Yakatemwa porphyria

Zvemukati

• Zviratidzo zvekucheka porphyria
• Kurapa kwepasipo porphyria

Ganda rinononoka porphyria ndiyo mhando inowanzoitika ye porphyria inokonzeresa maronda madiki kuti aoneke paganda rakaiswa kuzuva, senge kuseri kweruoko, kumeso kana kumusoro, nekuda kwekushayikwa kwe enzyme inogadzirwa nechiropa inotungamira kune kuunganidzwa kwesimbi paganda.ropa uye ganda. Cutaneous porphyria haina mushonga, asi inogona kudzorwa nekushandiswa kwemishonga yakatemwa nachiremba.

Kazhinji, kunonoka ganda porphyria kunoonekwa panguva yekukura, kunyanya kune varwere vanogara vachinwa doro kana vane matambudziko echiropa, senge hepatitis C, semuenzaniso.

Late ganda porphyria kazhinji harisi regeneti, zvisinei, mune zvimwe zviitiko rinogona kupfuura kubva kuvabereki kuenda kuvana, uye kurairwa kwemajini kunokurudzirwa usati wava nepamuviri, kana paine zviitiko zvinoverengeka mumhuri.

Zviratidzo zvekucheka porphyria

Chiratidzo chekutanga chechetere porphyria kutaridzika kwemabhuru madiki paganda rakaiswa kuzuva, izvo zvinotora nguva kupora, zvisinei, zvimwe zviratidzo zvinosanganisira:

• Kuwedzeredza kukura kwebvudzi kumeso;
• Ganda rakaomeswa mune dzimwe nzvimbo, senge maoko kana kumeso;
• Kusviba weti.

Mushure mokunge blisters yanyangarika, mavanga kana mavara mavara anogona kuoneka anotora nguva yakareba kupora.

Kuongororwa kwepasina porphyria kunofanirwa kuitwa nachiremba wesvikiro kubudikidza neropa, weti uye kuyedzwa kwendove kusimbisa kuvepo kwe porphyrin mumasero, sezvo chiri chinhu chinogadzirwa nechiropa panguva yechirwere.

Kurapa kwepasipo porphyria

Kurapa kwepasipo porphyria kunofanirwa kutungamirwa nedermatologist mukubatana pamwe nehepatologist, sezvo zvichidikanwa kudzora huwandu hwe porphyrin inogadzirwa nechiropa. Nekudaro, zvinoenderana nezviratidzo zvemurwere, kurapwa kunogona kuitwa nemushonga wepacificy porphyria, senge chloroquine kana hydroxychloroquine, kubvisa ropa nguva dzose kudzikira kwesimbi maseru kana mubatanidzwa wezvose zviri zviviri.

Pamusoro pezvo, panguva yekurapwa zvinokurudzirwa kuti murwere arege kunwa doro uye kusvibiswa nezuva, kunyangwe nehusiku hwezuva, uye nzira yakanakisa yekuchengetedza ganda kubva kuzuva kushandisa mabhurugwa, majuzi ane maoko marefu, ngowani uye magurovhosi, semuenzaniso .