Pierre Robin akateedzana

Pierre Robin akateedzana (kana chirwere) chiitiko umo mucheche ane diki pane yakajairwa rushaya rwepasi, rurimi runowira kumashure muhuro, uye kunetseka kufema. Iripo pakuzvarwa.

Izvo chaizvo zvikonzero zvekuteedzana kwaPierre Robin hazvizivikanwe. Chingave chiri chikamu chemazhinji majini syndromes.

Shaya yepasi inokura zvishoma nezvishoma asati aberekwa, asi inogona kukura nekukurumidza mukati memakore mashoma ekutanga ehupenyu.

Zviratidzo zveichi chiitiko zvinosanganisira:

• Yakachena muromo
• Yakakwirira-arched palate
• Shaya idiki kwazvo ine chirebvu chidiki
• Shaya iyo iri kumashure kumashure muhuro
• Kudzokorora hutachiona hutachiona
• Kuvhura kudiki padenga remuromo, izvo zvinogona kukonzera kudzipwa kana zvinwiwa zvichidzoka kunze nemumhino
• Mazino anoonekwa kana mwana achinge azvarwa
• Rurimi rwakakura zvichienzaniswa neshaya

Anopa hutano anogona kazhinji kuongorora mamiriro aya panguva yemuviri bvunzo. Kutaurirana neyechiremba nyanzvi kunogona kutonga kunze mamwe matambudziko akabatana neiyi syndrome.

Taura nachiremba wemwana wako nezve nzvimbo dzekurara dzakachengeteka. Vamwe vacheche vane akateedzana naPierre-Robin vanofanirwa kurara padumbu panzvimbo pemusana wavo kudzivirira rurimi rwavo kuti rurege kudzoka munzira yavo yemhepo.

Muzviitiko zvine mwero, mwana anozoda kuti aiswe chubhu kuburikidza nemhino uye nenzira yemhepo kudzivirira kuvharika kwemhepo. Muzviitiko zvakakomba, kuvhiyiwa kunodiwa kudzivirira kuvhara mukati memhepo yepamusoro. Vamwe vana vanoda kuvhiyiwa kuita gomba munzira yavo yekufambisa kana kufambisa shaya yavo kumberi.

Kudyisa kunofanirwa kuitwa zvine hungwaru kudzivirira kudzipwa uye kufema zvinwiwa mumhepo. Mwana angangoda kupihwa chikafu nehubhu kudzivirira kudzipwa.

Izvi zvinotevera zviwanikwa zvinogona kupa rumwe ruzivo nezve Pierre Robin kuteedzana:

• Kuzvarwa Kwakaremara Tsvagiridzo yeVana - www.birthdefects.org/pierre-robin-syndrome
• Iyo Cleft Palate Foundation - www.cleftline.org
• National Sangano reRare Dambudziko --rarediseases.org/rare-diseases/pierre-robin- inotevera

Zvinetso zvekudzipa uye zvekudya zvinogona kuenda zvega pamusoro pemakore mashoma ekutanga sezvo shaya yepasi ichikura kuita saizi yakajairika. Kune njodzi huru yezvinetso kana nzira dzemumhepo dzemwana dzikasachengetwa kubva pakuvharika.

Aya matambudziko anogona kuitika:

• Kufema kunetseka, kunyanya kana mwana akarara
• Choking episode
• Kuunganidzwa kwemoyo kukundikana
• Rufu
• Kudyisa matambudziko
• Yakaderera ropa okisijeni uye kukuvara kwehuropi (nekuda kwekunetseka kufema)
• Rudzi rweBP yakakwira inonzi pulmonary hypertension

Vacheche vanozvarwa vaine chirwere ichi vanowanzoonekwa pakuzvarwa.

Fonera wako mupi kana mwana wako achidzipwa zvikamu kana matambudziko ekufema. Kuvharika kwenzira dzemuchadenga kunogona kukonzera ruzha rwakanyanya kana mwana afema. Kunogona zvakare kutungamira kublue kweganda (cyanosis).

Zvakare daidza kana mwana wako aine mamwe matambudziko ekufema.

Iko hakuna kunozivikanwa kudzivirira. Kurapa kunogona kuderedza matambudziko ekufema uye kudzipwa.

Pierre Robin chirwere; Pierre Robin yakaoma; Pierre Robin anomaly

• Mucheche akaoma uye akapfava marara

Dhar V. Syndromes ane kuratidzwa kwemuromo. Mune: Kliegman RM, Stanton BF, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Chinyorwa chePediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chits. 337.

Purnell CA, Gosain AK. Pierre Robin akateedzana. Mune: Rodriguez ED, Losee JE, Neligan PC, eds. Kuvhiya kwepurasitiki: Vhoriyamu yechitatu: Craniofacial, Musoro uye Neck Kuvhiya uye Chiremba KwePurasitiki Kuvhiya. 4th ed. Philadelphia, PA: Elsevier; 2018: chits. 36.