Chii chinonzi SCID (Yakanyanya Yakasanganiswa Immunodeficiency Syndrome)

Zvemukati

• Zvinogona kukonzerwa
• Ndezvipi zviratidzo
• Chii chinonzi kuongororwa
• Kurapwa kunoitwa sei

Yakakomba Yakasanganiswa Immunodeficiency Syndrome (SCID) inosanganisira seti yezvirwere zviripo kubvira pakuzvarwa, izvo zvinoonekwa nekushandurwa kwema immune system, umo maantibodies ari pazasi uye ma lymphocyte akaderera kana asipo, zvichiita kuti muviri utadze kudzivirira kubva kuzvirwere, kuisa mwana panjodzi, uye kunogona kutotungamira kurufu.

Zviratidzo zvakajairika zvechirwere zvinokonzerwa nezvirwere zvinotapukira uye kurapwa kunorapa chirwere kunosanganisira kuisirwa mapfupa emongo.

Zvinogona kukonzerwa

SCID inoshandiswa kuseta seti yezvirwere zvinogona kukonzerwa nehutachiona hurema hwakabatana neX chromosome uye zvakare nekushomeka kweADA enzyme.

Ndezvipi zviratidzo

Zviratidzo zveSCID zvinowanzoonekwa mukati megore rekutanga rehupenyu uye zvinogona kusanganisira chirwere chinotapukira chisingapindure kurapwa senge pneumonia, meningitis kana sepsis, izvo zvakaoma kurapa uye kazhinji hazvipindure pakushandiswa kwemushonga, uye hutachiona hweganda, fungal hutachiona mumuromo uye nharaunda nharaunda, manyoka uye chirwere chechiropa.

Chii chinonzi kuongororwa

Kuongororwa kunoitwa kana mwana achirwara nezvirwere zvinowanzoitika, izvo zvisina kugadziriswa nekurapwa. Sezvo chirwere ichi chiri nhaka, kana chero nhengo yemhuri ichirwara neichi chirwere, chiremba anozokwanisa kuongorora chirwere ichi achangoberekwa mwana, icho chinosanganisira kuitisa kuongororwa kweropa kuti aongorore huwandu hweanorwisa uye maT seli. .

Kurapwa kunoitwa sei

Mushonga unonyanya kushanda weSCID ndeyekuiswazve kwemapfupa ematsenga maseru kubva kune anopa hutano uye anoenderana, uyo kazhinji anoporesa chirwere.

Kusvikira mupi anowirirana awanikwa, kurapwa kunosanganisira kugadzirisa hutachiona uye kudzivirira hutachiona hutsva nekuzviparadzanisa mwana kuti arege kusangana nevamwe vangangove hutachiona hwezvirwere.

Mwana anogona zvakare kuiswa kune immunodeficiency correction kuburikidza neyemunoglobulin kutsiva, iyo inongofanirwa kupihwa chete kuvana vanopfuura mwedzi mitatu uye / kana vakatove nezvirwere.

Panyaya yevana vane SCID inokonzerwa nekushomeka kweiyo enzyme yeADA, chiremba anogona kukurudzira enzyme kutsiva kurapa, pamwe nekushandisa kwevhiki nevhiki kweADA inoshanda, iyo inopa kugadziriswazve kwema immune system mukati memwedzi 2-4 mushure mekutanga kwerapi .

Pamusoro pezvo, zvakakosha kutaura kuti majekiseni ane hutachiona anorarama kana akadzivirirwa haafanire kupihwa vana ava, kudzamara chiremba varaira zvimwe.