Munyori: Janice Evans
Zuva Rekusika: 3 Chikunguru 2021
Gadziridza Zuva: 9 Chivabvu 2024
Anonim
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Congenital protein C kana S kushomeka kushomeka kwemapuroteni C kana S mune inoyerera chikamu cheropa. Mapuroteni zvinhu zvakasikwa zvinobatsira kudzivirira kuwanda kweropa.

Congenital protein C kana S kushomeka chirwere chakagara nhaka. Izvi zvinoreva kuti inopfuudzwa kuburikidza nemhuri. Kuberekwa kunoreva kuti iripo pakuzvarwa.

Iko kusagadzikana kunokonzera kusanzwisisika kweropa kuvhara.

Mumwe muvanhu mazana matatu ane rimwe rinowanzo geni uye rimwe rakakanganisa geni rekushomeka kweprotein C.

Mapuroteni S kushomeka kushoma zvakanyanya uye kunoitika mune angangoita 1 muvanhu zviuru makumi maviri.

Kana iwe uine ichi chiitiko, iwe uri mukana wekuvandudza ropa reropa. Zviratidzo zvakafanana neakadzika vein thrombosis, uye zvinosanganisira:

  • Marwadzo kana unyoro munzvimbo yakakanganiswa
  • Kutsvuka kana kuzvimba munzvimbo yakakanganiswa

Anopa hutano anoita bvunzo dzepanyama uye obvunza nezve nhoroondo yako yezvokurapa nezviratidzo.

Rabhoritari bvunzo dzichaitwa kutarisa mapuroteni C uye S.

Ropa-kutetepa zvinodhaka zvinoshandiswa kurapa uye kudzivirira kuwanda kweropa.


Mhedzisiro yacho inowanzo kuve yakanaka nekurapwa, asi zviratidzo zvinogona kudzoka, kunyanya kana vamiririri-vanocheka ropa vakamiswa.

Zvinetso zvinogona kusanganisira:

  • Kurohwa kwehudiki
  • Kupfuura kudarika kumwe kurasikirwa kwepamuviri (kudzokazve kwepamuviri)
  • Kudzokorora kunoitika mutsinga
  • Pulmonary embolism (ropa rinovhara mumapapu arteri)

Muzviitiko zvisingawanzoitika, kushandisa warfarin kutetepa ropa uye kudzivirira kugwamba kunogona kukonzera kupfupisa kwakawedzera kugwamba uye maronda eganda akakomba. Vanhu vari panjodzi kana vakasarapwa pamwe neropa-rinoonda mushonga heparin vasati vatora warfarin.

Fonera mupiki wako kana iwe uine zviratidzo zvekugwamba mutsinga (kuzvimba uye kutsvuka kwegumbo).

Kana mupi wako akakuongorora uine chirwere ichi, unofanirwa kungwarira kudzivirira kugwamba kubva pakuumba. Izvi zvinogona kuitika kana ropa richifamba zvishoma nezvishoma mutsinga, senge kubva pakuzorora kwenguva refu kwemubhedha panguva yekurwara, kuvhiyiwa, kana kugara muchipatara. Izvo zvinogona zvakare kuitika mushure mekureba ndege kana kufamba kwemotokari.

Mapuroteni S kushomeka; Mapuroteni C kushomeka


  • Ropa kugadzirwa
  • Ropa rinovhara

Anderson JA, Hogg KE, Weitz JI. Hypercoagulable nyika. Muna: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Basic Misimboti uye Maitiro. 7th ed. Philadelphia, PA: Elsevier; 2018: chitsuwa 140.

Patterson JW. Iyo vasculopathic reaction pateni. Mune: Patterson JW, ed. Weedon's Ganda Pathology. 4th ed. Philadelphia, PA: Elsevier; 2015: chits. 8.

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