Munyori: Janice Evans
Zuva Rekusika: 28 Chikunguru 2021
Gadziridza Zuva: 21 Gunyana 2024
Anonim
Porphyrin Miedzo - Mushonga
Porphyrin Miedzo - Mushonga

Zvemukati

Chii chinonzi porphyrin bvunzo?

Porphyrin bvunzo dzinoyera mwero we porphyrins muropa rako, weti, kana chigaro. Porphyrins makemikari anobatsira kugadzira hemoglobin, rudzi rweprotein mumasero ako matsvuku eropa. Hemoglobin inotakura oxygen kubva mumapapu ako ichienda kune imwe muviri wako wese.

Zvakajairika kuti uve nediki porphyrins muropa rako uye nezvimwe zvinwiwa zvemuviri. Asi yakawandisa porphyrin inogona kureva kuti iwe une mhando ye porphyria. Porphyria chirwere chisingawanzo chinogona kukonzera matambudziko akakomba ehutano. Porphyria inowanzo kuve yakakamurwa kuita maviri mapoka:

  • Acute porphyrias, iyo inonyanya kukanganisa huta uye inokonzeresa zviratidzo zvemudumbu
  • Zvimedu porphyrias, iyo inokonzeresa zviratidzo zveganda kana iwe uchinge wasangana nezuva

Dzimwe porphyrias dzinokanganisa zvese huta uye ganda.

Mamwe mazita: protoporphyrin; protoporphyrin, ropa; protoporhyrin, chigaro; porphyrins, mutsvina yadzo; uroporphyrin; porphyrins, weti; Mauzerall-Granick bvunzo; acid; ALA; porphobilinogen; PBG; yemahara erythrocyte protoporphyrin; yakatsemurwa erythrocyte porphyrins; FEP


Chii chavanoshandiswa?

Porphyrin bvunzo dzinoshandiswa kuongorora kana kuongorora porphyria.

Nei ini ndichida iyo porphyrin bvunzo?

Iwe unogona kuda porphyrin bvunzo kana iwe uine zviratidzo zve porphyria. Pane zviratidzo zvakasiyana zvemhando dzakasiyana dze porphyria.

Zviratidzo zveacute porphyria zvinosanganisira:

  • Marwadzo emudumbu
  • Kuzvimbirwa
  • Kusvotwa uye kurutsa
  • Weti tsvuku kana shava
  • Kuchenesa kana kurwadziwa mumaoko uye / kana tsoka
  • Tsvina kushaya simba
  • Kuvhiringidzika
  • Hallucinations

Zviratidzo zvekucheka porphyria zvinosanganisira:

  • Oversensitivity kune zuva
  • Blister paganda rakaratidzwa kune zuva
  • Kutsvuka uye kuzvimba paganda rakafumurwa
  • Itching
  • Shanduko muganda reganda

Iwe unogona zvakare kuda iyo porphyrin bvunzo kana mumwe munhu mumhuri yako aine porphyria. Mazhinji mhando dze porphyria dzinogarwa nhaka, zvichireva kuti mamiriro akapfuudzwa kubva kumubereki kuenda kumwana.

Chii chinoitika panguva yeparphyrin kuyedzwa?

Porphyrins inogona kuyedzwa muropa, weti, kana chigaro. Mhando dzakajairika dze porphyrin bvunzo dzakanyorwa pazasi.


  • Kuongorora Ropa
    • Nyanzvi yezvehutano inotora muyero weropa kubva mutsinga iri muruoko rwako, uchishandisa tsono diki. Mushure mekunge tsono yaiswa, kashoma reropa kanounganidzwa muthubhu yekuyedza kana muhombodo. Unogona kunzwa kakuruma kana tsono ichipinda kana kubuda. Izvi zvinowanzotora maminetsi asingasviki mashanu.
  • 24-Hour Weti Wemuenzaniso
    • Iwe unotora zvese zvako weti mukati me24-awa nguva. Pamuedzo uyu, mupi wezvehutano kana rabhoritari anokupa mudziyo pamwe nemirawo yakanangana nekutora sampuli dzako kumba. Ive neshuwa yekutevera mirairo yese zvakanyatsonaka. Iyi yemaawa makumi maviri nemasere weti yemuyedzo bvunzo inoshandiswa nekuti huwandu hwezvinhu mumuti, kusanganisira porphyrin, inogona kusiana mukati mezuva rese. Saka kuunganidza akati wandei muzuva kunogona kupa iwo wakajeka mufananidzo wewako zvemukati zvemukati.
  • Random Urine Bvunzo
    • Unogona kupa sampuli yako chero nguva yezuva, pasina gadziriro chaiyo kana kubata kunodiwa. Uyu muedzo unowanzoitwa muhofisi yemutarisiri wehutano kana labhu.
  • Stool Bvunzo (inonziwo protoporphyrin muchitsiko)
    • Iwe unotora sampuro yechigaro chako woiisa mumudziyo wakakosha. Wako wekuchengeta hutano anokupa rairo yekuti ungagadzirira sei sampuro yako uye ugozvitumira kune lab.

