Chirwere chaWilson

Zvemukati

• Zviratidzo nezviratidzo zvechirwere cheWilson
• Chiropa-chakabatana
• Neurological
• Kayser-Fleischer mhete uye sunflower cataract
• Zvimwe zviratidzo
• Chii chiri chikonzero uye ndiani ari panjodzi yechirwere cheWilson?
• Chirwere cheWilson chinoonekwa sei?
• Kuongorora kwepanyama
• Lab miedzo
• Chirwere chaWilson chinorapwa sei?
• Chekutanga danho
• Chikamu chechipiri
• Chikamu chechitatu
• Ndeapi maonero echirwere cheWilson?
• Unogona here kudzivirira chirwere chaWilson?
• Matanho anotevera

Chii chinonzi Wilson's disease?

Chirwere chaWilson, chinozivikanwawo se hepatolenticular degeneration uye inofambira mberi lenticular degeneration, iri isingawanzoitika geni kusagadzikana kunokonzera mhangura chepfu mumuviri. Inobata nezve 1 muvanhu zviuru makumi matatu pasirese.

Mumuviri une hutano, chiropa chinosefa kunze kwemhangura yakawandisa chobva chaiburitsa kuburikidza neweti. Nechirwere cheWilson, chiropa hachigone kubvisa imwezve mhangura zvakanaka. Iyo yemhangura yekuwedzera inozovaka mumitezo yakaita seuropi, chiropa, uye maziso.

Kuongorora kwekutanga kwakakosha pakumisa kufambira mberi kwechirwere cheWilson. Kurapa kunogona kusanganisira kutora mushonga kana kutora chiropa. Kunonoka kana kusagamuchira kurapwa kunogona kukonzera kukundikana kwechiropa, kukuvara kwehuropi, kana zvimwe zvinotyisidzira hupenyu.

Taura nachiremba wako kana mhuri yako iine nhoroondo yechirwere cheWilson. Vanhu vazhinji vane chirwere ichi vanorarama hupenyu hwakajairika, hune hutano.

Zviratidzo nezviratidzo zvechirwere cheWilson

Zviratidzo nezviratidzo zvechirwere cheWilson zvinosiyana zvakanyanya, zvinoenderana nenhengo inobatika. Vanogona kukanganisa zvimwe zvirwere kana mamiriro. Chirwere chaWilson chinogona kungoonekwa nachiremba uye kuburikidza nekuongororwa kwekuongororwa.

Chiropa-chakabatana

Zviratidzo zvinotevera zvinogona kuratidza kuunganidzwa kwemhangura muchiropa:

• kushaya simba
• kunzwa kuneta
• kuonda
• kusvotwa
• kurutsa
• kurasikirwa nenzara
• kuvava
• jaundice, kana yero yeganda
• edema, kana kuzvimba kwemakumbo nedumbu
• kurwadziwa kana kuzvimba mudumbu
• dandemutande angiomas, kana rinoonekwa bazi-seropa tsinga paganda
• tsandanyama

Zvizhinji zvezviratidzo izvi, senge jaundice uye edema, zvakafanana kune mamwe mamiriro akaita sechiropa uye itsvo kutadza. Chiremba wako achaitisa bvunzo dzakawanda asati asimbisa kuongororwa kwechirwere cheWilson.

Neurological

Kuunganidzwa kwemhangura muuropi kunogona kukonzera zviratidzo zvakadai se:

• ndangariro, kutaura, kana kukanganisika kwemaonero
• kufamba zvisina kujairika
• migraines
• kumedza mate
• kushaya hope
• kudzikama nemaoko
• hunhu hunochinja
• kuchinja manzwiro
• kuora mwoyo
• matambudziko kuchikoro

Mumatanho epamberi, izvi zviratidzo zvinogona kusanganisira mhasuru, kubatika, uye kurwadziwa kwemhasuru panguva yekufamba.

Kayser-Fleischer mhete uye sunflower cataract

Chiremba wako anozotarisawo Kayser-Fleischer (KF) mhete uye sunflower cataract mumaziso. KF zvindori zvisina kujairika zvegoridhe-shava discoloration mumaziso izvo zvinokonzereswa nemadhosi emhangura yakawanda. KF zvindori zvinoratidzika munenge zvikamu makumi mapfumbamwe nezvinomwe kubva muzana zvevanhu vane chirwere cheWilson.

