Glanzmann thrombasthenia

Glanzmann thrombasthenia chirwere chisingawanzoitika chemaplatelet eropa. Maplatelet chikamu cheropa iro rinobatsira mukugwamba kweropa.

Glanzmann thrombasthenia inokonzerwa nekushaikwa kweprotein inowanzo kuve pamusoro pemaplatelet. Ichi chinhu chinodiwa kuti maplatelet atundane pamwechete kuti aumbe ropa.

Mamiriro acho akaberekwa, zvinoreva kuti aripo kubva pakuberekwa. Kune akatiwandei maitiro echisikigo anogona kukonzeresa mamiriro acho.

Zviratidzo zvinogona kusanganisira chero zvinotevera:

• Kubuda ropa kwakanyanya panguva uye mushure mekuvhiyiwa
• Kubuda ropa mazino
• Kutuka zviri nyore
• Kubuda kumwedzi kwakanyanya kubuda ropa
• Mhino dzemhino dzisingamire nyore
• Kubuda ropa kwenguva refu nekukuvara kudiki

Iyi miedzo inotevera inogona kushandiswa kuongorora mamiriro aya:

• Yakazara kuverenga ropa (CBC)
• Platelet kuunganidzwa bvunzo
• Platelet basa kuongorora (PFA)
• Prothrombin nguva (PT) uye yakasarudzika thromboplastin nguva (PTT)

Mimwe bvunzo inogona kudikanwa. Nhengo dzemhuri dzinogona zvakare kuda kuyedzwa.

Iko hakuna chaiwo marapirwo echirwere ichi. Kuisirwa platelet kunogona kupihwa kune vanhu vari kubuda ropa zvakanyanya.

Masangano anotevera zviwanikwa zvakanaka zvekuziva nezveGlanzmann thrombasthenia:

• Genetic uye Rare Zvirwere Ruzivo Center (GARD) - rarediseases.info.nih.gov/diseases/2478/glanzmann-thrombasthenia
• Sangano reNyika reRare Disorders (NORD) - rarediseases.org/rare-diseases/glanzmann-thrombasthenia

Glanzmann thrombasthenia mamiriro ehupenyu hwese, uye hapana mushonga. Iwe unofanirwa kutora matanho akakosha kuyedza kudzivirira kubuda ropa kana iwe uine mamiriro aya.

Chero ani ane chirwere chekubuda ropa anofanirwa kudzivirira kutora maaspirin uye mamwe asiri -steroidal anti-anogumbura zvinodhaka (NSAIDs) senge ibuprofen uye naproxen. Iyi mishonga inogona kuwedzera kubuda ropa nekudzivirira maplatelet kubva mukuumbana.

Zvinetso zvinogona kusanganisira:

• Kubuda ropa kwakanyanya
• Iron kushomeka kupererwa neropa mukuenda kumwedzi kwevakadzi nekuda kwekubuda ropa zvisina kujairika

Fonera wako mupi wezvehutano kana:

• Iwe une kubuda ropa kana kupwanya kwechikonzero chisingazivikanwe
• Kubuda ropa hakuregi mushure mekurapa kwese

Glanzmann thrombasthenia inzvimbo inogarwa nhaka. Iko hakuna kunozivikanwa kudzivirira.

Chirwere chaGlanzmann; Thrombasthenia - Glanzmann

Bhatt MD, Ho K, Chan AKC. Kukanganisika kwe coagulation mune neonate. Muna: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Basic Misimboti uye Maitiro. 7th ed. Philadelphia, PA: Elsevier; 2018: chitsuwa 150.

Nichols WL. Von Willebrand chirwere uye hemorrhagic kukanganisika kweplatelet uye vascular basa. Mune: Goldman L, Schafer AI, eds. Goldman-Cecil Mushonga. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: chits. 173.