Munyori: Virginia Floyd
Zuva Rekusika: 13 Nyamavhuvhu 2021
Gadziridza Zuva: 20 Chikumi 2024
Anonim
Hemoglobinuria paroxística Nocturna
Vhidhiyo: Hemoglobinuria paroxística Nocturna

Hemoglobinuria bvunzo muyedzo weti unoongorora hemoglobin mumugini.

Iyo yakachena-yekubata (yepakati mukati) weti sampuro inodiwa. Nzira yekuchenesa-kubata inoshandiswa kudzivirira utachiona kubva panhengo yemurume kana yemukadzi kuti isapinda mune weti sampuro. Kuti utore weti yako, unogona kuwana yakakosha-yekubata kit kubva kune wako wekuchengeta hutano mupi iyo ine yekuchenesa mhinduro uye isina kuchena unopukuta. Tevera mirairo chaizvo kuitira kuti mhedzisiro ive yechokwadi.

Hapana gadziriro yakasarudzika inodikanwa bvunzo iyi. Kana iko kuunganidzwa kuri kutorwa kubva kumucheche, akati wandei emamwe mabhegi ekuunganidza anogona kudikanwa.

Muedzo unosanganisira kungoita weti chaiyo. Iko hakuna kusagadzikana.

Hemoglobin mamorekuru akasungirirwa kumasero matsvuku eropa. Hemoglobin inobatsira kufambisa oxygen uye carbon dioxide nemuviri.

Masero matsvuku eropa ane hupenyu hwepakati hwemazuva zana nemakumi maviri. Mushure menguva ino, dzakaputswa kuita zvikamu zvinogona kugadzira red sero tsvuku. Kuputsika uku kunoitika mu spleen, mwongo wefupa, uye chiropa. Kana masero matsvuku eropa akaputsika mumidziyo yeropa, mativi awo anofamba akasununguka muropa.


Kana mwero wehemoglobin muropa uchikwira zvakanyanya, hemoglobin inotanga kuoneka mune weti. Izvi zvinonzi hemoglobinuria.

Muedzo uyu unogona kushandiswa kubatsira kuongorora zvikonzero zvehemoglobinuria.

Kazhinji, hemoglobin haioneke mune weti.

Hemoglobinuria inogona kunge iri mhedzisiro yeiyi inotevera:

  • Chirwere cheitsvo chinonzi acute glomerulonephritis
  • Kunopisa
  • Kupwanya kukuvara
  • Hemolytic uremic syndrome (HUS), kusagadzikana kunoitika kana hutachiona muhurongwa hwekudya hwaburitsa zvinhu zvine chepfu
  • Utachiona hweitsvo
  • Iropa bundu
  • Marariya
  • Paroxysmal nocturnal hemoglobinuria, chirwere umo masero matsvuku eropa anodonha pamberi pechinyakare
  • Paroxysmal inotonhora hemoglobinuria, chirwere umo immune system inogadzira antibodies anoparadza masero matsvuku eropa
  • Sickle cell anemia
  • Thalassemia, chirwere umo muviri unoita chimiro chisina kujairika kana huwandu husina kukwana hwehemoglobin
  • Thrombotic thrombocytopenic purpura (TTP)
  • Kuwedzera kwekuwedzera
  • Tiibhii

Weti - hemoglobin


  • Weti sampuro

Landry DW, Bazari H. Kusvika kumurwere ane chirwere chetsvo. Mune: Goldman L, Schafer AI, eds. Goldman-Cecil Mushonga. 26th ed. Philadelphia, PA: Elsevier; 2020: chits. 106.

Riley RS, McPherson RA. Yekutanga kuongorora weti. Mune: McPherson RA, Pincus MR, eds. Henry's Clinical Diagnosis uye Management nemaLabhoritari Maitiro. 23rd ed. St Louis, MO: Elsevier; 2017: chitsiko 28.

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