Lorenzo mafuta ekurapa Adrenoleukodystrophy

Zvemukati

• Zviratidzo zveLorenzo Oiri
• Mashandisiro ekushandisa Oiri yaLorenzo
• Mativi Mhedzisiro yeLorenzo Oiri
• Contraindications yeLorenzo Oiri

Mafuta aLorenzo chikafu chekuwedzera ne glycero trioleatel uyeglycerol trierucate,yaishandiswa kurapa adrenoleukodystrophy, chirwere chisingawanzozivikanwa zvakare chinonzi chirwere chaLorenzo.

Adrenoleukodystrophy inokonzerwa nekuunganidzwa kwemarefu-cheni akawanda emafuta acids muuropi uye adrenal gland uye inokonzeresa kudzikiswa kwemitsipa. Oiri yaLorenzo inobatsira kuomesa fatty acid mazinga uye kana ikashandiswa mune asymptomatic varwere, inoderedza njodzi yekubatwa nechirwere chinodzikira uye, mune vamwe varwere vane zviratidzo, vanogona kusimudzira hupenyu hwehupenyu.

Zviratidzo zveLorenzo Oiri

Mafuta aLorenzo anoratidzwa pakurapa adrenoleukodystrophy, achibatsira kudzivirira matambudziko muhurongwa hwemitsipa muvana vane adrenoleukodystrophy, asi vasati varatidza chero zviratidzo. Muvana vanoratidza zviratidzo zvechirwere, Oiri yaLorenzo inoratidzirwa semushonga wekuvandudza uye kuwedzera hupenyu hwehupenyu.

Mashandisiro ekushandisa Oiri yaLorenzo

Iko kushandiswa kweLorenzo's Oiri inosanganisira kutora maviri kusvika matatu mL / zuva kubatsira kubata vana vane adrenoleukodystrophy. Nekudaro, iyo muyero unofanirwa kuve wakaringana zvinoenderana nehutano hwemurwere.

Mativi Mhedzisiro yeLorenzo Oiri

Mhedzisiro yemafuta aLorenzo haashoma, asi inogona kusanganisira kupwanya kana kubuda ropa.

Contraindications yeLorenzo Oiri

Lorenzo's Oiri inopesana mune vakadzi vane nhumbu uye vanoyamwisa nekuti hapana zvidzidzo zvinoratidza kushanda pamwe nekuchengeteka.

Hazvifanirwe kushandiswa kune varwere vane kuderera kwehuwandu hwemaplatelets muropa, thrombocytopenia, kana nekuderera kwemasero machena eropa, neutropenia.