Hemophilia

Hemophilia zvinoreva boka reropa rekubuda ropa umo kugwamba kweropa kunotora nguva yakareba.

Pane mhando mbiri dzehemophilia:

• Hemophilia A (classic hemophilia, kana factor VIII kushomeka)
• Hemophilia B (chirwere cheKisimusi, kana kushomeka kwechikonzero IX)

Paunobuda ropa, akateedzana maitiro anoitika mumuviri ayo anobatsira kuwanda kweropa fomu. Maitiro aya anonzi coagulation cascade. Inosanganisira mapuroteni akasarudzika anonzi coagulation, kana zvinogwambisa ropa. Unogona kuve nemukana wepamusoro wekubuda ropa zvakawandisa kana chimwe kana zvimwe zvezvinhu izvi zvisipo kana zvisiri kushanda sezvavanofanira.

Hemophilia inokonzerwa nekushaikwa kweyekugwamba kwechinhu VIII kana IX muropa. Muzviitiko zvakawanda, hemophilia inopfuudzwa kuburikidza nemhuri (nhaka). Kazhinji yenguva, inopfuudzwa kuvana vechirume.

Chiratidzo chikuru chehemophilia kubuda ropa. Makesi akapfava anogona kunge asingawanikwe kusvika gare gare muhupenyu, mushure mekubuda ropa zvakanyanya mushure mekuvhiyiwa kana kukuvara.

Muzviitiko zvakaipisisa, kubuda ropa kunoitika pasina chikonzero. Kubuda ropa mukati kunogona kuitika chero kupi uye kubuda ropa muzvibatanidzwa zvakajairika.

Kazhinji kazhinji, haemophilia inoonekwa mushure mekunge munhu aine chirwere chisina kujairika. Inogona zvakare kuongororwa nekuongororwa kweropa kunoitwa kuti uone dambudziko, kana dzimwe nhengo dzemhuri dziine chirwere.

Mushonga unowanzozivikanwa ndewokutsiva chinoshaikwa chekugwamba muropa kuburikidza netsinga (intravenous infusions).

Kuchengetwa kwakakosha panguva yekuvhiyiwa kunoda kutorwa kana uine chirwere ichi chekubuda ropa. Saka, iva nechokwadi chekuudza chiremba wako kuti une chirwere ichi.

Izvo zvakakoshawo zvikuru kugovana ruzivo nezve chirwere chako nehama dzeropa sezvo dzingangobatwawo.

Kubatana neboka rekutsigira uko nhengo dzinogovana zvakajairika nyaya kunogona kudzikamisa kushushikana kwechirwere chenguva refu (chisingaperi).

Vanhu vazhinji vane hemophilia vanokwanisa kuita zvakajairika zviitiko. Asi vamwe vanhu vane kubuda ropa mumajoini, izvo zvinogona kudzikisira basa ravo.

Nhamba shoma yevanhu vane hemophilia vanogona kufa nekubuda ropa kwakanyanya.

Hemophilia A; Classic hemophilia; Factor VIII kushomeka; Hemophilia B; Chirwere cheKisimusi; Chinhu cheIX kushomeka; Kubuda ropa kusagadzikana - hemophilia

• Ropa rinovhara

Carcao M, Moorehead P, Lillicrap D.Hemophilia A uye B. Muna: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Basic Misimboti uye Maitiro. 7th ed. Philadelphia, PA: Elsevier; 2018: chits. 135.

Horo JE. Hemostasis uye kuwanda kweropa. Mune: Horo JE, ed. Guyton uye Horo Chinyorwa cheMedhi Physiology. 13 ed. Philadelphia, PA: Elsevier; 2016: chits. 37.

Ragni MV. Hemorrhagic kusagadzikana: coagulation factor kushomeka. Mune: Goldman L, Schafer AI, eds. Goldman-Cecil Mushonga. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: chits. 174.