Ndichafanira here kuita chero chinhu kugadzirira bvunzo?

Iwe haudi chero yakakosha gadziriro yekuongororwa kweropa kana weti.


Kweye stool bvunzo, unogona kurairwa kuti usadye nyama kana kutora chero mishonga ine maasipurini kwemazuva matatu usati waedzwa.

Kune here chero njodzi kune porphyrin bvunzo?

Pane njodzi shoma yekuongororwa ropa. Unogona kunge uine marwadzo mashoma kana kupwanya panzvimbo yakaiswa tsono, asi zviratidzo zvizhinji zvinokurumidza kupera.

Iko hakuna kuzivikanwa njodzi kune weti kana chestool bvunzo.

Zvinorevei mhedzisiro yacho?

Kana huwandu hwakawanda hwe porphyrin hunowanikwa muropa rako, weti, kana chigaro, wako mupi wezvehutano anogona kurayira mimwe bvunzo kuti asimbise kuongororwa uye kuti uwane rudzi rwe porphyria yauinayo. Nepo pasina mushonga we porphyria, mamiriro acho anogona kutarisirwa. Dzimwe shanduko dzehupenyu uye / kana mishonga inogona kubatsira kudzivirira zviratidzo uye kunetseka kwechirwere. Kunyatsorapwa kunoenderana nerudzi rwe porphyria yauinayo. Kana iwe uine mibvunzo nezvemhedzisiro yako kana nezve porphyria, taura nemupi wako wezvehutano.

Dzidza zvakawanda nezve bvunzo dzemarabhoritari, mareferenzi masosi, uye mhinduro dzekunzwisisa

Pane chero chimwe chinhu chandinofanira kuziva nezve porphyrin bvunzo?

Kunyange mhando zhinji dze porphyria dzakagara nhaka, mamwe marudzi porphyria anogona zvakare kuwanikwa. Kuwana porphyria kunogona kukonzerwa nezvakasiyana zvinhu, zvinosanganisira kuwedzeredza kutungamira, hutachiona, hepatitis C, kuwedzerwa kwesimbi, uye / kana doro rinorema.

