Dermatomyositis

Dermatomyositis chirwere chetsandanyama chinosanganisira kuzvimba uye nekuputika kweganda. Polymyositis yakafanana neyakaomarara mamiriro, ayo zvakare anosanganisira kushomeka kwemhasuru, kuzvimba, unyoro, uye kukuvara kwemasuru asi pasina kuputika kweganda. Ose ari maviri chikamu cheboka rakakura rechirwere chinonzi infusing myopathy.

Chikonzero che dermatomyositis hachizivikanwe. Nyanzvi dzinofunga kuti zvinogona kunge zvichikonzerwa nehutachiona hutachiona hwemhasuru kana dambudziko nedziviriro yemuviri. Izvo zvinogona zvakare kuitika kune vanhu vane kenza mudumbu, mapapu, kana zvimwe zvikamu zvemuviri.

Chero ani zvake anogona kuvandudza mamiriro aya. Inowanzoitika muvana vane makore mashanu kusvika gumi nemashanu uye vakuru vane makore makumi mana kusvika makumi matanhatu. Inobata vakadzi kazhinji kupfuura varume.

Zviratidzo zvinogona kusanganisira:

• Tsvina kushaya simba, kuomarara, kana kurwadziwa
• Matambudziko kumedza
• Ruvara rwepepuru kumaziso epamusoro
• Pepuru-tsvuku ganda kuputika
• Kufema kwekufema

Iko kushomeka kwemhasuru kunogona kuuya nekukasira kana kukura zvishoma nezvishoma pamusoro pevhiki kana mwedzi. Iwe unogona kunetseka kusimudza maoko ako pamusoro wako, kusimuka kubva pakagara nzvimbo, uye kukwira masitepisi.

Rash inogona kuoneka pachiso chako, makonji, mutsipa, mapendekete, pamusoro pechipfuva, uye musana.

Anopa hutano anoita bvunzo dzepanyama. Miedzo inogona kusanganisira:

• Ropa rinoyedza kutarisa mwero wemhasuru enzyme inonzi creatine phosphokinase uye aldolase
• Kuongororwa kweropa kwezvirwere zvemuviri
• ECG
• Electromyography (EMG)
• Magnetic resonance imaging (MRI)
• Tsvina biopsy
• Ganda biopsy
• Kumwe kuongorora kuongororwa kwekenza
• Chest x-ray uye CT scan yechipfuva
• Lung basa bvunzo
• Kumedza kudzidza
• Myositis chaiyo uye inosanganisirwa autoantibodies

Mushonga mukuru ndiko kushandiswa kwemishonga yecorticosteroid. Muyero wemishonga unodzurwa zvishoma nezvishoma sezvo simba remhasuru rinovandudza. Izvi zvinotora anenge mavhiki mana kusvika matanhatu. Iwe unogona kugara pane yakaderera dosi yemushonga wekorticosteroid mushure meizvozvo.

Mishonga yekudzvinyirira immune system inogona kushandiswa kutsiva iyo corticosteroids. Iyi mishonga inogona kusanganisira azathioprine, methotrexate kana mycophenolate.

Mishonga inogona kuyedzwa kana chirwere chinoramba chichishanda kunyangwe iyi mishonga ndeiyi:

• Inopinza gamma globulin
• Biologic zvinodhaka

Kana tsandanyama dzako dzikasimba, mupi wako anogona kukuudza kuti udzike zvishoma nezvishoma pamadhivha ako. Vanhu vazhinji vane chirwere ichi vanofanirwa kutora mushonga unonzi prednisone kwehupenyu hwavo hwese.

Kana kenza iri kukonzera mamiriro acho, kushaya simba kwemhasuru uye kuputika kunogona kuita zvirinani kana bundu rabviswa.

Zviratidzo zvinogona kupera zvachose mune vamwe vanhu, senge vana.

Mamiriro acho anogona kuuraya kune vakuru nekuda kwe:

• Yakanyanya mhasuru kushaya simba
• Kushaya zvokudya zvinovaka muviri
• Chirwere chemabayo
• Kukundikana kwemapapu

Zvikonzero zvikuru zvekufa nemamiriro aya igomarara uye chirwere chemapapu.

Vanhu vane chirwere chemapapu neanti-MDA-5 antibody vane fungidziro yakashata kunyangwe yekurapa kwazvino.

Zvinetso zvinogona kusanganisira:

• Chirwere chemapapu
• Chakakomba itsvo kutadza
• Kenza (yakaipa)
• Kuzvimba kwemoyo
• Joint kurwadziwa

Fonera mupiki wako kana iwe uine mhasuru kushaya simba kana zvimwe zviratidzo zveichi chiitiko.

• Dermatomyositis - Gottron papule
• Dermatomyositis - Gottron's papules paruoko
• Dermatomyositis - heliotrope eyelids
• Dermatomyositis pamakumbo
• Dermatomyositis - Gottron papule
• Paronychia - kukwikwidza
• Dermatomyositis - heliotrope mapundu kumeso

Aggarwal R, Mutasvi LG, Ruperto N, et al. 2016 American College yeRheumatology / European League Against Rheumatism Criteria yeMinimal, Moderate, uye Major Clinical Mhinduro muVakuru Dermatomyositis uye Polymyositis: An International Myositis Kuongorora uye Clinical Study Boka / Pediatric Rheumatology International Trials Sangano Kubatana Initiative. Arthritis Rheumatol. 2017; 69 (5): 898-910. PMID: 28382787 www.ncbi.nlm.nih.gov/pubmed/28382787.

Dalakas MC. Zvirwere zvinopisa tsandanyama. N Engl J Med. 2015; 373 (4): 393-394. PMID: 26200989 www.ncbi.nlm.nih.gov/pubmed/26200989.

Nagaraju K, Gladue HS, Lundberg IE. Zvirwere zvinopisa zvemhasuru uye mamwe maopathies. Mune: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Kelley uye Firestein's Bhuku reRheumatology. 10th ed. Philadelphia, PA: Elsevier; 2017: chits. 85.

National Sangano reRare Disorders webhusaiti. Dermatomyositis. rarediseases.org/rare-diseases/dermatomyositis/. Yakasvika munaApril 1, 2019.