Sunflower cataract inoratidzika mu1 pavanhu vashanu vane chirwere cheWilson. Iyi inzvimbo yakasarudzika yemhando ine ma spokes anobudikira kunze.

Zvimwe zviratidzo

Kuvakwa kwemhangura mune dzimwe nhengo kunogona kukonzera:

• bluish discoloration muzvipikiri
• itsvo matombo
• nguva isati yasvika osteoporosis, kana kushomeka kwefupa
• arthritis
• kutadza kuenda kumwedzi
• yakaderera BP

Chii chiri chikonzero uye ndiani ari panjodzi yechirwere cheWilson?

Shanduko mu ATP7B geni, iro rinotungamira kwekufambisa kwemhangura, rinokonzera chirwere chaWilson. Iwe unofanirwa kugara nhaka geni kubva kuvabereki vaviri kuitira kuti uve nechirwere cheWilson. Izvi zvinogona kureva kuti mumwe wevabereki vako ane mamiriro kana anotakura geni.

Iyo geni inogona kusvetuka chizvarwa, saka iwe ungangoda kutarisa kupfuura vabereki vako kana kutora genetiki bvunzo.

Chirwere cheWilson chinoonekwa sei?

Chirwere chaWilson chinogona kunge chakaomera vanachiremba kutanga kuongorora Zviratidzo zvakafanana nezvimwe zvehutano senge heavy metal chepfu, hepatitis C, uye cerebral palsy.

Dzimwe nguva chiremba wako anozogona kutonga kunze kwechirwere cheWilson kana zviratidzo zvetsinga zvangoitika uye pasina K-F mhete inoonekwa.Asi izvi hazvisi nguva dzose kune vanhu vane zviratidzo zvechiropa-kana zvimwe zviratidzo.

Chiremba anozobvunza nezve ako zviratidzo uye obvunza nhoroondo yemhuri yako yekurapa. Vanozoshandisawo zvakasiyana siyana zveyedzo kuti vatarise kukuvara kunokonzerwa nekuunganidzwa kwemhangura.

Kuongorora kwepanyama

Munguva yemuviri wako, chiremba wako acha:

• ongorora muviri wako
• teerera manzwi mudumbu
• tarisa maziso ako pasi pechiedza chakajeka cheKF mhete kana sunflower cataract
• kuyedza mota yako uye ndangariro hunyanzvi

Lab miedzo

Zvekuongororwa kweropa, chiremba wako achatora masampuli uye ozoaita kuti aongororwe kubazi kuti aongorore:

• kusagadzikana muzvironda zvako zvechiropa
• huwandu hwemhangura muropa
• yakadzika mazinga e ceruloplasmin, protein inotakura mhangura kuburikidza neropa
• geni rakachinjika, iro rinodaidzwawo kunzi kuongorora majini
• shuga shoma yeropa

Chiremba wako anogona zvakare kukukumbira iwe kuti utore weti yako kwemaawa makumi maviri nemana kuti utsvage kuunganidzwa kwemhangura.

Chirwere chaWilson chinorapwa sei?

Kubudirira kurapwa kwechirwere cheWilson kunoenderana nenguva kupfuura mishonga. Kurapa kunowanzoitika mumatanho matatu uye kunofanirwa kugara kweupenyu hwese. Kana munhu akamira kutora mishonga, mhangura inogona kuvaka zvakare.

Chekutanga danho

Mushonga wekutanga kubvisa mhangura yakawandisa kubva mumuviri wako kuburikidza nekubiridzira kurapa. Chelating vamiririri vanosanganisira zvinodhaka senge d-penicillamine uye trientine, kana Syprine. Iyi mishonga inobvisa iyo yakawedzera mhangura kubva kunhengo dzako uye yoiburitsa muropa. Itsvo dzako dzinobva dzasefa iyo mhangura kupinda weti.

Trientine ine mashoma akataurwa mhedzisiro pane d-penicillamine. Zvinogona kuitika mhedzisiro d-penicillamine inosanganisira:

• kupindwa nechando
• mapundu
• nyaya dzeitsvo
• mapfupa emongo

Chiremba wako achakupa madosi epasi ekubiridzira zvinodhaka kana iwe uine nhumbu, sezvo zvichikonzera kuberekwa kuremara.

Chikamu chechipiri

Icho chinangwa chechipiri chikamu ndechekuchengetedza zvakajairika mazinga emhangura mushure mekubviswa. Chiremba wako achapa zinc kana tetrathiomolybdate kana iwe wapedza kurapwa kwekutanga kana kuratidza zviratidzo asi uine chirwere chaWilson.

