Phenylketonuria Kudya: Yakabvumidzwa, Yakarambidzwa Kudya uye Menyu

Zvemukati

• Chikafu chinotenderwa mu phenylketonuria
• Chikafu chakarambidzwa mu phenylketonuria
• Nhamba ye phenylalanine inobvumidzwa nezera
• Mharidzo menyu
• Semuenzaniso menyu yemwana ane makore matatu ekuberekwa ane phenylketonuria:

Mune chikafu chevanhu vane phenylketonuria zvakakosha kwazvo kudzora kudyiwa kwe phenylalanine, inova amino acid inowanikwa kunyanya muzvikafu zvine mapuroteni, senyama, hove, mazai, mukaka uye zvigadzirwa zvemukaka. Nekudaro, avo vane phenylketonuria vanofanirwa kugara vachiongororwa ropa kuti vaongorore huwandu hwe phenylalanine muropa uye, pamwe chete nachiremba, vanoverenga huwandu hwe phenylalanine iyo yavanogona kumedza mukati mezuva.

Sezvo zvichidikanwa kuti udzivise chikafu chakawanda chine mapuroteni, phenylketonurics inofanirawo kushandisa mapuroteni ekuwedzera pasina phenylalanine, nekuti mapuroteni akakosha zvakanyanya mumuviri, asingakwanise kubviswa zvachose.

Uye zvakare, mukushaikwa kwe phenylalanine kudya, muviri unoda madosi epamusoro e tyrosine, inova imwe amino acid inova yakakosha mukusimudzira mukushaikwa kwe phenylalanine. Neichi chikonzero, zvinowanzo kuve zvakakosha kuti uwedzere ne tyrosine mukuwedzera kune chikafu. Tarisa uone kuti zvimwe zvekuchengetedza zvakakosha pakurapa phenylketonuria.

Chikafu chinotenderwa mu phenylketonuria

Zvikafu zvinobvumidzwa kune vanhu vane phenylketonuria ndeizvi:

• Zvibereko:apuro, peya, vise, mazambiringa, acerola, ndimu, jabuticaba, currant;
• Humwe hupfu: starch, mufarinya;
• Candy: shuga, michero jellies, uchi, sago, cremogema;
• Mafuta: oiri yemiriwo, mafuta echirimwa asina mukaka uye zvigadzirwa;
• Vamwe: candies, lollipops, zvinwiwa zvinwiwa, michero popsicles isina mukaka, kofi, tii, yemiriwo gelatin inogadzirwa negungwa, masardard, mhiripiri.

Kune zvekare zvimwe zvekudya zvinotenderwa phenylketonurics, asi izvo zvinofanirwa kudzorwa. Izvi zvekudya ndezvi:

• Muriwo mune zvese, senge sipinashi, chard, madomasi, manhanga, yamu, mbatatisi, mbatatisi, okra, beet, cauliflower, karoti, chayote.
• Vamwe: mupunga manoni asina mazai, mupunga, coconut mvura.

Uye zvakare, pane akasiyana mavhezheni ezvimisikidzo ane mashoma mashoma e phenylalanine, senge mupunga, hupfu hwegorosi kana pasita, semuenzaniso.

Kunyangwe zvirambidzo zvekudya zvakanaka kune phenylketonurics, kune zvakawanda zvigadzirwa zveindasitiri izvo zvisina phenylalanine mukuumbwa kwavo kana kuti varombo mune iyi amino acid. Nekudaro, mune zvese zviitiko zvakakosha kuti uverenge pane chigadzirwa chigadzirwa kana chiine phenylalanine.

Ona rondedzero izere yezvikafu zvinobvumidzwa uye huwandu hwe phenylalanine.

Chikafu chakarambidzwa mu phenylketonuria

Chikafu chakarambidzwa mu phenylketonuria ndeavo vakapfuma mu phenylalanine, ayo ari kunyanya chikafu chine mapuroteni, akadai se:

• Zvikafu zvemhuka: nyama, hove, hove, mukaka uye nyama zvigadzirwa, mazai, uye nyama zvigadzirwa soseji, soseji, bhekoni, ham.
• Chikafu chemavambo chakatangira: gorosi, nyemba, bhinzi, pizi, nyemba, soya uye zvigadzirwa zvechigadzirwa, chestnuts, walnuts, nzungu, hazelnuts, maarumondi, pistachios, mapaini nzungu;
• Zvinotapira zvine aspartame kana chikafu chine chinozipa ichi;
• Zvigadzirwa zvine chikafu chinorambidzwa, senge makeke, makuki uye chingwa.

Sezvo kudya kwe phenylketonurics kuri kushomeka mu protein, vanhu ava vanofanirwa kutora akakosha ekuwedzera maamino acids ayo asina phenylalanine yekuona kukura kwakakodzera uye kushanda kwemuviri.

Nhamba ye phenylalanine inobvumidzwa nezera

Huwandu hwe phenylalanine hunogona kudyiwa mazuva ese hunosiyana zvichienderana nezera uye huremu, uye kudyiswa kwe phenylketonurics kunofanirwa kuitwa nenzira isingapfuure iyo inobvumidzwa phenylalanine kukosha. Chinyorwa chiri pazasi chinoratidza hunotenderwa hunhu hweiyi amino acid maererano neboka rezera:

• Pakati pemwedzi 0 ne6: 20 kusvika 70 mg / kg pazuva;
• Pakati pemwedzi minomwe uye gore rimwe chete: 15 kusvika 50 mg / kg pazuva;
• Kubva pa1 kusvika pamakore mana ezera: 15 kusvika 40 mg / kg pazuva;
• Kubva pamakore mana kusvika kumanomwe ezera: 15 kusvika 35 mg / kg pazuva;
• Kubva 7 zvichienda mberi: 15 kusvika 30 mg / kg pazuva.

Kana munhu ane phenylketonuria akamedza phenylalanineine chete muhuwandu hwakatenderwa, mota uye kugona kwavo kugona hakukanganisike. Kuti udzidze zvimwe ona: Nzwisisa zvirinani chii Phenylketonuria uye kuti inorapwa sei.

Mharidzo menyu

Menyu yezvikafu zve phenylketonuria inofanira kuve yakasarudzika uye kugadzirirwa neyehutano, sezvo ichifanira kufunga nezvezera remunhu, huwandu hwe phenylalanine inobvumidzwa uye mhedzisiro yekuongororwa kweropa.

Semuenzaniso menyu yemwana ane makore matatu ekuberekwa ane phenylketonuria:

Kushivirira: 300 mg ye phenylalanine pazuva

Izvo zvakakoshawo kuti munhu uye nhengo dzemhuri yavo vatarise pane izvo zvigadzirwa zvinonyora kuti kana chikafu chine phenylalanine kana zvirimo zvirimo, nokudaro kugadzirisa huwandu hwechikafu chinogona kudyiwa.