Munyori: Janice Evans
Zuva Rekusika: 26 Chikunguru 2021
Gadziridza Zuva: 22 Gunyana 2024
Anonim
Yakashata dysplasia - Mushonga
Yakashata dysplasia - Mushonga

Fibrous dysplasia chirwere chepfupa chinoparadza uye chinotsiva zvakajairika pfupa nefibrous bone tishu. Rimwe kana akawanda mapfupa anogona kukanganiswa.

Fibrous dysplasia inowanzoitika muhudiki. Vanhu vazhinji vane zviratidzo panguva iyo ivo vane makore makumi matatu ekuberekwa. Chirwere ichi chinowanzoitika mumadzimai.

Fibrous dysplasia yakabatana nedambudziko nemajini (gene mutation) ayo anodzora maseru anogadzira mapfupa. Iko kushanduka kunoitika kana mwana achikura mudumbu. Mamiriro acho haasi kupfuudzwa kubva kumubereki kuenda kumwana.

Zviratidzo zvinogona kusanganisira chero zvinotevera:

  • Kurwadziwa kwepfupa
  • Zvironda zvepfupa (maronda)
  • Endocrine (mahormone) gland matambudziko
  • Kutsemuka kana kuora kwemapfupa
  • Rakajairika ganda ganda (pigmentation), inoitika neMcCune-Albright syndrome

Maronda emapfupa anogona kumira kana mwana asvika pakuyaruka.

Anopa hutano anozoongorora muviri. X-ray yemapfupa anotorwa. MRI inogona kukurudzirwa.

Iko hakuna kurapwa kweiyo fibrous dysplasia. Bone kutsemuka kana hurema zvinorapwa sekudikanwa. Zvinetso zveHormone zvinoda kurapwa.


Maonero acho anoenderana nekuomarara kwechimiro uye zviratidzo zvinoitika.

Zvichienderana nemapfupa anokanganiswa, matambudziko ehutano anogona kubuda anosanganisira:

  • Kana dehenya bone richikanganiswa, panogona kuve nekuona kana kurasikirwa kwekunzwa
  • Kana gumbo bone rakakanganiswa, panogona kuve nekuoma kwekufamba uye matambudziko akabatana senge arthritis

Fonera waunopa kana mwana wako aine zviratidzo zveichi chiitiko, sekudzokorora kutsemuka kwemapfupa uye kusatsanangurwa kwemapfupa kuora.

Nyanzvi mune orthopedics, endocrinology, uye genetics vanogona kuve vanobatanidzwa mukuongororwa kwemwana wako nekutarisirwa.

Iko hakuna inozivikanwa nzira yekudzivirira fibrous dysplasia. Kurapa kunovavarira kudzivirira kusagadzikana, sekudzokororazve kwemapfupa kutsemuka, kubatsira kuita kuti mamiriro acho asanyanya kuoma.

Yekuzvimba fibrous hyperplasia; Idiopathic fibrous hyperplasia; McCune-Albright chirwere

  • Anterior skeletal anatomy

Czerniak B. Fibrous dysplasia uye maronda ane hukama. Mune: Czerniak B, ed. Dorfman naCzerniak's Bone Tumors. 2nd ed. Philadelphia, PA: Elsevier Saunders; 2016: chits. 8.


Heck RK, Toy PC. Benign mapfupa mapundu uye asiri mapurasitiki mamiriro achifananidza mapundu emapfupa. Mu: Azar FM, Beaty JH, Kanale ST, eds. Kushanda kwaCampbell Orthopedics. 13 ed. Philadelphia, PA: Elsevier; 2017: chitsiko 25.

Mutengesi SN, Nadol JB. Otologic kuratidzwa kwe systemic chirwere. Mune: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Musoro uye Neck Kuvhiya. 6th ed. Philadelphia, PA: Elsevier Saunders; 2015: chitsiko 149.

Shiflett JM, Perez AJ, Mubereki AD. Skull maronda muvana: dermoids, langerhans cell histiocytosis, fibrous dysplasia, uye lipomas. Mune: Winn HR, ed. Youmans uye Winn Neurological Kuvhiya. 7th ed. Philadelphia, PA: Elsevier; 2017: chitsiko 219.

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