Sei kurapwa kwehemophilia

Zvemukati

• Mhando dzekurapa
• Kurapa mune zviitiko zvehemophilia ine inhibitor
• Kuchengeta panguva yekurapa

Kurapa kwehemophilia kunoitwa nekutsiva izvo zvinogwambisa izvo zvisina kukwana mumunhu, chinova chinhu VIII, mune hemophilia mhando A, uye factor IX, mune hemophilia mhando B, sezvo zvichikwanisika kudzivirira. kubuda ropa zvakanyanya.

Hemophilia chirwere chemajini umo mune kuderera kwekuita kana kusavapo kwechinhu chinovhara, ayo mapuroteni aripo muropa anogoneswa kana paita mutsinga wetsinga yeropa, kudzivirira kubuda kweropa kwakanyanya. Nekudaro, kana uchishandisa iko kutsiviwa kwezvinhu zvinogwamba, zvinokwanisika kuti munhu ane hemophilia ararame hupenyu hwakajairika, pasina zvirambidzo zvakawanda. Dzidza zvakawanda nezve hemophilia.

Mhando dzekurapa

Kunyangwe pasina mushonga, kurapwa kwehemophilia kunobatsira kudzivirira kubuda kweropa kubva mukuitika kazhinji, uye kunofanirwa kutungamirwa nahematologist uye kunogona kuitwa nenzira mbiri dzakasiyana:

• Kudzivirira kurapwa: inoumbwa nekuchinja kwenguva kwechavhara, kuitira kuti vagare vaine mwero mumuviri, uye kudzivirira kubuda kweropa. Rudzi urwu rwekurapa rungangodaro rusiri kudikanwa mumamiriro ehaemophilia ane hunyoro, uye zvinogona kukurudzirwa kuti uite kurapwa iko chete kana paine imwe mhando yeropa.
• Kurapa mushure mekubuda ropa: ndiwo marapirwo ari kudiwa, anoitwa mune zvese zviitiko, nekuiswa kweye clotting factor concentrate kana paine kubuda kweropa episode, iyo inobvumira kuti igadziriswe nekukurumidza.

Mune chero marapirwo, madosi anofanirwa kuverengerwa zvinoenderana nehuremu hwemuviri, kuomarara kwehemophilia uye nematanho ekuvhara basa chinhu icho munhu mumwe nemumwe anacho muropa rake. Factor VIII kana IX inosanganisa ine yeupfu ampoule inosanganiswa nemvura yakasanganiswa yekushandisa.

Uye zvakare, mamwe marudzi eheestatic mumiriri anonamira anogona kushandiswa kubatsira mukugwamba, senge cryoprecipitate, prothrombin yakaoma uye desmopressin, semuenzaniso. Aya marapirwo anoitwa mahara neSUS, mumatunhu ehematology nzvimbo, nekungotumirwa nachiremba mukuru kana wehematologist.

Kurapa mune zviitiko zvehemophilia ine inhibitor

Mamwe mahemophiliacs anogona kukudziridza antibodies achipokana nechinhu VIII kana IX concentrate inoshandiswa pakurapa, inonzi inhibitors, iyo inogona kukanganisa mhinduro yekurapa.

Mune zviitiko izvi, zvinogona kuve zvakakosha kuita kurapwa nemadosi epamusoro, kana nekubatanidzwa kwezvimwe zvikamu zvecocagulant zvinoriumba.

Kuchengeta panguva yekurapa

Vanhu vane hemophilia vanofanira kutora matanho anotevera:

• Dzidzira mabasa epanyama, kusimbisa mhasuru nemajoini, zvichideredza mikana yekubuda ropa. Nekudaro, zvakakosha kuti usabatike nemitambo yemitambo kana kusangana kwemhirizhonga;
• Cherekedza kuoneka kwezviratidzo zvitsva, kunyanya muvana, uye kuderera nekurapwa;
• Gara uine mishonga padyo, kunyanya kana iri yekufamba;
• Iva nechitupa, sebhandi, inoratidza chirwere, nekuda kwekukurumidzira;
• Zivisa mamiriro acho pese paunoita chero maitiro, senge kushandiswa kwejekiseni, kuvhiya mazino kana nzira dzekurapa;
• Dzivisa mishonga inobatsira kubuda ropa, senge aspirin, anti-inflammatories uye anticoagulants, semuenzaniso.

Uye zvakare, kurapwa kwemuviri kunofanirwawo kuve chikamu chekurapa kwehemophilia, sezvo ichisimudzira yakagadziriswa mota mashandiro, ichideredza njodzi yezvinetso, senge acute hemolytic synovitis, kunova kuzvimba kwemajoini nekuda kwekubuda ropa, uye kunovandudza mhasuru toni, uye nekudaro inogona kutodzora kudiwa kwekutora ropa rinovhara ropa uye nekuvandudza hupenyu.