Munyori: Marcus Baldwin
Zuva Rekusika: 14 Chikumi 2021
Gadziridza Zuva: 25 Kurume 2025
Anonim
Chii chinonzi Lynch syndrome, chinokonzera uye maitiro ekuziva - Utano
Chii chinonzi Lynch syndrome, chinokonzera uye maitiro ekuziva - Utano

Zvemukati

Lynch syndrome ndeye zvisingawanzoitika geni mamiriro ayo anowedzera njodzi yemunhu yekuva nemukenza wematumbo asati ave nemakore makumi mashanu. Kazhinji mhuri dzine Lynch syndrome dzine huwandu hwakanyanya hwekenza yemakenza, iyo inogona kubatsira chiremba kuti aongorore.

Kunyangwe pasina nzira yakapusa yekudzora njodzi yekenza, kuva nemararamiro ane hutano nekuchengetedza nguva dzakagadzwa pamwe neyegastroenterologist kunogona kudzora mikana yezvinetso, kunyangwe kenza ikamuka, sekurapa kunogona kutanga nekukurumidza.

Nzira yekuziva sei Lynch syndrome

Lynch syndrome ndeye genetiki, nhaka yemugariro iyo isingatungamire pakuonekwa kwezviratidzo kana zviratidzo, nekudaro, kuzivikanwa kweshanduko inoitwa kuburikidza nekuongororwa nachiremba kwezvimwe zvinodiwa, senge:


  • Kuva nekenza yemuura pamberi pemakore makumi mashanu;
  • Nhoroondo yemhuri yekenza yemudumbu muvechidiki;
  • Nhoroondo yemhuri yezviitiko zvinoverengeka zvecancer yechibereko;

Mukuwedzera, mhuri dzine zviitiko zvakawanda zveimwe kanzira inoenderana, senge ovarian, bladder, kana testicular cancer, inogona zvakare kuve neLynch syndrome. Pamusoro pechiratidzo chiri kuburikidza nekuongororwa kweinotarisirwa, simbiso inogona kuitwa kuburikidza nemamorekuru mageneti ekuyedza anovavarira kuona shanduko mumageneti ane hukama neichi chirwere.

Chii chinokonzera chirwere

Lynch syndrome inoitika kana kusanzwisisika kweimwe yemageneti ane chekuita nekubvisa shanduko muDNA kuchioneka, kuchidzivirira kuratidzika kwekenza. Aya majini anogona kusanganisira MLH1, MSH2, MSH6, PMS2 uye EPCAM uye, nekudaro, kuongororwa kwerabhoritari kweropa kunowanzoitwa kusimbisa shanduko idzi.

Nekudaro, kune zvekare zviitiko zvemhuri zvinounza chirwere chisina kana shanduko mumageneti mashanu aya.


Ndezvipi njodzi dzekuve nechirwere

Mukuwedzera kune ngozi yakawanda yekuva nekenza yemukaka asati ava nemakore makumi mashanu, Lynch syndrome inogonawo kufarira kukura kwemamwe marudzi ekenza, akadai se:

  • Kenza yemudumbu;
  • Kenza yechiropa kana bile ducts;
  • Kenza yeurinal turakiti;
  • Kenza yeitsvo;
  • Gomarara reganda;
  • Kenza yechibereko kana yemazai, mune vakadzi;
  • Bundu rebongo.

Nekuda kwenjodzi yakawedzera yemhando dzakasiyana dzegomarara, zvinokurudzirwa kugara uchingobvunzana mune dzakasiyana zvekurapa kuti uongororwe uye uone chero shanduko pachine nguva. Muedzo unowanzoitwa muzviitiko izvi ndewekupa mazano kuberekwa, uko mukana wekuti ubatwe nekenza uye mukana wekutumira geni kuvana, semuenzaniso, unosimbiswa. Nzwisisa chinonzi kurairiswa kwemajini uye kuti kunoitwa sei.


Kurapwa kunoitwa sei

Iko hakuna chaiyo kurapwa kweLynch syndrome, zvisinei, dzimwe nzira dzekuchengetedza dzinogona kubatsira kudzikisa njodzi yekenza senge kuve nekudya kune hutano uye kwakaringana, kudzidzira kurovedza muviri nguva dzose uye kudzivirira kuputa uye kunwa, sezvo izvi zvinhu zvinogona kufarira kuvandudzwa mamwe marudzi ekenza.

Uye zvakare, kuwedzera kudyiwa kwezvikafu zvakapfuma muma antioxidants kunogona kubatsira kudzikisa njodzi yekenza. Ona nzira yekubika jisi ina idzo dzinobatsira kudzivirira cancer.

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