Munyori: Joan Hall
Zuva Rekusika: 2 Kukadzi 2021
Gadziridza Zuva: 28 Chikumi 2024
Anonim
Poreswa (Live)
Vhidhiyo: Poreswa (Live)

Potter syndrome uye Potter phenotype zvinoreva boka rezvakawanikwa zvine chekuita nekushaikwa kweamniotic fluid uye itsvo kutadza mumucheche asati azvarwa.

MuPotter syndrome, dambudziko rekutanga kukundikana kweitsvo. Itsvo dzinotadza kukura zvakanaka sezvo mwana ari kukura mudumbu. Itsvo dzinowanzo gadzira amniotic fluid (semurini).

Potter phenotype inoreva chimiro chechiso chinowanzoitika mumwana achangozvarwa kana pasina amniotic fluid. Kushaikwa kweamniotic fluid kunonzi oligohydramnios. Pasina amniotic fluid, mucheche haana kusungwa kubva pamadziro echibereko. Iko kumanikidza kwemadziro echibereko kunotungamira kuchimiro chisina kujairika chechiso, kusanganisira maziso akaparadzaniswa zvakanyanya.

Potter phenotype inogona zvakare kutungamira kune asina kujairika mitezo, kana mitezo inobatwa munzvimbo dzisina kujairika kana zvibvumirano.

Oligohydramnios inomisawo kukura kwemapapu, saka mapapu haashande nemazvo pakuzvarwa.

Zviratidzo zvinosanganisira:

  • Maziso akaparadzaniswa zvakanyanya neepicanthal folds, yakafara mhuno bhiriji, nzeve dzakadzika, uye chinodzora chin
  • Kushayikwa kweiyo weti kuburitsa
  • Kunetseka kufema

Nhumbu ultrasound inogona kuratidza kushomeka kweamniotic fluid, kusavapo kweitsvo dze fetal, kana itsvo dzisina kujairika zvakanyanya mumwana asati aberekwa.


Iyi bvunzo inotevera inogona kushandiswa kubatsira kuongorora mamiriro acho mumwana achangozvarwa:

  • X-ray yemudumbu
  • X-ray yemapapu

Kudzoreredza pakuendesa kunogona kuyedzwa kuchimirira kuongororwa. Kurapa kuchapihwa chero chekuvharisa nzira yekubuda urinary.

Ichi chiitiko chakakomba kwazvo. Kazhinji yenguva yacho inouraya. Mhedziso-yenguva pfupi mhedzisiro inoenderana nekuoma kwekubatanidzwa kwemapapu. Yakareba-mhedzisiro mhedzisiro inoenderana nekuomarara kweitsvo kubatanidzwa.

Iko hakuna kunozivikanwa kudzivirira.

Muumbi we phenotype

  • Amniotic fluid
  • Yakafara nasal bhiriji

Joyce E, Ellis D, Miyashita Y. Nephrology. Mune: Zitelli BJ, McIntire SC, Nowalk AJ, eds. Zitelli naDavis 'Atlas yePediatric Panyama Kuongorora. 7th ed. Philadelphia, PA: Elsevier; 2018: chitsiko 14.


Marcdante KJ, Kliegman RM. Kuberekwa uye kukura kwakasarudzika kweiyo Urinary turakiti. Mune: Marcdante KJ, Kliegman RM, eds. Nelson Zvakakosha zvePediatrics. 8th ed. Philadelphia, PA: Elsevier; 2019: chap 168.

Mitchell AL. Kuberekwa kusakanganiswa. Mune: Martin RJ, Fanaroff AA, Walsh MC, eds. Fanaroff naMartin's Neonatal-Perinatal Mushonga. 11th ed. Philadelphia, PA: Elsevier; 2020: chits.

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