Hugles-Stovin Syndrome Zviratidzo uye Kurapa

Zvemukati

• Zviratidzo
• Kurapa
• Matambudziko

Hugles-stovin syndrome chirwere chisingawanzoitika uye chakakomba chinokonzeresa aneurysms yakawanda mupurmonary arteri uye akati wandei mamiriro eakadzika mutsinga thrombosis panguva yehupenyu. Kubva pakatsanangurwa kekutanga kwechirwere ichi pasirese, vanhu vasingasvike makumi mana vakaonekwa mugore ra2013.

Chirwere ichi chinogona kuzviratidza muzvikamu zvitatu zvakasiyana, uko kwekutanga kunowanzo kuve ne thrombophlebitis, yechipiri nhanho ine pulmonary aneurysms, uye yechitatu neyekupedzisira nhanho inozivikanwa nekumuka kweanorism iyo inogona kukonzeresa kukosora kweropa uye kufa.

Chiremba akakodzera kwazvo kuongorora uye kurapa chirwere ichi ndiye rheumatologist uye kunyangwe hazvo chikonzero chacho chisati chave kunyatso kuzivikanwa, zvinofungidzirwa kuti zvinogona kunge zvine chekuita nesystemic vasculitis.

Zviratidzo

Hugles-stovin zviratidzo zvinosanganisira:

• Kukosora ropa;
• Kunetseka kufema;
• Kunzwa kwekufema kwekufema;
• Kurwadziwa nemusoro;
• Yakakwira, inoramba ichirwara;
• Kurasikirwa kweinenge 10% yehuremu pasina chikonzero chiri pachena;
• Papilledema, kunova kuwedzera kwepisiki papillai inomiririra kuwedzera kwekumanikidza mukati mehuropi;
• Kuzvimba uye kurwadziwa kwakanyanya mumhuru;
• Kuona kaviri uye
• Kugwinha.

Kazhinji munhu ane Hugles-stovin syndrome ane zviratidzo zvemakore mazhinji uye iyo syndrome inogona kutovhiringidzwa nechirwere chaBehçet uye vamwe vaongorori vanotenda kuti ichi chirwere hachina kukwana chikamu chechirwere chaBehçet.

Chirwere ichi hachiwanzo kuongororwa muhucheche uye chinogona kuongororwa mukuyaruka kana mukukura mushure mekuratidzira zvataurwa pamusoro apa uye kuyedzwa senge kuongororwa ropa, chest X-rays, MRIs kana computed tomography yemusoro uye chipfuva, kuwedzera kune doppler ultrasound yekutarisa ropa uye moyo kutenderera. Iko hakuna kwekuyera chirwere uye chiremba anofanirwa kufungidzira iyi syndrome nekuda kwekufanana kwayo nechirwere cheBehçet, asi pasina zvese hunhu hwayo.

Zera revanhu vanoonekwa vane chirwere ichi rinosiyana pakati pemakore gumi nemaviri nemakumi mana nemasere.

Kurapa

Mushonga weHugles-Stovin syndrome hauna kunyatsojeka, asi chiremba anogona kukurudzira kushandiswa kwecorticosteroids yakadai sehydrocortisone kana prednisone, anticoagulants senge enoxaparin, pulse therapy uye immunosuppressants senge Infliximab kana Adalimumab iyo inogona kudzikisira njodzi pamwe nemhedzisiro. yeaneurysms uye thrombosis, nekudaro ichivandudza hupenyu hwehupenyu uye kudzikisira njodzi yekufa.

Matambudziko

Hugles-Stovin syndrome inogona kunetsa kurapa uye ine kufa kwakanyanya nekuti chinokonzera chirwere hachizivikanwe uye nekudaro marapirwo anogona kunge asingakwanise kuchengetedza hutano hwemunhu akabatwa. Sezvo paine zviitiko zvishoma zvinoonekwa pasi rese, vanachiremba havawanzo kuziva chirwere ichi, izvo zvinogona kuita kuti kuongororwa uye kurapwa kuome.

Pamusoro pezvo, maanticoagulants anofanirwa kushandiswa zvine hungwaru nekuti mune dzimwe nguva anogona kuwedzera njodzi yekubuda ropa mushure mekuputika kweanurysm uye kubuda kweropa kunogona kukura zvekuti kunotadzisa kuchengetedza hupenyu.