Munyori: Gregory Harris
Zuva Rekusika: 15 Kubvumbi 2021
Gadziridza Zuva: 1 Chikunguru 2025
Anonim
Marfan Syndrome: Wrist and Thumb Sign
Vhidhiyo: Marfan Syndrome: Wrist and Thumb Sign

Arachnodactyly mamiriro mune iyo minwe yakareba, yakatetepa, uye yakakombama. Dzinotaridzika kunge makumbo etsvo (arachnid).

Yakareba, minwe yakatetepa inogona kunge yakajairika uye isingabatanidzwe nechero matambudziko ekurapa. Mune zvimwe zviitiko, zvakadaro, "zvigunwe zvemhungu" zvinogona kunge zviri chiratidzo chechinetso chiri kukanganisika.

Zvinokonzera zvinogona kusanganisira:

  • Homocystinuria
  • Marfan chirwere
  • Zvimwe zvisingawanzoitika geni kusagadzikana

Ongorora: Kuva neminwe mirefu, yakatetepa inogona kunge yakajairwa.

Vamwe vana vanozvarwa vaine arachnodactyly. Inogona kuve yakanyanya kuoneka nekufamba kwenguva. Taura nemupi wako wezvehutano kana mwana wako aine minwe mirefu, yakatetepa uye uine hanya kuti mamiriro ezvinhu anogona kuvapo.

Iye mupi achaita bvunzo dzepanyama. Iwe uchazobvunzwa mibvunzo nezve nhoroondo yekurapa. Izvi zvinosanganisira:

  • Wakatanga rinhi kucherekedza minwe ichiumbwa kudai?
  • Iko kune chero nhoroondo yemhuri yekukurumidza kufa? Kune here chero nhoroondo yemhuri yeanozivikanwa matambudziko enhaka?
  • Ndezvipi zvimwe zviratidzo zviripo? Wakaona here zvimwe zvinhu zvisina kujairika?

Bvunzo dzekuziva kazhinji hadzidiwe kunze kwekunge fungidziro yekugara nhaka inofungidzirwa.


Dolichostenomelia; Spider minwe; Achromachia

Doyle Al, Doyle JJ, Dietz HC. Marfan chirwere. Mune: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Chinyorwa chePediatrics. 21st ed. Philadelphia, PA: Elsevier; 2020: chap 722.

Herring JA. Orthopedic-inoenderana syndromes. Mune: Herring JA, ed. Tachdjian's Pediatric Orthopedics. 5 ed. Philadelphia, PA: Elsevier Saunders; 2014: chits. 41.

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