Zvinyorwa

  1. American Porphyria Foundation [Internet]. Houston: American Porphyria Nheyo; c2010–2017. Nezve Porphyria; [yakataurwa 2019 Dec 26]; [angangoita matatu skrini. Inowanikwa kubva: https://www.porphyriafoundation.org/for-patients/about-porphyria
  2. American Porphyria Foundation [Internet]. Houston: American Porphyria Nheyo; c2010–2017. Porphyrins uye Porphyria Kuongorora; [yakataurwa 2019 Dec 26]; [angangoita 6 skrini. Inowanikwa kubva ku: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/diagnosis
  3. American Porphyria Foundation [Internet]. Houston: American Porphyria Nheyo; c2010–2017. Kutanga Mutsetse Kuyedza; [yakataurwa 2019 Dec 26]; [angangoita mana skrini. Inowanikwa kubva: https://www.porphyriafoundation.org/for-patients/about-porphyria/testing-for-porphyria/first-line-tests
  4. Hepatitis B Nheyo [Internet]. Doylestown (PA): Hepb.org; c2017. Nhaka yeMetabolic Zvirwere; [yakataurwa 2017 Zvita 20]; [angangoita 11 skrini. Inowanikwa kubva ku: http://www.hepb.org/research-and-programs/liver/risk-factors-for-liver-cancer/inherited-metabolic-diseases
  5. Hinkle J, Cheever K. Brunner & Suddarth's Handbook yeLabhoritari uye Yekuongorora Yekuongorora. 2nd Ed, Kindle. Philadelphia: Wolters Kluwer Hutano, Lippincott Williams & Wilkins; c2014. Yakapatsanurwa Erythrocyte Porphyrins (FEP); p. 308.
  6. Lab Kuedza Pamhepo [Internet]. American Association yeKiriniki Chemistry; c2001–2017. Glossary: ​​Random Urine Sample; [yakataurwa 2017 Zvita 20]; [angangoita matatu skrini.Inowanikwa kubva ku: https://labtestsonline.org/glossary#r
  7. Lab Kuedza Pamhepo [Internet]. American Association yeKiriniki Chemistry; c2001–2017. Porphyrin Miedzo; [yakagadziridzwa 2017 Zvita 20; yakataurwa 2017 Zvita 20]; [angangoita matatu skrini. Inowanikwa kubva ku: https://labtestsonline.org/tests/porphyrin-tests
  8. Mayo Clinic [Indaneti]. Mayo Foundation Yekurapa Dzidzo uye Tsvagiridzo; c1998–2017. Porphyria: Zviratidzo uye Zvinokonzera; 2017 Nov 18 [yakataurwa 2017 Zvita 20]; [angangoita matatu skrini. Inowanika kubva: https://www.mayoclinic.org/diseases-conditions/porphyria/symptoms-causes/syc-20356066
  9. Mayo Clinic: Mayo Medical Laboratories [Internet]. Mayo Foundation Yekurapa Dzidzo uye Tsvagiridzo; c1995–2017. Bvunzo ID: FQPPS: Porphyrins, Tsvina: Ongororo; [yakataurwa 2017 Zvita 20]; [angangoita maviri skrini. Inowanikwa kubva: https://www.mayomedicallaboratories.com/test-catalog/Overview/81652
  10. Mayo Clinic: Mayo Medical Laboratories [Internet]. Mayo Foundation Yekurapa Dzidzo uye Tsvagiridzo; c1995–2017. Bvunzo ID: FQPPS: Porphyrins, Tsvina: Specimen; [yakataurwa 2017 Zvita 20]; [angangoita matatu skrini. Inowanikwa kubva ku: https://www.mayomedicallaboratories.com/test-catalog/Specimen/81652
  11. Merck Chinyorwa Chevatengi Vhezheni [Internet]. Kenilworth (NJ): Merck & Co Inc. .; c2017. Yakasimba Intermittent Porphyria; [yakataurwa 2017 Zvita 20]; [angangoita matatu skrini. Inowanikwa kubva ku: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/acute-intermittent-porphyria
  12. Merck Chinyorwa Chevatengi Vhezheni [Internet]. Kenilworth (NJ): Merck & Co Inc. .; c2017. Pfupiso yePorphyria; [yakataurwa 2017 Zvita 20]; [angangoita maviri skrini. Inowanikwa kubva: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/overview-of-porphyria
  13. Merck Chinyorwa Chevatengi Vhezheni [Internet]. Kenilworth (NJ): Merck & Co Inc. .; c2017. Porphyria Cutanea Tarda; [yakataurwa 2017 Zvita 20]; [angangoita matatu skrini. Inowanikwa kubva: http://www.merckmanuals.com/home/hormonal-and-metabolic-disorders/porphyrias/porphyria-cutanea-tarda
  14. National Mwoyo, Mapapu, uye Ropa Institute [Internet]. Bethesda (MD): Dhipatimendi reUtano reU.S. Kuedzwa kweropa; [yakataurwa 2017 Zvita 20]; [angangoita matatu skrini. Inowanikwa kubva: https://www.nhlbi.nih.gov/health-topics/blood-tests
  15. National Institute of Diabetes uye Digestive uye Kidney Zvirwere [Internet]. Bethesda (MD): Dhipatimendi reUtano reU.S. Porphyria; 2014 Feb [yakataurwa 2017 Zvita 20]; [angangoita mana skrini. Inowanikwa kubva: https://www.niddk.nih.gov/health-information/liver-disease/porphyria
  16. Yunivhesiti yeRochester Medical Center [Internet]. Rochester (NY): Yunivhesiti yeRochester Medical Center; c2017. Hutano Encyclopedia: Porphyrins (Urini); [yakataurwa 2017 Zvita 20]; [angangoita maviri skrini. Inowanikwa kubva ku: https://www.urmc.rochester.edu/encyclopedia/content.aspx?contenttypeid=167&contentid;=porphyrins_urine

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