuruu Mucheche Syndrome - Utano
Bhuruu Mucheche Syndrome - Utano

Zvemukati

Mhedziso

Bhuruu mucheche chirwere mamiriro ezvinhu vamwe vacheche vanozvarwa vaine kana kukura pakutanga kwehupenyu. Inotaridzwa neruzhinji rweganda bhuruu nebhuruu kana yepepuru tinge, inonzi cyanosis.

Uku kuratidzika kwebhuruu kunoonekwa zvakanyanya apo ganda rakatetepa, senge miromo, nzeve, uye mibhedha yezvipikiri. Blue baby syndrome, nepo isingawanzo kuitika, inogona kuitika nekuda kweakawanda akaberekwa (zvichireva zviripo pakuzvarwa) kukanganisa kwemoyo kana zvakatipoteredza kana magene.

Chii chinokonzera blue baby syndrome?

Mwana anotora bhuruu nekuda kweropa risina mweya. Kazhinji, ropa rinosvinirwa kubva pamoyo kuenda kumapapu, kwarinogamuchira oxygen. Ropa rinotenderera richidzoka kuburikidza nemoyo uyezve nemuviri wese.

Kana paine dambudziko nemoyo, mapapu, kana ropa, ropa rinogona kunge risina oxygen zvakanaka. Izvi zvinokonzera ganda kutora bhuruu bhuru. Kushaikwa kwe oxygenation kunogona kuitika nekuda kwezvikonzero zvakati.

Tetralogy yeKunyepera (TOF)

Kunyange iri isingawanzo kuberekwa yemoyo hurema, TOF ndiyo inonyanya kukonzera bhuruu mucheche chirwere. Chaizvoizvo mubatanidzwa wezvakakanganiswa nemoyo zvina izvo zvinogona kudzikisa kuyerera kweropa kuenda kumapapu uye kubvumira oxygen-isina ropa kuyerera kubuda mumuviri.


TOF inosanganisira mamiriro akaita kunge uine gomba pamadziro rinopatsanura ma ventricle ekuruboshwe uye kurudyi emoyo uye mhasuru inokanganisa kuyerera kweropa kubva kurudyi ventricle kuenda mupulmonary, kana mapapu, tsinga.

Methemoglobinemia

Aya mamiriro anobva kunitrate chepfu. Izvo zvinogona kuitika muvacheche vanopihwa fomura yemucheche yakasanganiswa nemvura yakanaka kana chikafu chevacheche chakagadzirwa nezvikafu zvine nitrate, senge sipinashi kana beet.

Mamiriro acho anowanzoitika muvacheche vari pasi pemwedzi mitanhatu yekuberekwa. Kana uyu mudiki, vacheche vane maturakiti ane huta uye asina kugadzikana emudumbu, ayo ari mukana wekushandura nitrate kuita nitrite. Sezvo nitrite inotenderera mumuviri, inogadzira methemoglobin. Nepo methemoglobin iine okisijeni-yakapfuma, haiburitse iyo oxygen muropa. Izvi zvinopa vacheche vane mamiriro avo bluish hue.

Methemoglobinemia inogona zvakare kuve isingaite yekuberekwa.

Kumwe kuberekwa kwemoyo kuremara

Genetics inokonzeresa zvakanyanya kuberekwa kwemoyo kuremara. Semuenzaniso, vacheche vanozvarwa vaine Down syndrome vanowanzove nematambudziko emoyo.


Nyaya dzine hutano hwemadzimai, senge iri pasi uye isina kudzorwa mhando 2 chirwere cheshuga, zvinogona zvakare kukonzera mucheche achikura hurema hwemwoyo.

Zvimwe zvinokanganisa moyo zvinokonzerwawo pasina chikonzero chakajeka zvachose. Izvo chete mashoma ekuzvarwa kwemoyo kuremara anokonzera cyanosis.

Ndezvipi zviratidzo?