Zinc inotorwa nemuromo semunyu kana acetate (Galzin) inochengetedza muviri kubva kunotora mhangura kubva muzvikafu. Iwe unogona kunge uine dumbu diki rinogumbuka kubva kutora zinc. Vana vane chirwere cheWilson asi hapana zviratidzo vangangoda kutora zinc kudzivirira mamiriro kubva pakuwedzera kana kunonoka kufambira mberi.

Chikamu chechitatu

Mushure mekunge zviratidzo zvave nani uye ako emhangura mazinga akajairika, iwe uchazoda kutarisa pane-refu-refu yekurapa kurapa. Izvi zvinosanganisira kuenderera zinc kana chelating kurapwa uye kugara uchiongorora huwandu hwemhangura.

Iwe unogona zvakare kubata ako emhangura mazinga nekudzivirira chikafu chine huwandu hwakakwira, senge:

• michero yakaomeswa
• chiropa
• howa
• nzungu
• hove
• chokoreti
• multivitamini

Iwe ungangoda kuongorora ako emvura masosi kumba, futi. Panogona kunge paine imwe mhangura mumvura yako kana imba yako iine pombi dzemhangura.

Mishonga inogona kutora chero kubva pamwedzi mina kusvika kumatanhatu kuti ishande mumunhu ari kuona zviratidzo. Kana munhu akasapindura kurapwa uku, vangangoda kuisirwa chiropa. Kubudirira kwechiropa kunogona kuporesa chirwere cheWilson. Kubudirira kwehuwandu hwekushandurwa kwechiropa ndeye 85 muzana mushure megore rimwe.

Ndeapi maonero echirwere cheWilson?

Pakutanga iwe unowana kana uine geni rechirwere cheWilson, zvirinani kufungidzira kwako kuri. Chirwere chaWilson chinogona kukura kuita kutadza kwechiropa uye kukuvara kwehuropi kana chikasarapwa.

Kurapa kwekutanga kunogona kubatsira kudzoreredza nyaya dzetsinga uye kukuvara kwechiropa. Kurapa mune inotevera nhanho kunogona kudzivirira kumwe kufambira mberi kwechirwere, asi hazvingagone kudzosera kukanganisa. Vanhu vari mumatanho epamberi vangangofanira kudzidza maitiro ekugadzirisa zviratidzo zvavo pamusoro pehupenyu hwavo.

Unogona here kudzivirira chirwere chaWilson?

Chirwere chaWilson inzara inogarwa nhaka kubva kuvabereki kuenda kuvana vavo. Kana vabereki vane mwana ane chirwere cheWilson, vanogona kuve nevamwe vana vane chirwere ichi zvakare.

Kunyangwe iwe usingakwanise kudzivirira chirwere cheWilson, unogona kunonoka kana kunonoka kutanga kwemamiriro acho. Kana iwe ukaona kuti une chirwere cheWilson kutanga, iwe unogona kukwanisa kudzivirira zviratidzo kubva pakuratidza nekutora mishonga senge zinc. Nyanzvi yegenetic inogona kubatsira vabereki kuona njodzi yavo inogona kupfuudza chirwere cheWilson kuvana vavo.

Matanho anotevera

Ita musangano nachiremba wako kana iwe kana mumwe munhu waunoziva angave aine chirwere cheWilson kana ari kuratidza zviratidzo zvekukundikana kwechiropa. Chiratidzo chikuru cheichi chiitiko nhoroondo yemhuri, asi iyo geni rakachinjika rinogona kusvetuka chizvarwa. Iwe ungangoda kubvunza yeiyo geneti bvunzo pamwe chete nezvimwe bvunzo izvo chiremba wako acharonga.

Iwe uchazoda kutanga kurapwa kwako nekukasira kana iwe ukawana kuongororwa kwechirwere cheWilson. Kurapa kwekutanga kunogona kubatsira kudzivirira kana kunonoka mamiriro acho, kunyanya kana usiri kuratidza zviratidzo izvozvi. Mishonga inosanganisira vanobiridzira uye zinc uye zvinogona kutora kusvika kumwedzi mitanhatu kushanda. Kunyangwe mushure mekunge huwandu hwemhangura hwadzokera pane zvakajairwa, iwe unofanirwa kuramba uchinwa mishonga, sezvo chirwere chaWilson chiri cheupenyu hwese.