West syndrome: chii, zviratidzo uye kurapwa

Zvemukati

• Main maficha
• Zvinokonzera West syndrome
• Kurapwa kunoitwa sei
• West syndrome inorapwa here?

West Syndrome chirwere chisingawanzozivikanwa chinowanzoonekwa nekugwinha kwepfari, chinowanzoitika pakati pevakomana uye icho chinotanga kuzviratidza mukati megore rekutanga rehupenyu hwemucheche. Kazhinji, matambudziko ekutanga anoitika pakati pemwedzi mitatu ne mishanu yehupenyu, kunyangwe chirwere ichi chichigona kuitwa kusvika pamwedzi gumi nemiviri.

Kune matatu marudzi eiyo syndrome, iyo inoratidza chiratidzo, idiopathic uye iyo cryptogenic, uye mukuratidzira mwana ane chikonzero chakadai sekuti mwana anga asina kufema kwenguva yakareba; cryptogenic ndipo painokonzereswa nechimwe chirwere chehuropi kana kusagadzikana, uye iyo idiopathic ndipo panokonzeresa chikonzero uye mwana angave neakajairika mota kukura, sekugara uye kukambaira.

Main maficha

Izvo zvinokatyamadza zveiyo syndrome zvinononoka kukura kwepfungwa, mazuva ese pfari pfari (dzimwe nguva inodarika zana), kuwedzera kune bvunzo dzakadai seye electroencephalogram inosimbisa kusahadzika. Vanenge makumi mapfumbamwe muzana evana vane chirwere ichi vanowanzo kuve nepfungwa, autism uye shanduko dzemumuromo zvakajairika. Bruxism, kufema muromo, mazino malocclusion uye gingivitis ndidzo shanduko dzinowanzoitika muvana ava.

Izvo zvinowanzoitika ndezvekuti mutakuri weiyi syndrome inokanganiswawo nezvimwe zvinokanganisa huropi, izvo zvinogona kutadzisa kurapwa, kuve nekukura kwakanyanya, kuve kunonetsa kudzora. Nekudaro, kune vacheche kana vakapora zvakakwana.

Zvinokonzera West syndrome

Zvinokonzera chirwere ichi, icho chinogona kukonzerwa nezvinhu zvinoverengeka, hazvizivikanwe zvechokwadi, asi zvakajairika matambudziko ekuzvarwa, sekushayikwa kwehuropi oxygenation panguva yekusununguka kana nguva pfupi mushure mekuberekwa, uye hypoglycemia.

Mamwe mamiriro ezvinhu anoita kunge anofarira chirwere ichi huropi husina kumira zvakanaka, prematurity, sepsis, Angelman syndrome, sitiroko, kana hutachiona hwakadai rubella kana cytomegalovirus panguva yekuzvitakura, kuwedzera pakushandisa zvinodhaka kana kunwisa doro panguva yepamuviri. Chimwe chikonzero ndiko kuchinjika mune geni Aristaless-inoenderana neyemumbaobox (ARX) pane X chromosome.

Kurapwa kunoitwa sei

Kurapa kweWest Syndrome kunofanira kutanga nekukurumidza sezvinobvira, nekuti panguva yekugwinha kwepfari uropi hunogona kukuvara zvisinga gadziriswe, zvichikanganisa zvakanyanya hutano hwemwana nekukura.

Iko kushandiswa kwemishonga yakadai seadrenocorticotrophic hormone (ACTH) ndeimwe nzira yekurapa, kuwedzera kune physiotherapy uye hydrotherapy. Mishonga yakadai se sodium valproate, vigabatrin, pyridoxine uye benzodiazepines inogona kupihwa nachiremba.

West syndrome inorapwa here?

Muzviitiko zvakapusa, apo West syndrome haina hukama nezvimwe zvirwere, painenge isingaburitse zviratidzo, ndiko kuti, kana chikonzero chayo chisingazivikanwe, ichifungidzirwa sediopathic West syndrome uye kana mwana achirapwa pakutanga, munguva pfupi apo dambudziko rekutanga kuoneka, chirwere chinogona kudzorwa, nemukana wekurapa, pasina kudiwa kwekurapwa kwemuviri, uye mwana anogona kuve neakajairika kukura.

Nekudaro, kana mucheche aine zvimwewo zvinoenderana nezvirwere uye kana hutano hwake hwakakomba, hosha yacho haigone kurapwa, kunyangwe kurapwa kunogona kuunza nyaradzo. Munhu akanakisa kuratidza kuti hutano hwemwana mucherechedzo chiremba, mushure mekuongorora bvunzo dzese, anozokwanisa kuratidza mishonga yakakodzera kwazvo uye kudiwa kwepfungwa yekusimudzira psychomotor uye physiotherapy.