Mukuwedzera kune bhuruu ruvara rweganda, zvimwe zviratidzo zveblue baby syndrome zvinosanganisira:

  • kugumbuka
  • kuneta
  • nyaya dzekudyisa
  • kutadza kuwedzera uremu
  • nyaya dzekuvandudza
  • kukurumidza kurova kwemoyo kana kufema
  • kirubhu (kana kutenderera) minwe nezvigunwe

Inoonekwa sei?

Kunze kwekutora nhoroondo yezvekurapa uye kuita bvunzo dzepanyama, chiremba wevana wemwana wako anogona kuita bvunzo dzinoverengeka. Aya maedzo anobatsira kuona chikonzero cheblue baby syndrome. Miedzo inogona kusanganisira:

  • kuongororwa ropa
  • X-ray yechipfuva yekuongorora mapapu uye kukura kwemoyo
  • electrocardiogram (EKG) kutarisa mashandiro emagetsi emoyo
  • echocardiogram kuti uone maitiro emoyo
  • catheterization yemoyo yekufungidzira arteri yemoyo
  • oxygen saturation test kuti uone kuti yakawanda sei oxygen iri muropa

Inorapwa sei?

Kurapa kunoenderana nechikonzero cheblue baby syndrome. Kana mamiriro acho akagadzirwa nehutachiona hwemwoyo, mwana wako angangoda kuvhiyiwa pane imwe nguva.


Mishonga inogona kukurudzirwa zvakare. Aya mazano anotsamira pakuomarara kwekukanganisa. Vacheche vane methemoglobinemia vanogona kudzoreredza mamiriro nekutora mushonga unonzi methylene bhuruu, inogona kupa oxygen muropa. Mushonga uyu unoda mushonga uye unowanzoendeswa kuburikidza netsono yakaiswa mutsinga.

Ndingaite sei kudzivirira bhuruu mwana chirwere?

Zvimwe zviitiko zvebhuruu mucheche chirwere chirwere chemusikirwo uye hachigone kudzivirirwa. Zvimwe, zvakadaro, zvinogona kudzivirirwa. Matanho ekutora anosanganisira:

  • Usashandise zvakanaka mvura. Usagadzirire fomura yemwana nemvura yematsime kana kupa vana mvura yakanaka yekunwa kudzamara vapfuura mwedzi gumi nemiviri. Mvura inobikira haibvise nitrate. Nitrate mazinga mumvura haafanire kudarika 10 mg / L. Dhipatimendi rako rezvehutano rinogona kukupa rumwe ruzivo rwekuti ungawana kupi tsime rakaedzwa.
  • Deredza chikafu chine nitrate. Zvikafu zvakapfuma mu nitrate zvinosanganisira broccoli, sipinashi, beet, uye karoti. Deredza mari yaunodyisa mwana wako vasati vava nemwedzi minomwe. Kana iwe ukagadzira wega wega chikafu chevana uye uchifanira kushandisa iyi miriwo, shandisa mazaya pane kutsva.
  • Dzivisa zvinodhaka zvisiri pamutemo, kusvuta, doro, uye mimwe mishonga panguva yekuzvitakura. Kudzivisa izvi kunobatsira kudzivirira kuberekwa kwemoyo kusakwana. Kana uine chirwere cheshuga, ita shuwa kuti inodzorwa-zvakanaka uye kuti uri pasi pekuchengetwa nachiremba.

Ndeapi maonero evana vane chirwere ichi?

Blue baby syndrome chirwere chisingawanzoitika nezvakasiyana zvikonzero. Chiremba wako anogona kuraira chero chinhu kubva pasina kurapwa kwekukurumidza kune kuvhiyiwa. Kuvhiya kunogona kuve nenjodzi huru kana kuchiitwa pane achangozvarwa.

Kamwe chinokonzeresa chikazivikanwa uye chikabudirira kurapwa, vana vazhinji vane bhuruu mwana chirwere vanogona kurarama zvakajairika hupenyu hune mashoma mashoma mhedzisiro.

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