Munyori: Charles Brown
Zuva Rekusika: 2 Kukadzi 2021
Gadziridza Zuva: 3 Chikunguru 2025
Anonim
Maffucci chirwere - Utano
Maffucci chirwere - Utano

Zvemukati

Maffucci syndrome hosha isingawanzo inobata ganda nemapfupa, ichikonzera mapundu mushwashwa, kuora mumapfupa uye kuoneka kwemamota erima muganda anokonzerwa nekukura kusingaite kwemitsipa yeropa.

At Zvinokonzera Maffucci syndrome iwo magene uye anokanganisa varume nevakadzi zvakaenzana. Kazhinji, zviratidzo zvechirwere zvinokura muhucheche kutenderedza makore 4-5 ezera.

THE Maffucci syndrome haina mushonga, zvakadaro, varwere vanogona kuwana kurapwa kudzikisa zviratidzo zvechirwere uye nekuvandudza kwavo hupenyu hwehupenyu.

Zviratidzo zveMaffucci Syndrome

Zviratidzo zvikuru zveMaffucci syndrome ndezvi:

  • Benign tumarara mune shwashwa yemaoko, tsoka uye mapfupa marefu eruoko nemakumbo;
  • Mapfupa anova asina kusimba uye anogona kutsemuka zviri nyore;
  • Kupfupisa kwemapfupa;
  • Hemangiomas, ayo ane diki diki kana bhuruu akapfava mamota paganda;
  • Pfupi;
  • Kushaya mhasuru.

Vanhu vane Maffucci Syndrome vanogona kuita gomarara repfupa, kunyanya muhenya, asiwo ovari kana gomarara rechiropa.


O kuongororwa kweMaffucci syndrome zvinoitwa kuburikidza nekuongororwa kwemuviri uye kuongororwa kwezviratidzo zvinoratidzwa nevarwere.

Kurapa kweMaffucci's Syndrome

Kurapa kweMaffucci's Syndrome kunosanganisira kudzikisira zviratidzo zvechirwere kuburikidza nekuvhiyiwa kugadzirisa kuremara kwemapfupa kana zvinowedzera kubatsira kukura kwemwana.

Ivo vanhu vanobatwa nechirwere vanofanirwa kugara vachionana nachiremba wemazino kuti vaongorore shanduko mumapfupa, kukura kwekenza yemapfupa uye kurapa kutsemuka kunoitika nekuda kwechirwere. Iyo dermatologist inofanirwa zvakare kubvunzwa kuti iongorore kutaridzika uye kukura kwehemangiomas paganda.

Izvo zvakakosha kuti varwere vagare vaine bvunzo dzepanyama, radiographs kana computed tomography scans.

Mifananidzo yaMaffucci's Syndrome

Kunobva:Nzvimbo dzeDziviriro Kudzora uye Kudzivirira

Mufananidzo 1: Kuvapo kwemamota madiki muzvibatanidzo zveminwe zvinoonekwa neMaffucci's Syndrome;


Mufananidzo 2: Hemangioma paganda remurwere ane Maffucci syndrome.

Inobatsira chinongedzo:

  • Hemangioma
  • Proteus Syndrome

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