Rigid munhu chirwere

Zvemukati

• Zviratidzo
• Kurapa

Mune iro rakaomarara munhu chirwere, munhu wacho ane kuomarara kwakasimba kunogona kuzviratidza mumuviri wese kana mumakumbo chete, semuenzaniso. Kana izvi zvikakanganiswa, munhu anokwanisa kufamba semusoja nekuti haakwanise kufambisa tsandanyama nemajoini ake zvakanaka.

Ichi chirwere chinodzivirira muviri chinowanzo kuratidza pakati pemakore makumi mana nemakumi mashanu ekuberekwa uye chinozivikanwawo seMoersch-Woltmann syndrome kana muChirungu, Stiff-man syndrome. Chete inenge 5% yezviitiko zvinoitika muhudiki kana kuyaruka.

Rigid's disease syndrome inogona kuratidza nenzira nhanhatu dzakasiyana:

1. Yakasarudzika fomu iyo inobata chete iyo lumbar dunhu nemakumbo;
2. Musiyano wefomu kana uchingogumira kungori 1 nhengo ine iyo dystonic kana yekumashure mamiriro;
3. Kazhinji fomu kana kuomarara kunoitika mumuviri wese nekuda kweakanyanya autoimmune encephalomyelitis;
4. Kana paine kusagadzikana kwekufamba kunoshanda;
5. Iine dystonia uye yakajairwa parkinsonism uye
6. Nenhaka spastic paraparesis.

Kazhinji munhu ane chirwere ichi haangori chete nechirwere ichi, asi zvakare ane zvimwe zvirwere zvekuzvimiririra zvakaita serudzi rwe1 chirwere cheshuga, chirwere chetachiona kana vitiligo, semuenzaniso.

Chirwere ichi chinogona kurapwa nekurapwa kunoratidzwa nachiremba asi kurapwa kwacho kunogona kutora nguva.

Zviratidzo

Zviratidzo zveyakaomarara munhu chirwere zvakakomba uye zvinosanganisira:

• Inoenderera mberi mhasuru mhasuru iyo ine zvibvumirano zvidiki mune mamwe mhasuru pasina munhu ari kugona kudzora, uye
• Kuomarara kuomarara mumhasuru izvo zvinogona kukonzeresa kuputika kwemhasuru tambo, kutsemuka uye kutyoka kwemabhonzo.

Nekuda kwezviratidzo izvi munhu anogona kunge aine hyperlordosis uye kurwadziwa musana, kunyanya kana mhasuru dzekumashure dzichikanganisika uye dzinogona kudonha kazhinji nekuti haakwanise kufamba uye kuenzanisa zvakanaka.

Kuomarara kwemhasuru kunowanzo simuka mushure menguva yekushushikana sebasa nyowani kana kuita mabasa pane veruzhinji, uye kuomarara kwemhasuru hakuitike panguva yekurara nekuremara kwemaoko nemakumbo zvakajairika nekuda kwekuvapo kwezvipenga izvi, kana chirwere hachirapike.

Kunyangwe kuwedzera kwemhasuru toni mumatunhu akabatwa, iwo tendon reflexes akajairwa uye nekudaro kuongororwa kunogona kuitwa pamwe nekuongororwa kweropa kunotsvaga chaiwo marwisi uye electromyography. X-rays, MRIs uye CT scans inofanirwawo kurairwa kusabvisa mukana weimwe hosha.

Kurapa

Kurapa kwemunhu akaomarara kunofanirwa kuitwa nekushandisa zvinodhaka zvakaita sebaclofen, vecuronium, immunoglobulin, gabapentin uye diazepam inoratidzirwa nachiremba wezveuropiyo. Dzimwe nguva, zvingave zvichidikanwa kuti ugare muICU kuitira kuvimbisa kushanda kwakakodzera kwemapapu nemoyo panguva yechirwere uye nguva yekurapa inogona kusiyana kubva pamavhiki kusvika kumwedzi.

Kuisirwa plasma uye kushandiswa kweanti-CD20 monoclonal antibody (rituximab) inogona zvakare kuratidzwa uye kuve nemhedzisiro. Vanhu vazhinji vanoonekwa kuti vane chirwere ichi vanorapwa pavanowana kurapwa.